Auditory nerve hearing disordersVestibular schwannoma (acoustic neuroma)

Vestibular schwannoma (acoustic neuroma)

Benign tumor that slowly grows, typically on the vestibular portion of the VC nerve. Can expand and push on the brainstem if it gets large enough

Neurofibromatosis 1 (Recklinghausen’s disease) / NF 1

Autosomal dominant condition caused by a genetic defect in neural growth factor. Changes in skin pigmentation and growth of tumors along nerves, including vesetibular schwannomas

Neurofibromatosis 2 / NF 2

Autosomal dominant condition caused by a genetic defect in neural growth factor. Changes in skin pigmentation and growth of tumors along nerves, including vesetibular schwannomasv on BOTH auditory nerves

Auditory neuropathy spectrum disorders (ANSD)

Inefficient nerve function (dyssynchronous firing), causing poor understanding and HL. Incidence in children with SN HL is up to 13.4%

Cochlear nerve aplasia/hypoplasia

Congenital hypoplasia or aplasia of vestibulocochlear nerve. Usually only in one ear

Auditory brainstem response (ABR)

Audiologist test measuring brainstem response with electrodes