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carbamoyl-p synthetase
NH4+ + HCO3- + 2ATP → Carbamoyl-P + 2ADP
Ornithine Transcarbamoylase
Ornithine + Carbamoyl-P → Citrulline
Argininosuccinate Synthetase
Citrulline + ATP → Citrullyl-AMP + 2Pi
Argininosuccinate synthetase
Citrullyl-AMP + Asp → Argininosuccinate + AMP
Argininosuccinase
Argininoscuccinate → Arginine + Fumarate
Arginase
Arginine + H2O → Urea + Ornithine