cystic fibrosis

CFTR gene is involved in controlling what ?

Mucus production in lungs and digestive system

Cystic fibrous complications are…

Jaundice and weakened bones

Newborn screening test for CF

Heel prick test

CF treatment mucolytic drugs ?

Inhaled>Dornase Alfa via nebuliser

Oral>Carbocisteine

CF bronchodilator drug ?

Salbutamol

CF antibiotics given?

Prophylaxis or acute

CF oral drugs that help fix cause ?

Kaftrio (Elexacaftor, Tezacaftor, Ivacaftor)

Oral drugs given solo ?

Ivacaftor (kalydeco) given solo.

Oral Drug prescribed under a managed access scheme (between NHS & manufacturers while drug effectiveness is being established)

Orkambi (lumacaftor & ivacaftor)

If CF patients have exocrine pancreatic insufficiency what drug give ?

Pancreatin supplements before food

What is PEP?

Positive expiratory pressure

Physio intervention device

CF drugs available under managed access scheme ?

Lumacaftor.& Ivacaftor (orkambi)