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Tolosa-Hunt Syndrome
Painful ophthalmoplegia
Granulomatous inflammation
cavernous sinus
Superior orbital fissures
Orbital apex
MR- T1/T2 isointense to grey matter, vivid enhancement
Tx: high dose steroid
Extraconal orbital lesion
Dermoid cyst - most common in paeds
Lacrimal gland lesion - dacryocystocoele, dacryoadenitis
Haemangioma
Nerve sheath tumour- schwannoma, neurofibroma
Rhabdomyosarcoma
Lymphoma/leukemia
Extra orbital lesion extending into extraconal
orbital cellulitis
Mets
Sinonasal tumour
Meningioma
Intraconal orbital lesion
Optic nerve glioma
Optic nerve meningioma
Optic neuritis
Vascular malformation
Lymphatic malformation
Mets
Lymphoma/leukemia
Conal orbital lesion
Painless
thyroid ophthalmopathy (no tendon)
Lymphoma
Painful
orbital pseudotumour
Intraocular lesion
Painful
ocular trauma
Uveitis
Glaucoma
Painless
staphyloma
Coloboma
Retinoblastoma
Mets
Retinoblastoma
USS
echogenic mass with variable shadowing
CT
contrast enhance retrolental mass
calcification
haemorrhage-dense vitreous
MR
T1 hyperintense compared to vitreous
T2 hypointense to vitreous
diffusion restriction
Leukocoria ddx
Retinoblastoma
Persistent Hyperplastic Primary Vitreous
Coats Disease
Larval granulomatosis
Coats Disease aka exudative retinitis
Leukocoria, 3-9yo
telangiectasias and aneurysms of retinal blood vessels
→ subretinal exudative fluid collections
→ RETINAL DETACHMENT
Tx:
ophthalmology ref
photocoagulation/cryotherapy/surgical repair