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Last updated 3:07 PM on 8/25/26
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9 Terms

1
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Tolosa-Hunt Syndrome

Painful ophthalmoplegia

Granulomatous inflammation

  • cavernous sinus

  • Superior orbital fissures

  • Orbital apex

MR- T1/T2 isointense to grey matter, vivid enhancement

Tx: high dose steroid

2
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Extraconal orbital lesion

Dermoid cyst - most common in paeds

Lacrimal gland lesion - dacryocystocoele, dacryoadenitis

Haemangioma

Nerve sheath tumour- schwannoma, neurofibroma

Rhabdomyosarcoma

Lymphoma/leukemia


Extra orbital lesion extending into extraconal

  • orbital cellulitis

  • Mets

  • Sinonasal tumour

  • Meningioma


3
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Intraconal orbital lesion

Optic nerve glioma

Optic nerve meningioma

Optic neuritis

Vascular malformation

Lymphatic malformation

Mets

Lymphoma/leukemia


4
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Conal orbital lesion

Painless

  • thyroid ophthalmopathy (no tendon)

  • Lymphoma


Painful

  • orbital pseudotumour


5
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Intraocular lesion

Painful

  • ocular trauma

  • Uveitis

  • Glaucoma


Painless

  • staphyloma

  • Coloboma

  • Retinoblastoma

  • Mets


6
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Retinoblastoma

USS

  • echogenic mass with variable shadowing


CT

  • contrast enhance retrolental mass

  • calcification

  • haemorrhage-dense vitreous


MR

  • T1 hyperintense compared to vitreous

  • T2 hypointense to vitreous

  • diffusion restriction


7
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Leukocoria ddx

  1. Retinoblastoma

  2. Persistent Hyperplastic Primary Vitreous

  3. Coats Disease

  4. Larval granulomatosis


8
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Coats Disease aka exudative retinitis

Leukocoria, 3-9yo


telangiectasias and aneurysms of retinal blood vessels

→ subretinal exudative fluid collections

→ RETINAL DETACHMENT


Tx:

  • ophthalmology ref

  • photocoagulation/cryotherapy/surgical repair


9
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