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Hereditary Haemorrhagic Telangiectasia
AKA
Osler-Weber-Rendu Syndrome
Skin/Mucosal manifestation
nasal telangiectasia-nose bleed
skin/oral cavity/conjunctival telangiectasia
Liver manifestation
AVMs in liver
massively dilated hepatic artery
→portal HTN
→high output heart failure
Lung manifestation
AVMs in lung
→paradoxical & septic emboli
→brain abscess
GI manifestation
AVM
angiodysplasia
CNS manifestation
AVM
aneurysm