ANEMIA 4

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65 Terms

1
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A DISORDER THAT SHOWS A DEFECT IN DNA SYNTHESIS

MEGALOBLASTIC ANEMIA

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MEGALOBLASTIC ANEMIA IS CAUSED BY?

VITAMIN B12 (COBALAMIN), FOLATE DEFICIENCY, PERNICIOUS ANEMIA

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IN MEGALOBLASTIC ANEMIA, HEMOGLOBIN HEMATOCRIT AND RETICS COUNT ARE INCREASED OR DECREASED?

DECREASED

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VITAMIN B12 DEFICIENCY IS ALSO KNOWN AS?

PERNICIOUS ANEMIA, ADDISON’S ANEMIA

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WHAT ARE THE CLINICAL FINDINGS FOR VITAMIN B12 DEFICIENCY?

PERNICIOUS ANEMIA, ACHLORHYDRIA, WEAKNESS AND NUMBNESS, SORE TONGUE, GI DISORDER, CNS PROBLEMS

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NON-MEGALOBLASTIC ANEMIA IS CAUSED BY?

LIVER DISEASE, ALCOHOLISM, BONE MARROW FAILURE

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MEGALOBLASTIC OR NON-MEGALOBLASTIC. PRESENCE OF HYPERSEGMENTED NEUTROPHILS

MEGALOBLASTIC

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MEGALOBLASTIC OR NON-MEGALOBLASTIC. ABSENCE OF HYPERSEGMENTED NEUTROPHILS

NON-MEGALOBLASTIC

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SHAPE OF MACROCYTES IN MEGALOBLASTIC ANEMIA?

OVAL

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SHAPE OF MACROCYTES IN NON MEGALOBLASTIC ANEMIA?

ROUND

11
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MCV VALUE IN MEGALOBLASTIC ANEMIA

MORE THAN OR EQUAL TO 120 FL

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MCV VALUE IN NON MEGALOBLASTIC ANEMIA

100-115 FL

13
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WHAT ARE THE DISORDERS OF IRON METABOLISM AND HEME SYNTHESIS

IRON DEFICIENCY ANEMIA, SIDEROBLASTIC ANEMIA, ANEMIA OF CHRONIC DISEASE, IRON OVERLOAD

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WHAT ARE THE DISORDERS OF BONE MARROW FAILURE?

APLASTIC ANEMIA

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WHAT ARE THE DISORDERS OF DNA METABOLISM

MEGALOBLASTIC AND NON-MEGALOBLASTIC ANEMIA

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ERYTHROPOIETIC DISORDER AND MAY BE ACQUIRED OR INHERITED

PURE RED CELL APLASIA

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IF PRCA IS ACQUIRED, THIS MAY MEAN?

TRANSIENT ERYTHROBLASTOPENIA OF CHILDHOOD

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IF PRCA IS INHERITED, THIS MAY MEAN?

DIAMOND-BLACKFAN ANEMIA

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CHARACTERIZED BY APLASTIC ANEMIA, PHYSICAL ABNORMALITIES AND CANCER SUSCEPTIBILITY

FANCONI ANEMIA

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CHARACTERIZED BY PANCYTOPENIA, MUCOCUTANEOUS ABNORMALITIES, AND BONE MARROW FAILURE

DYSKERATOSIS CONGENITA

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CHARACTERIZED BY PANCREATIC INSUFFICIENCY, CYTOPENIA, SKELETAL ABNORMALITIES AND HEMATOLOGIC MALIGNANCIES

SHWACHMAN-BODIAN DIAMOND SYNDROME

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WHAT CAN BE SEEN IN THE PERIPHERAL SMEAR OF SHWACHMAN-BODIAN DIAMOND SYNDROME

NEUTROPENIA AND PANCYTOPENIA

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CLINICAL FEATURE OF FALCONI ANEMIA

LOW BIRTH WEIGHT, SKIN HYPERPIGMENTATION, SHORT STATURE

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FATAL BONE MARROW FAILURE SYNDROME

APLASTIC ANEMIA

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THIS SHOWS NO RESPONSE IN ERYTHROPOIETIN

APLASTIC ANEMIA

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ACQUIRED APLASTIC ANEMIA IS HOW MANY PERCENT?

80-85%

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INHERITED APLASTIC ANEMIA IS HOW MANY PERCENT?

15-20%

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MOST COMMON FORM OF IRON OVERLOAD DISEASE

HEREDITARY HEMOCHROMATOSIS

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HEREDITARY HEMOCHROMATOSIS IS CAUSED BY A MUTATION IN WHAT GENE?

HFE GENE

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THIS GENE REGULATES THE AMOUNT OF IRON ABSORBED FROM FOOD

HFE GENE

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WHAT IS THE TREATMENT FOR HEREDITARY HEMOCHROMATOSIS

PHLEBOTOMY

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WHAT IS THE ENZYME AFFECTED IN CONGENITAL ERYTHROPOIETIC PORPHYRIA (CEP)—GUNTHER’S DISEASE

UROPORPHYRINOGEN III SYNTHASE DEFICIENCY

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WHAT IS THE ENZYME AFFECTED IN ERYTHROPOIETIC PROTOPORPHYRIA (EPP)

FERROCHELATASE DEFICIENCY

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WHAT IS THE ENZYME AFFECTED IN X-LINKED ERYTHROPOIETIC PROTOPORPHYRIA (XLEPP)

ALA-SYNTHASE (GAIN OF FUNCTION)

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PORPHYRIA LITERALLY MEANS?

PURPLE

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GROUP OF INHERITED DISORDERS CHARACTERIZED BY IMPAIRED PROTOPORPHYRIN PRODUCTION

PORPHYRIA

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THIS INTERFERES WITH CONVERSION OF AMINOLEVULINIC ACID TO PORPHOBILINOGEN

LEAD

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LEAD INTERFERES WITH INCORPORATION OF?

IRON AND PROTOPORPHYRIN

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LEAD INHIBITS WHAT?

PYRIMIDINE 5’-NUCLEOTIDASE

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THIS IS MOSTLY SEEN IN CHILDREN

LEAD POISONING (PLUMBISM)

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THIS DISORDER BLOCK IN PROTOPORPHYRIN PATHWAY

SIDEROBLASTIC ANEMIA

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IRON OVERLOAD IN BONE MARROW

SIDEROBLASTIC ANEMIA

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ERYTHROBLASTS WITH IRON DEPOSITS SURROUNDING THE NUCLEUS

RING/RINGED SIDEROBLAST

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IRON ACCUMULATION IN MATURE RBCS

SIDEROCYTE/PAPPENHEIMER BODY

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STAIN FOR RINGED SIDEROBLAST

PRUSSIAN BLUE

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STAIN FOR SIDEROCYTE/PAPPENHEIMER BODY

PERL’S PRUSSIAN BLUE, WRIGHT STAIN

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THIS CAUSES THE INABILITY TO USE IRON

ANEMIA OF CHRONIC DISEASE

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IN ANEMIA OF CHRONIC DISEASE THERE IS AN INCREASED LEVEL OF?

HEPCIDIN

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THIS IS THE MEASURE OF IRON BOUND TO TRANSFERRIN

SERUM IRON

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INDIRECTLY MEASURES TRANSFERRIN CONCENTRATION BY MEASURING ITS ABILITY TO BIND IRON

TOTAL IRON BINDING CAPACITY

51
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PERCENTAGE OF IRON BINDING SITES OCCUPIED BY IRON

TRANSFERRIN SATURATION

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REFLECTION OF BODY’S TISSUE IRON STORES

SERUM FERRITIN

53
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MEASUREMENT OF PROTOPORPHYRIN WITHOUT IRON

FREE ERYTHROCYTE PROTOPORPHYRIN

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IT IS THE MOST COMMON CAUSE OF ANEMIA IN THE US

IRON DEFICIENCY ANEMIA

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INSUFFICIENT IRON FOR HEMOGLOBIN SYNTHESIS

IRON DEFICIENCY ANEMIA

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IRON DEFICIENCY ANEMIA MAY ARISE FROM?

PREGNANCY, NORMAL GROWTH, MENSTRUATING WOMEN, BLOOD LOSS, INTRAVASCULAR HEMOLYSIS, GI DISORDER, PARASITIC INFECTION, MARCH HEMOGLOBINURIA

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CLINICAL SYMPTOMS OF IRON DEFICIENCY ANEMIA

FATIGUE, DIZZINESS, PALLOR, PICA, ANGULAR CHEILOSIS, GLOSSITIS, KOILONYCHIA

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WHAT IS THE NEW TERM FOR ANEMIA OF CHRONIC DISEASE

ANEMIA OF CHRONIC INFLAMMATION

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SIDEROBLASTIC ANEMIA IS HEREDITARY IN?

X-LINKED AND AUTOSOMAL

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IF SIDEROBLASTIC ANEMIA IS ACQUIRED IT CAN CAUSE WHAT DISEASE?

PRIMARY SIDEROBLASTIC ANEMIA AND SECONDARY SIDEROBLASTIC ANEMIA

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IN LEAD POISONING, RBC PROTOPORPHYRIN IS INCREASED OR DECREASED?

INCREASED

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RBC PROTOPORPHYRIN IS MEASURED USING A?

FREE ERYTHROCYTE PROTOPORPHYRIN

63
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CLINICAL SYMPTOMS OF PORPHYRIA

PHOTOSENSITIVITY, FLUORESCENCE IN TEETH AND BONE, PSYCHOSIS, WINE-RED COLOR OF URINE

64
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IN MEGALOBLASTIC ANEMIA, LACTATE DEHYDROGENASE IS INCREASED OR DECREASED?

INCREASED

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THIS IS SIMILAR TO PERNICIOUS ANEMIA WITHOUT CNS INVOLVEMENT

FOLIC ACID DEFICIENCY