Peds - 12 - Hypermobility

hypermobility spectrum disorder

HSD stands for _______________

ehlers danlos syndrome

EDS stands for ________________

joint hypermobility JH

______________ can be localized but is often symmetrical bilaterally

trauma

if a single joint is affected unilaterally, those issues may be from ________

generalized joint hypermobility GJH

______________ is when 5+ joints have JH, usually inherited

pain, chronic fatigue

when GJH is accompanied by symptoms like _______ or _______, it is characterized as a medical condition

ehlers danlos syndrome EDS

______________ is a group of heritable connective tissue disorders with GJH and skin hyperextensibility in common

hypermobility spectrum disorder HSD

_____________ are hypermobility disorders that do not meet the criteria of EDS

CANNOT

typically children (can/cannot) be diagnosed with EDS

collagen

GJH, HSD, and EDS all involve abnormalities in ________ biosynthesis, structure, and process

>= 6/9

generalized joint hypermobility in kids is indicated by a beighton score of ______ in children and adolescents

>= 5/9

generalized joint hypermobility in kids is indicated by a beighton score of ______ in adults

1. generalized joint hypermobility (beighton)

2. presence of 2 or more:

   1. 12 systemic manifestations

   2. positive family history

   3. MSK complications including at least one of:

      1. MSK pain in 2+ limbs

      2. chronic widespread pain for >3mo

      3. recurrent joint dislocation in the absence of trauma

3. exclusion of other CT disorders

see attached photo for clarification

a diagnosis of EDS requires these three things: (will we need to know this much detail? i have no idea)

• (2) pinkies greater than 90 deg extension

• (2) thumbs touching forearms

• (2) knees locked out more than 10 deg hyperE

• (2) elbows extend an extra 10 deg

• (1) palms flat on the floor without bending knees

the 9 possible points on the beighton score come from these 5 characteristics:

HSD and hEDS (hypermobile EDS)

systemic effects of both ______________:

• affect CT throughout the body and all body systems

• chronic pain, fatigue, dysautonomia, proprioceptive, and coordination deficits

• associated with developmental coordination disorder

• frequently comorbid with ASD and ADHS

maintain neutral

chronic fatigue can occur with HSD and hEDS because it takes more work to ___________

FALSE

T/F: POTS is a red flag

POTS

_______ may be the result of vascular pooling in hyperelastic vascular structures and abnormal sympathetic activity

TRUE

T/F: vascular EDS is a red flag

vascular EDS

_________ is hypermobility of blood vessels that has the life-threatening risk for aortic or organ rupture

translucent skin, prominent veins

two signs of vEDS are _______ and _______

activity or exercise

overall for EDS and hypermobility, a key symptom is pain exacerbated by _______________

CARDIOVASCULAR HISTORY

when taking a hypermobility history, make sure to take _______________

*no case information in these cards

*no case information in these cards

stand test

the __________ can be used to test for POTs related signs and symptoms, and to rule out OH

functional strength, gait, endurance

when doing a physical exam for hypermobility, look at these three things:

hypermobile

it is debated whether the ________ ROM should be included in strengthening

tissue healing

because of collagen/ECM considerations, hypermobile kids may have poor ___________, increasing the recovery timeline