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Wilson’s Disease
Autosomal recessive
Excessive accumulation of copper in liver
Mutation in ATP7B copper binding protein in chromosome 13
Features Of Wilson’s Disease
Affects teens or young adults
Liver problems e..g cirrhosis or chronic hepatitis
Neurological symptoms e.g. tremor, dystonia, tremor
Depression
Psychosis
Kayser-fleischer rings in cornea
Haemolytic anaemia

Diagnosis Of Wilson’s Disease
Serum caeruloplasmin
24 hour urine copper assay
Liver biopsy
Slit lamp examination for kayser-fleischer rings
MRI brain → double panda sign
Management Of Wilson’s Disease
Penicillamine
Tridentine
Zinc salts
Liver transplant