Part 12: Peds Tumors- Rhabdomyosarcoma

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10 Terms

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What is rhabdomyosarcoma?

highly malignant cancer of embryonic mesenchyme that develops into muscle

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Rhabdomyosarcoma epidemiology

  • Most common pediatric soft tissue sarcoma

  • More common in children & teens than in infants- as is the case with all sarcomas

  • Can occur anywhere, but most commonly occurs in H&N

<ul><li><p> Most common <strong>pediatric soft tissue sarcoma</strong></p></li><li><p>More common in children &amp; teens than in infants- as is the case with all sarcomas</p></li><li><p>Can occur anywhere, but most commonly occurs in H&amp;N</p></li></ul><p></p>
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Rhabdomyosarcoma epidemiology

Unknown

associated with fetal alcohol syndrome

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Presentation of rhabdomyosarcoma

painful mass

<p>painful mass </p>
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Pathology (cell types) for rhabdomyosarcoma

several subtypes

only one worth mentioning is pleomorphic

<p>several subtypes</p><p>only one worth mentioning is <strong>pleomorphic </strong></p>
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staging for rhabdomyosarcoma

nope

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Treatment for rhabdomyosarcoma

  1. Surgery

  1. RTT

  2. Chemo

Option 1: Surgical excision= best option but if large deformity, then

Option 2: RTT or Chemo = good cosmetic results

  • RTT: RTT + chemo- good local control

  • Chemo: an effective adjunct

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RTT to treat rhabdomyosarcoma

  1. What is included in tx field

  2. Fractionation

  1. What is included in tx field: tumor volume + 2cm margin

  2. Fractionation:

    1. Option 1: 180 cGy/day to 5040

    2. Option 2: Hyperfractionation 110 cGy 2x/ day to 5940

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5 year survival for rhabdomyosarcoma

vary considerably depending on primary site, cell type and behavior