Pediatric Genitourinary/Gastrointestinal Disorders

0.0(0)
studied byStudied by 0 people
learnLearn
examPractice Test
spaced repetitionSpaced Repetition
heart puzzleMatch
flashcardsFlashcards
Card Sorting

1/33

flashcard set

Earn XP

Description and Tags

Study Analytics
Name
Mastery
Learn
Test
Matching
Spaced

No study sessions yet.

34 Terms

1
New cards

Pediatric Kidneys

  • Kidneys are large and not well-protected from trauma.

  • Shorter urethra in girls increases the risk of infection.

  • Slower glomerular filtration rate → kidneys are less efficient at regulating fluid, electrolyte, and acid/base balance.

  • Smaller bladder capacity:

    • Infants: 20 cc to 50 cc

    • Adults: 700 cc

  • Urine Output:

    • Infants: 2 mL/kg/hr

    • Older Children: 0.5 to 1 mL/kg/hr

  • The renal system reaches maturity at 2 years of age.

2
New cards

Urine Collection in Pediatric Patients

  • Always discuss and obtain permission for the procedure with a caregiver before catheterization.

  • Involve Child Life Services (CLS) for older children before invasive urine collection techniques.

  • Urine Bag:

    • Appropriate for infants and toddlers.

    • May be sterile or clear for urinalysis (UA).

  • Straight Catheterization:

    • Used for urinalysis (UA).

    • In most cases of retention or obstruction, this technique is the same as in adult patients but may be difficult due to smaller anatomy and patient cooperation.

<ul><li><p>Always discuss and obtain permission for the procedure with a caregiver before catheterization.</p></li><li><p class="">Involve Child Life Services (CLS) for older children before invasive urine collection techniques.</p></li><li><p class=""><strong>Urine Bag:</strong></p><ul><li><p class="">Appropriate for infants and toddlers.</p></li><li><p class="">May be sterile or clear for urinalysis (UA).</p></li></ul></li><li><p class=""><strong>Straight Catheterization:</strong></p><ul><li><p class="">Used for urinalysis (UA).</p></li><li><p class="">In most cases of retention or obstruction, this technique is the same as in adult patients but may be difficult due to smaller anatomy and patient cooperation.</p></li></ul></li></ul><p></p>
3
New cards

Urinary Tract Infection (UTI)

  • An infection of the urinary tract, most commonly the bladder, caused by bacterial transmission via the urethra.

  • Females are at an increased risk due to their shorter urethra length and the proximity of the urethra to the vagina and anus.

  • Infant Symptoms:

    • Irritability

    • Fever

    • Poor feeding

    • Vomiting

    • Jaundice

  • Children Symptoms:

    • Fever

    • Vomiting

    • Dysuria

    • Incontinence

    • Urinary hesitancy and urgency

    • Hematuria

    • Abdominal pain

    • Flank pain

    • Foul-smelling urine

  • If left untreated → pyelonephritis, urosepsis, renal scarring, and hydronephrosis.

  • Diagnostic Tests: Urinalysis (UA) with reflux to culture.

    • UA: Positive for blood, nitrates, leukocyte esterase, white blood cells, or bacteria.

    • Culture: Will reveal the infecting organism.

4
New cards

UTI: Nursing Care

Most patients will manage this at home; care surrounds education for prevention and treatment:

  • Ensure adequate hydration.

  • Avoid:

    • Urinary retention

    • Frequent bathroom breaks (*note for school-aged child).

  • Females:

    • No bubble baths or soap application to the vulva.

    • Wipe front to back.

    • Cotton underwear.

    • Change pads/tampons frequently during menstruation.

    • Void after intercourse.

  • Complete full course of antibiotics and return to PCP for re-check.

  • Pain Management:

    • Acetaminophen.

    • Ibuprofen.

    • Small children may void in a warm bath or with a heating pad.

  • Hospital Admission Criteria & Care:

    • Criteria: Infant <2 months—s/sx: urosepsis, immunocompromised patient, inability to tolerate oral medications.

    • Care: Administer antibiotic therapy, hydrate via oral or IV fluids, pain management, and antipyretic PRN.

5
New cards

What are Some Structural Urinary Disorders?

  • Hypospadias/Epispadias

  • Vesicoureteral Reflux

6
New cards

Hypospadias/Epispadias

Hypospadias:

  • A congenital anomaly of the male urethra, foreskin, and penis leading to the abnormal ventral placement of the urethral opening.

Epispadias:

  • A defect in which the urethral opening is on the dorsal surface of the penis.

Abnormal displacement has the potential to cause developmental or functional issues:

  • Deflection of the urinary stream.

  • Inability to urinate standing.

  • Erectile dysfunction causing intercourse difficulties.

  • Problems with fertility due to improper deposition of sperm.

Circumcision is contraindicated before surgical repair.

<p><strong>Hypospadias:</strong></p><ul><li><p class="">A congenital anomaly of the male urethra, foreskin, and penis leading to the abnormal <strong><u>ventral</u></strong> placement of the urethral opening.</p></li></ul><p class=""><strong>Epispadias:</strong></p><ul><li><p class="">A defect in which the urethral opening is on the <strong><u>dorsal</u></strong> surface of the penis.</p></li></ul><p class=""><strong>Abnormal displacement has the potential to cause developmental or functional issues</strong>:</p><ul><li><p class="">Deflection of the urinary stream.</p></li><li><p class="">Inability to urinate standing.</p></li><li><p class="">Erectile dysfunction causing intercourse difficulties.</p></li><li><p class="">Problems with fertility due to improper deposition of sperm.</p></li></ul><p class=""><strong>Circumcision is contraindicated before surgical repair.</strong></p>
7
New cards

Hypospadias/Epispadias: Nursing Care

Surgical repair occurs 6 to 12 months of age and is usually outpatient.

Post-Operative Care—Caregiver Support and Education Surrounding:

  • Pain Medication Administration:

    • Analgesics (acetaminophen, ibuprofen)

    • Antispasmodics (oxybutynin).

  • Antibiotics are given post-op to prevent infection while the catheter is in place.

  • Surgical site care: Dressing stays in place for 3 days; soak it off; may apply Vaseline to outer diapers once the dressing comes off.

  • Double-diapering and catheter care.

  • When to call the provider or go to the ED: Fever, excessive bleeding, inconsolable pain, change in urine output.

<p><strong>Surgical repair occurs 6 to 12 months of age and is usually outpatient.</strong></p><p class=""><strong>Post-Operative Care—Caregiver Support and Education Surrounding:</strong></p><ul><li><p class=""><strong>Pain Medication Administration:</strong> </p><ul><li><p class="">Analgesics (acetaminophen, ibuprofen)</p></li><li><p class="">Antispasmodics (oxybutynin).</p></li></ul></li><li><p class=""><strong>Antibiotics</strong> are given post-op to prevent infection while the catheter is in place.</p></li><li><p class=""><strong>Surgical site care:</strong> Dressing stays in place for 3 days; soak it off; may apply Vaseline to outer diapers once the dressing comes off.</p></li><li><p class=""><strong>Double-diapering and catheter care.</strong></p></li><li><p class=""><strong>When to call the provider or go to the ED:</strong> Fever, excessive bleeding, inconsolable pain, change in urine output.</p></li></ul><p></p>
8
New cards

Vesicoureteral Reflux (VUR)

Retrograde passage of urine from the bladder into the upper urinary tract → renal scarring.

Potential for renal insufficiency or failure later in life.

Primary:

  • Congenital abnormality → Inadequate closure of the uretrovesical junction → Failure of the anti-reflux mechanism.

Secondary:

  • Result of high pressure in the bladder → failure of the uretrovesical junction to close.

  • May be caused by neurogenic bladder, obstruction, or dysfunction of the bladder.

Diagnostic Test:

  • Voiding Cystourethrogram (VCUG).

Grading:

  • Severity is graded on a I to V scale.

  • Grades III to V are associated with recurrent UTIs, hydronephrosis, and renal injury.

9
New cards

Vesicoureteral Reflux (VUR): Nursing Care

Daily administration of prophylactic antibiotics until VUR is resolved, either spontaneously or surgically.

Educate the child and caregiver about:

  • Proper toileting

  • Perineal hygiene

  • The need for regular urine testing and Voiding Cystourethrogram (VCUGs).

Post-Operative Care:

  • IVFs—1.5 maintenance rate to promote urinary output.

  • Strict I & Os.

  • Foley and stents may be in place—urine will be bloody for 2 to 3 days post-op.

  • Administer analgesics and antispasmodics.

  • Ambulate and advance diet as tolerated.

<p><strong>Daily administration of prophylactic antibiotics until VUR is resolved, either spontaneously or surgically.</strong></p><p class=""><strong>Educate the child and caregiver about:</strong></p><ul><li><p class="">Proper toileting</p></li><li><p class="">Perineal hygiene</p></li><li><p class="">The need for regular urine testing and Voiding Cystourethrogram (VCUGs).</p></li></ul><p class=""><strong>Post-Operative Care:</strong></p><ul><li><p class="">IVFs—1.5 maintenance rate to promote urinary output.</p></li><li><p class="">Strict I &amp; Os.</p></li><li><p class="">Foley and stents may be in place—urine will be bloody for 2 to 3 days post-op.</p></li><li><p class="">Administer analgesics and antispasmodics.</p></li><li><p class="">Ambulate and advance diet as tolerated.</p></li></ul><p></p>
10
New cards

What are Some Acquired Urinary Disorders?

  • Nephrotic Syndrome

  • Post-Streptococcal Glomerulonephritis

  • Hemolytic Uremic Syndrome (HUS)

11
New cards

Nephrotic Syndrome

  • Increased permeability across the glomerular filtration barrier → plasma protein through the basement membrane → loss of protein in the urine and decreased protein and albumin in the serum.

  • Hypoalbuminemia → a change in osmotic pressure → fluid shifts into interstitial tissue → shift in volume prompts kidneys to conserve water and sodium → edema.

  • Primary:

    • This syndrome occurs in the absence of disease.

    • It includes idiopathic nephrotic syndrome, which is the most common form (90% of patients).

  • Secondary:

    • This syndrome is associated with disease or is secondary to another process that causes glomerular injury (e.g., SLE, Henoch-Schonlein Purpura, Sickle Cell Disease, Infective Endocarditis).

  • Signs & Symptoms:

    • Nephrotic-range proteinuria—urinary protein excretion greater than 50 mg/kg per day.

    • Hypoalbuminemia—serum albumin concentration less than 3 g/dL (30 g/L).

    • Edema (generalized—anasarca).

    • Hyperlipidemia.

<ul><li><p>Increased permeability across the glomerular filtration barrier → plasma protein through the basement membrane → loss of protein in the urine and decreased protein and albumin in the serum.</p></li><li><p class="">Hypoalbuminemia → a change in osmotic pressure → fluid shifts into interstitial tissue → shift in volume prompts kidneys to conserve water and sodium → edema.</p></li><li><p class=""><strong>Primary:</strong></p><ul><li><p class="">This syndrome occurs in the absence of disease.</p></li><li><p class="">It includes idiopathic nephrotic syndrome, which is the most common form (90% of patients).</p></li></ul></li><li><p class=""><strong>Secondary:</strong></p><ul><li><p class="">This syndrome is associated with disease or is secondary to another process that causes glomerular injury (e.g., SLE, Henoch-Schonlein Purpura, Sickle Cell Disease, Infective Endocarditis).</p></li></ul></li><li><p class=""><strong>Signs &amp; Symptoms:</strong></p><ul><li><p class=""><strong>Nephrotic-range proteinuria</strong>—urinary protein excretion greater than 50 mg/kg per day.</p></li><li><p class=""><strong>Hypoalbuminemia</strong>—serum albumin concentration less than 3 g/dL (30 g/L).</p></li><li><p class=""><strong>Edema </strong>(generalized—anasarca).</p></li><li><p class=""><strong>Hyperlipidemia</strong>.</p></li></ul><p></p></li></ul><p></p>
12
New cards

Nephrotic Syndrome: Nursing Care

Promote Diuresis:

  • Administer corticosteroids (prednisone) and diuretics (furosemide) as ordered.

  • Daily weights.

  • Monitor urine output and proteinuria.

  • Regular assessment of vital signs and edema.

  • Administer albumin as ordered for severe hypoalbuminemia.

Prevent Infection:

  • Give prophylactic antibiotics as ordered.

  • Vaccine administration—pneumococcal and varicella.

  • Avoid live vaccines during steroid treatment.

Nutrition:

  • May require fluid and salt restriction.

  • Encourage foods high in protein and potassium (if low from diuretics).

Child & Caregiver Support and Education:

  • Surrounding the course of treatment and preventing relapse by adhering to the treatment plan.

  • Teach how to check for proteinuria via urine dipstick.

  • Offer supportive resources to children distressed with appearance.

13
New cards

Post-Streptococcal Glomerulonephritis

An immune complex disease that occurs after an infection.

Infection → immunologic response → glomerular inflammation and injury → can lead to uremia and renal failure.

Signs & Symptoms:

  • Recent infection (viral URI, strep)

  • Fatigue

  • Proteinuria

  • Hematuria

  • Decreased glomerular filtration rate

  • Retention of sodium and water → edema & hypertension

Nursing Care:

  • Antibiotic therapy if strep infection is present.

  • Monitor and manage hypertension with antihypertensives (e.g., labetalol) and diuretics.

  • Sodium and water restriction.

  • Strict I & Os.

  • Cluster care to allow for rest.

  • May require dialysis for life-threatening fluid overload refractory to treatment, uremia, elevated K+ resistant to treatment.

14
New cards

Hemolytic Uremic Syndrome (HUS)

Three defining features of HUS:

  • Hemolytic Anemia

  • Thrombocytopenia

  • Acute Renal Failure

Acquired HUS:

  • Shiga toxin-producing E. coli (STEC): 90% of pediatric cases of HUS.

    • Ex: Undercooked beef, feces, certain animals, unpasteurized dairy.

    • Signs & Symptoms: Begins 5 to 10 days after diarrhea onset.

      • Abdominal pain

      • Vomiting

      • Diarrhea (bloody)

      • Hematuria

  • Streptococcus pneumoniae: 5% to 15% of pediatric cases of HUS.

    • Develops following a pneumococcal infection; the pneumococcal vaccine is protective against many strains.
      Initial disease in patients is more severe (higher mortality rate) than in patients with STEC.

    • Signs & Symptoms:

      • Pneumonia

      • Usually with empyema (collection of pus outside the lungs) or effusion

      • Dyspnea

      • Respiratory distress

      • Fever

      • Cough

  • Patients may progress to severe AKI or renal failure; 50% of patients will need dialysis.

  • Neurologic Signs & Symptoms (can be seen in about 20% of patients):

    • Altered mental status

    • Seizures

    • Coma

    • Stroke

15
New cards

HUS: Nursing Care

Care is Supportive:

Anemia:

  • Slow infusion of PRBCs (for Hgb <6) over 3 to 4 hours to prevent fluid overload.

Thrombocytopenia:

  • PLT transfusion if significant bleeding is present.

Maintain Appropriate Fluid Balance:

  • This is tricky as patients with HUS may have increased (oliguria or anuria) or decreased (vomiting, diarrhea) intravascular volume.

    • If decreased intravascular volume—administer fluids to restore euvolemic state.

    • If increased intravascular volume—administer diuretics and antihypertensives as ordered.

Monitor Kidney Function, Prevent Further Injury:

  • Labs—CBC, CRT, BUN, electrolytes

  • Avoid administration of nephrotoxic medications.

Manage HTN:

  • Restore euvolemia, administer diuretics or antihypertensives as ordered.

Patient May Require:

  • Education should be given surrounding the risk of transmission (STEC is shed for 7 days; longer in younger patients for 3 weeks).

16
New cards

Gastrointestinal Disorders in Children

Upper GI Tract:

  • The lower esophageal sphincter is fully developed at 1 month of age.

  • Stomach capacity is 200 mL, with gastric emptying faster than in adults.

  • Adults: 2,000 mL to 3,000 mL capacity.

Lower GI Tract:

  • The small intestine is 250 cm vs 600 cm in adults.

  • Healthy infants have a faster intestinal transit time than adults.

  • The liver is ½ the size of the abdominal cavity, and the edge may be palpable on examination 2 cm to 4 cm below the right costal margin.

  • Immature neuromuscular function often causes stooling after eating as a result of gastrocolic reflux.

  • By 2 years of age, voluntary control of bowel movements occurs.

  • Meconium is the first stool and appears black in color, sticky.

<p><strong>Upper GI Tract:</strong></p><ul><li><p class="">The lower esophageal sphincter is fully developed at 1 month of age.</p></li><li><p class="">Stomach capacity is 200 mL, with gastric emptying faster than in adults.</p></li><li><p class=""><strong>Adults</strong>: 2,000 mL to 3,000 mL capacity.</p></li></ul><p class=""><strong>Lower GI Tract:</strong></p><ul><li><p class="">The small intestine is 250 cm vs 600 cm in adults.</p></li><li><p class="">Healthy infants have a faster intestinal transit time than adults.</p></li><li><p class="">The liver is ½ the size of the abdominal cavity, and the edge may be palpable on examination 2 cm to 4 cm below the right costal margin.</p></li><li><p class="">Immature neuromuscular function often causes stooling after eating as a result of gastrocolic reflux. </p></li><li><p class="">By 2 years of age, voluntary control of bowel movements occurs.</p></li><li><p class="">Meconium is the first stool and appears black in color, sticky.</p></li></ul><p></p>
17
New cards

Gastroesophageal Reflux Disease (GERD)

Gastroesophageal Reflux:

  • Passage of gastric contents into the esophagus (regurgitation or ‘spitting up’).

  • Frequent in infants <12 months (30x/day).

  • Physiologic in all ages until it causes symptoms of esophageal injury or complications → referred to as GERD.

Gastroesophageal Reflux Disease (GERD):

  • Signs & Symptoms:

    • May be vague and include—poor weight gain (FTT—failure to thrive), feeding refusal, irritability, respiratory symptoms (cough, wheezing), neck or back arching, heme + stools.

    • Underlying causes must be ruled out before diagnosis (e.g., food allergies, malrotation, neurologic impairment).

  • Conditions Associated with GERD:

    • Obesity

    • Cystic Fibrosis (CF)

    • Neurologic Impairment

    • Prematurity

    • Hiatal hernia

    • Achalasia

18
New cards

GERD: Nursing Care

Administering Feedings:

  • Elevate the head or the head of the bed.

  • Keep the infant upright for at least 30 minutes after feedings.

  • Offer smaller, more frequent feedings; avoid overfeeding.

  • Thicken feeds (e.g., oat cereal).

Other Modalities:

  • GERD should resolve spontaneously as the infant grows.

  • However, with moderate to severe cases, the infant may require medication.

    • PPI: Omeprazole

    • H2 Receptor Antagonist: Famotidine

  • Nissen fundoplication is reserved for infants with severe GERD, refractory to the treatment above.

<p><strong>Administering Feedings:</strong></p><ul><li><p class="">Elevate the head or the head of the bed.</p></li><li><p class="">Keep the infant upright for at least 30 minutes after feedings.</p></li><li><p class="">Offer smaller, more frequent feedings; avoid overfeeding.</p></li><li><p class="">Thicken feeds (e.g., oat cereal).</p></li></ul><p class=""><strong>Other Modalities:</strong></p><ul><li><p class="">GERD should resolve spontaneously as the infant grows.</p></li><li><p class="">However, with moderate to severe cases, the infant may require medication.</p><ul><li><p class=""><strong>PPI:</strong> Omeprazole</p></li><li><p class=""><strong>H2 Receptor Antagonist:</strong> Famotidine</p></li></ul></li><li><p class="">Nissen fundoplication is reserved for infants with severe GERD, refractory to the treatment above.</p></li></ul><p></p>
19
New cards

Esophageal Atresia & Tracheoesophageal Fistula (EA/TEF)

  • Congenital anomaly caused by a defect in the lateral section of the foregut into the esophagus and trachea (the trachea and esophagus do not separate normally during development).

  • Clinical presentation of TEF depends on the presence of EA.

  • EA: Proximal and distal ends of the esophagus do not communicate (blind pouch).

  • Signs & Symptoms (present after birth):

    • Drooling

    • Choking

    • Coughing

    • Cyanosis

    • Respiratory distress

    • Inability to feed (aspiration)

    • NGT coiled in the esophagus (cannot pass)

    • Abdominal distension

  • 50% of cases have associated anomalies (VACTERAL association or CHARGE syndrome).

  • Diagnostic Tests:

    • Chest X-ray

    • UGI series

<ul><li><p>Congenital anomaly caused by a defect in the lateral section of the foregut into the esophagus and trachea (the trachea and esophagus do not separate normally during development).</p></li><li><p class="">Clinical presentation of TEF depends on the presence of EA.</p></li><li><p class=""><strong>EA:</strong> Proximal and distal ends of the esophagus do not communicate (blind pouch).</p></li><li><p class=""><strong>Signs &amp; Symptoms</strong> (present after birth):</p><ul><li><p class="">Drooling</p></li><li><p class="">Choking</p></li><li><p class="">Coughing</p></li><li><p class="">Cyanosis</p></li><li><p class="">Respiratory distress</p></li><li><p class="">Inability to feed (aspiration)</p></li><li><p class="">NGT coiled in the esophagus (cannot pass)</p></li><li><p class="">Abdominal distension</p></li></ul></li><li><p class="">50% of cases have associated anomalies (VACTERAL association or CHARGE syndrome).</p></li><li><p class=""><strong>Diagnostic Tests:</strong></p><ul><li><p class="">Chest X-ray</p></li><li><p class="">UGI series</p></li></ul></li></ul><p></p>
20
New cards

EA/TEF: Nursing Care

EA Post-Operative Care:

  • Routine post-op care

  • Administer parenteral nutrition, IV antibiotics

  • Administer PO feeds when ordered

  • Caregiver support and education:

    • Signs and symptoms to watch for and when to call the provider

    • PPI administration

    • Possibility of need for future esophageal dilations

TEF Post-Operative Care:

  • NPO, NGT/OGT to low continuous suction

  • Administration of parenteral nutrition, IVFs

  • PRN suction and oxygen

  • Comfort measures

  • Caregiver education

<p><strong>EA Post-Operative Care:</strong></p><ul><li><p class="">Routine post-op care</p></li><li><p class="">Administer parenteral nutrition, IV antibiotics</p></li><li><p class="">Administer PO feeds when ordered</p></li><li><p class=""><strong>Caregiver support and education:</strong></p><ul><li><p class="">Signs and symptoms to watch for and when to call the provider</p></li><li><p class="">PPI administration</p></li><li><p class="">Possibility of need for future esophageal dilations</p></li></ul></li></ul><p class=""><strong>TEF Post-Operative Care:</strong></p><ul><li><p class="">NPO, NGT/OGT to low continuous suction</p></li><li><p class="">Administration of parenteral nutrition, IVFs</p></li><li><p class="">PRN suction and oxygen</p></li><li><p class="">Comfort measures</p></li><li><p class="">Caregiver education</p></li></ul><p></p>
21
New cards

Cleft Lip & Palate

The most common congenital craniofacial abnormality (30% associated with genetic syndromes).

Infants are at higher risk of developing this if the mother:

  • Smokes

  • Takes certain medications

  • Is considered advanced in age

Presentation:

  • Many infants present with both cleft lip and palate (50%).

  • May present with cleft lip alone or cleft palate alone.

  • May be left-sided, right-sided, or bilateral.

Examination:

  • Cleft lip: visualized on examination.

  • Cleft palate: visualized on examination and palpated with a gloved finger.

Repair Time:

  • Cleft lip: 3 months.

  • Cleft palate: 6 months.

<p>The most common congenital craniofacial abnormality (30% associated with genetic syndromes).</p><p class=""><strong>Infants are at higher risk of developing this if the mothe</strong>r:</p><ul><li><p class="">Smokes</p></li><li><p class="">Takes certain medications</p></li><li><p class="">Is considered advanced in age</p></li></ul><p class=""><strong>Presentation:</strong></p><ul><li><p class="">Many infants present with both cleft lip and palate (50%).</p></li><li><p class="">May present with cleft lip alone or cleft palate alone.</p></li><li><p class="">May be left-sided, right-sided, or bilateral.</p></li></ul><p class=""><strong>Examination:</strong></p><ul><li><p class=""><strong>Cleft lip</strong>: visualized on examination.</p></li><li><p class=""><strong>Cleft palate</strong>: visualized on examination and palpated with a gloved finger.</p></li></ul><p class=""><strong>Repair Time:</strong></p><ul><li><p class=""><strong>Cleft lip</strong>: 3 months.</p></li><li><p class=""><strong>Cleft palat</strong>e: 6 months.</p></li></ul><p></p>
22
New cards

Cleft Lip & Palate: Nursing Care

Promote Nutrition:

  • If cleft palate is present, the infant may not be able to generate enough pressure to suck milk from the bottle or breast.

    • Adaptive equipment may be used to assist in feedings (squeezable bottle or modified nipple).

  • If cleft lip (alone) is present, the infant can feed from the bottle or breast.

  • Increased risk for aspiration with a cleft palate, so prevent this by covering the palate with a prosthodontic device.

Encourage Infant-Parent Bonding:

  • Parents may experience distress surrounding the infant's appearance and hospitalization.

  • Support parents in providing feedings and other care to the infant.

  • Provide education for anticipated surgeries.

Post-Operative Care:

  • Pain management with medication and comfort measures (holding, rocking, singing) — anticipate their needs.

  • Prevent damage to the suture line of the lip and/or palate.

  • The infant should lie supine, and may require a mitten or welcome-sleeve restraints.

  • Do not allow the infant to suck on pacifiers, plastic syringes, or straws in older children undergoing repair.

  • No oral suctioning (or keep it to a minimum).

23
New cards

Acute Viral Gastroenteritis

Intestinal Infection:

  • Destruction of enterocytes → shift of fluid into intestinal lumen → loss of fluid and salt in stool (diarrhea).

  • Intestinal injury decreases digestion and absorption.

  • Occurs in infants and children year-round.

  • Transmitted most often by the fecal-oral route by symptomatic and asymptomatic carriers.

  • Examples of infectious pathogens: rotavirus, norovirus, and enteric adenovirus.

  • Symptomatic onset depends on the virus (incubation period differs).

Primary Signs & Symptoms:

  • Diarrhea

  • Vomiting

Other Signs & Symptoms:

  • Fever

  • Abdominal pain

  • Myalgia

  • Anorexia

Patients with moderate to severe cases of this disease may experience:

  • Weight loss

  • Electrolyte imbalance

  • Tachycardia

  • Hypotension

  • Sunken fontanelle

  • Dry mucous membranes

  • Reduced skin turgor

  • Low urine output

  • Listlessness

  • Lethargy

24
New cards

Acute Viral Gastroenteritis: Nursing Care

Treatment is Supportive:

  • Fluid repletion and replacement of ongoing fluid losses.

  • Mild to moderate: Oral Rehydration Therapy (ORT).

  • Moderate to severe: IV hydration.

  • Antiemetic medications (Zofran).

Diet:

  • Complex carbs are preferred.

  • Avoid fatty or sugary foods (BRAT diet not necessary).

Monitoring:

  • Daily weights.

  • Electrolytes.

  • PO intake (strict I & Os).

Caregiver Education:

  • Diarrhea may last several days after discharge home.

  • Handwashing.

  • Signs and symptoms of when to call the provider or return to the ED.

Rotavirus Vaccine.

25
New cards

Infantile Hypertrophic Pyloric Stenosis

  • Hypertrophy of the pylorus → obstruction of gastric outlet → forceful, often projectile vomiting.

  • Occurs in early infancy between 3 to 6 weeks.

  • Vomiting occurs immediately following feeding.

  • Infants are irritable and hungry, wanting to be fed again soon after emesis.

  • Signs & Symptoms:

    • Failure to gain weight or weight loss

    • Dehydration (dry mucous membranes, no tears)

    • Hyperchloremic metabolic alkalosis

    • Palpation of ‘olive-sized’ mass in RUQ.

  • Diagnostic Tests:

    • Abdominal ultrasound will demonstrate hypertrophied pylorus.

<ul><li><p><strong>Hypertrophy of the pylorus</strong> → obstruction of gastric outlet → forceful, often projectile vomiting.</p></li><li><p>Occurs in early infancy between 3 to 6 weeks.</p></li><li><p class="">Vomiting occurs immediately following feeding.</p></li><li><p class="">Infants are irritable and hungry, wanting to be fed again soon after emesis.</p></li><li><p class=""><strong>Signs &amp; Symptoms:</strong></p><ul><li><p class="">Failure to gain weight or weight loss</p></li><li><p class="">Dehydration (dry mucous membranes, no tears)</p></li><li><p class="">Hyperchloremic metabolic alkalosis</p></li><li><p class="">Palpation of ‘olive-sized’ mass in RUQ.</p></li></ul></li><li><p class=""><strong>Diagnostic Tests:</strong></p><ul><li><p class="">Abdominal ultrasound will demonstrate hypertrophied pylorus.</p></li></ul></li></ul><p></p>
26
New cards

Infantile Hypertrophic Pyloric Stenosis: Nursing Care

Treatment is surgical: Laparoscopic Pyloromyotomy

Pre-Operative Care:

  • Administer IVFs to correct dehydration and electrolyte disturbances.

  • Bolus of NS (x1 or x2, depending on the degree of dehydration and hypochloremia).

  • MIVFs at 1.5 to 2x maintenance rate.

  • NPO before surgery.

  • Provide education and support to caregivers regarding surgery.

Post-Operative Care:

  • Resume oral feeds and continue IVFs until tolerating PO.

  • Strict I & Os.

  • Monitor surgical site.

<p><strong>Treatment is surgical: </strong>Laparoscopic Pyloromyotomy</p><p><strong>Pre-Operative Care:</strong></p><ul><li><p class="">Administer IVFs to correct dehydration and electrolyte disturbances.</p></li><li><p class="">Bolus of NS (x1 or x2, depending on the degree of dehydration and hypochloremia).</p></li><li><p class="">MIVFs at 1.5 to 2x maintenance rate.</p></li><li><p class="">NPO before surgery.</p></li><li><p class="">Provide education and support to caregivers regarding surgery.</p></li></ul><p><strong>Post-Operative Care:</strong></p><ul><li><p class="">Resume oral feeds and continue IVFs until tolerating PO.</p></li><li><p class="">Strict I &amp; Os.</p></li><li><p class="">Monitor surgical site.</p></li></ul><p></p>
27
New cards

Intussusception

The most common cause of intestinal obstruction in children 6 months to 3 years of age.

  • Bowel telescopes into a distal portion of itself. If left untreated → edema, vascular compromise, and bowel obstruction.

Classified by location:

  • Ileocolic (90%)

  • Ileo-ileal

  • Jejuno-ileal

  • Colo-colic

  • May be preceded by a viral illness (URI, AOM).

  • Most cases are idiopathic (75%), while some may have a lead point (25%).

Signs & Symptoms:

  • Sudden, crampy, intermittent abdominal pain

  • Severe abdominal pain

  • Child may draw knees to chest

  • Vomiting

  • Diarrhea

  • Lethargy

  • Currant-jelly stools** (mucus + blood)

  • Sausage-shaped mass on abdominal palpation (RUQ)

<p><strong>The most common cause of intestinal obstruction in children 6 months to 3 years of age.</strong></p><ul><li><p class="">Bowel telescopes into a distal portion of itself. If left untreated → edema, vascular compromise, and bowel obstruction.</p></li></ul><p><strong>Classified by location:</strong></p><ul><li><p class=""><strong>Ileocolic (90%)</strong></p></li><li><p class="">Ileo-ileal</p></li><li><p class="">Jejuno-ileal</p></li><li><p class="">Colo-colic</p></li><li><p class="">May be preceded by a viral illness (URI, AOM).</p></li><li><p class="">Most cases are idiopathic (75%), while some may have a lead point (25%).</p></li></ul><p><strong>Signs &amp; Symptoms:</strong></p><ul><li><p class="">Sudden, crampy, intermittent abdominal pain</p></li><li><p class="">Severe abdominal pain</p></li><li><p class="">Child may draw knees to chest</p></li><li><p class="">Vomiting</p></li><li><p class="">Diarrhea</p></li><li><p class="">Lethargy</p></li><li><p class=""><strong>Currant-jelly stools** </strong>(mucus + blood)</p></li><li><p class=""><strong>Sausage-shaped mass</strong> on abdominal palpation (RUQ)</p></li></ul><p></p>
28
New cards

Intussusception: Nursing Care

Stable Child Without Signs & Symptoms of Perforation:

  • Administer IVFs.

  • Transport to radiology for air (pneumatic) or contrast (hydrostatic) enema.

  • Educate caregivers about the procedure and the likelihood of recurrence (50% recur within the first 72 hours following nonoperative reduction).

Ill-Appearing Child, Signs & Symptoms of Bowel Perforation, or Unsuccessful Nonoperative Intervention:

  • Emergent surgical intervention (diagnostic laparoscopy and/or exploratory laparotomy).

  • Administer IVFs and antibiotics.

  • NGT decompression.

  • Post-Operative Care:

    • Important to assess for signs and symptoms of recurrence (occurs in up to 20% of patients).

  • Caregiver support and education (high likelihood of recurrence).

<p><strong>Stable Child Without Signs &amp; Symptoms of Perforation:</strong></p><ul><li><p class="">Administer IVFs.</p></li><li><p class="">Transport to radiology for air (pneumatic) or contrast (hydrostatic) enema.</p></li><li><p class="">Educate caregivers about the procedure and the likelihood of recurrence (<strong>50% recur within the first 72 hours following nonoperative reduction</strong>).</p></li></ul><p><strong>Ill-Appearing Child, Signs &amp; Symptoms of Bowel Perforation, or Unsuccessful Nonoperative Intervention:</strong></p><ul><li><p class=""><strong>Emergent surgical intervention</strong> (diagnostic laparoscopy and/or exploratory laparotomy).</p></li><li><p class="">Administer IVFs and antibiotics.</p></li><li><p class="">NGT decompression.</p></li><li><p><strong>Post-Operative Care:</strong></p><ul><li><p class="">Important to assess for signs and symptoms of recurrence (<strong>occurs in up to 20% of patients</strong>).</p></li></ul></li><li><p class="">Caregiver support and education (<strong>high likelihood of recurrence</strong>).</p></li></ul><p></p>
29
New cards

Hirschsprung Disease

  • Neural crest fails to migrate completely during intestinal development → aganglionic segment of the colon → lack of propulsion of intestinal contents (functional obstruction).

  • The aganglionic segment may be short (rectosigmoid), long (extends proximal to the sigmoid colon), or total colonic aganglionosis.

  • Outcomes are worse with long-segment disease.

  • Associated with chromosomal anomalies (e.g., Trisomy 21).

  • Hallmark sign = delay or failure to pass meconium within the first 48 hours of life.

  • Signs & Symptoms:

    • Abdominal distension

    • Poor feeding

    • Constipation

    • Bilious emesis

    • "Squirt" or "blast" sign (explosive stool after rectal exam)

Hirschsprung-Associated Enterocolitis (HAEC):

  • Bacterial overgrowth in the bowel due to stool stasis, leading to bacterial translocation through the mucosa.

  • Can occur pre- or post-operatively (most common post-op complication).

  • May lead to intestinal perforation, peritonitis, septic shock, and death.

  • Signs & Symptoms of HAEC:

    • Fever

    • Vomiting

    • Lethargy

    • Explosive and foul-smelling diarrhea

<ul><li><p>Neural crest fails to migrate completely during intestinal development → aganglionic segment of the colon → lack of propulsion of intestinal contents (functional obstruction).</p></li><li><p class="">The aganglionic segment may be short (rectosigmoid), long (extends proximal to the sigmoid colon), or total colonic aganglionosis.</p></li><li><p class="">Outcomes are worse with long-segment disease.</p></li><li><p class="">Associated with chromosomal anomalies (e.g., Trisomy 21).</p></li><li><p class=""><strong>Hallmark sign</strong> = delay or failure to pass meconium within the first 48 hours of life.</p></li><li><p><strong>Signs &amp; Symptoms</strong>:</p><ul><li><p>Abdominal distension</p></li><li><p class="">Poor feeding</p></li><li><p class="">Constipation</p></li><li><p class="">Bilious emesis</p></li><li><p class="">"Squirt" or "blast" sign (explosive stool after rectal exam)</p></li></ul></li></ul><p><strong>Hirschsprung-Associated Enterocolitis (HAEC)</strong>:</p><ul><li><p class="">Bacterial overgrowth in the bowel due to stool stasis, leading to bacterial translocation through the mucosa.</p></li><li><p class="">Can occur pre- or post-operatively (most common post-op complication).</p></li><li><p class="">May lead to intestinal perforation, peritonitis, septic shock, and death.</p></li><li><p><strong>Signs &amp; Symptoms of HAEC</strong>:</p><ul><li><p>Fever</p></li><li><p class="">Vomiting</p></li><li><p class="">Lethargy</p></li><li><p class="">Explosive and foul-smelling diarrhea</p></li></ul></li></ul><p></p>
30
New cards

Hirschsprung Disease: Nursing Care

  • Surgical correction requires resection of the affected segment of the rectum and colon, bringing the normal ganglionic bowel down to an anastomosis with the distal rectum, close to the anus.

  • It may be a laparoscopic pull-through or an open (laparotomy) pull-through; multiple surgeries may be required.

Pre-Operative Care:

  • NPO and gastric decompression with NGT

  • IVFs and IV antibiotics

  • Rectal irrigations

  • Monitor for signs and symptoms of HAEC

  • Caregiver support and education

Post-Operative Care:

  • Pain management

  • NGT decompression until the return of bowel function (ROBF)

  • Monitor for signs and symptoms of HAEC (notify provider, IV antibiotics, and irrigation will need to be started)

  • Surgical site care and ostomy assessment/site care if present

  • Caregiver support and education

<ul><li><p>Surgical correction requires resection of the affected segment of the rectum and colon, bringing the normal ganglionic bowel down to an anastomosis with the distal rectum, close to the anus.</p></li><li><p class="">It may be a laparoscopic pull-through or an open (laparotomy) pull-through; multiple surgeries may be required.</p></li></ul><p> <strong>Pre-Operative Care</strong>: </p><ul><li><p class="">NPO and gastric decompression with NGT</p></li><li><p class="">IVFs and IV antibiotics</p></li><li><p class="">Rectal irrigations</p></li><li><p class="">Monitor for signs and symptoms of HAEC</p></li><li><p class="">Caregiver support and education</p></li></ul><p> <strong>Post-Operative Care</strong>: </p><ul><li><p class="">Pain management</p></li><li><p class="">NGT decompression until the return of bowel function (ROBF)</p></li><li><p class="">Monitor for signs and symptoms of HAEC (notify provider, IV antibiotics, and irrigation will need to be started)</p></li><li><p class="">Surgical site care and ostomy assessment/site care if present</p></li><li><p class="">Caregiver support and education</p></li></ul><p></p>
31
New cards

Anorectal Malformation (Imperforate Anus)

Anal tract fails to develop:

  • A normal opening is absent → the colon empties into the perineum or towards the vagina (female patients) or into the urinary system (male patients).

  • Atresia may be present: the rectum is a blind ending with no connection or external opening.

50% to 60% of patients have an associated anomaly (VACTERL), so all newborns with this malformation need a complete VACTERL workup:

  • Vertebral—tethered cord, scoliosis, myelomeningocele

  • Anal—atresia

  • Cardiac—ASD, PDA, tetralogy of Fallot

  • GI—tracheoesophageal fistula

  • Renal anomalies—vesicoureteral reflux

  • Limb—abnormalities

<p><strong>Anal tract fails to develop</strong>:</p><ul><li><p class="">A normal opening is absent → the colon empties into the perineum or towards the vagina (female patients) or into the urinary system (male patients).</p></li><li><p class=""><strong>Atresia may be present</strong>: the rectum is a blind ending with no connection or external opening.</p></li></ul><p class=""><strong>50% to 60% of patients have an associated anomaly (VACTERL), so all newborns with this malformation need a complete VACTERL workup</strong>:</p><ul><li><p class=""><strong>Vertebral</strong>—tethered cord, scoliosis, myelomeningocele</p></li><li><p class=""><strong>Anal</strong>—atresia</p></li><li><p class=""><strong>Cardiac</strong>—ASD, PDA, tetralogy of Fallot</p></li><li><p class=""><strong>GI</strong>—tracheoesophageal fistula</p></li><li><p class=""><strong>Renal anomalies</strong>—vesicoureteral reflux</p></li><li><p class=""><strong>Limb</strong>—abnormalities</p></li></ul><p></p>
32
New cards

Anorectal Malformation (Imperforate Anus): Nursing Care

If a fistula is present:

  • Prepare and transport for diagnostic tests (ECG, chest X-ray, renal ultrasound, etc.).

  • Perform rectal dilation as ordered.

  • Provide caregiver support and education.

  • The infant will need eventual surgical repair (at 3 months), instructions on performing dilations at home, and knowledge of the signs and symptoms of inadequate dilation.

  • Provide typical newborn care.

Infants without a fistula require surgery following birth (also those with a urinary fistula or cloaca):

  1. First surgery—colostomy to divert stool and gas.

  2. Second surgery—posterior sagittal anorectoplasty.

  3. Final surgery—colostomy reversal.

Pre-Op:

  • Administer antibiotics.

  • Maintain a limited clear or breastmilk diet 24 hours before surgery.

  • Continue dilations.

Post-Op:

  • Routine post-op care (pain management, advance diet as tolerated, monitor surgical site).

  • Ostomy care (for the first and second surgeries).

  • Apply bacitracin to the surgical site.

  • Nothing per rectum (for the final surgery).

33
New cards

Gastroschisis & Omphalocele

Gastroschisis:

  • Herniation of the abdominal wall contents through a ventral abdominal wall defect, to the right of the umbilicus, with umbilical cord insertion to the left of the defect.

  • Not enclosed within a sac → exposure to amniotic fluid → thickening of herniated organs, and peel may be present.

  • Increased risk in infants of young mothers (<20) and maternal obesity.

Omphalocele:

  • Full-thickness, midline abdominal wall defect that allows evisceration of the abdominal contents into an external peritoneal sac.

  • The umbilical cord inserts into the omphalocele membrane, not the abdominal wall.

  • Pulmonary hypoplasia may be present.

  • Associated with advanced maternal age and infants with chromosomal anomalies (trisomy 13, 18, and 21; Beckwith-Wiedemann Syndrome).

  • Defects are usually larger than gastroschisis.

<p><strong>Gastroschisis:</strong></p><ul><li><p class="">Herniation of the abdominal wall contents through a ventral abdominal wall defect, to the right of the umbilicus, with umbilical cord insertion to the left of the defect.</p></li><li><p class="">Not enclosed within a sac → exposure to amniotic fluid → thickening of herniated organs, and peel may be present.</p></li><li><p class=""><strong>Increased risk in <u>infants of young mothers (&lt;20)</u> </strong>and <strong><u>maternal obesity</u></strong>.</p></li></ul><p><strong>Omphalocele:</strong></p><ul><li><p class="">Full-thickness, midline abdominal wall defect that allows evisceration of the abdominal contents into an external peritoneal sac.</p></li><li><p class="">The umbilical cord inserts into the omphalocele membrane, not the abdominal wall.</p></li><li><p class="">Pulmonary hypoplasia may be present.</p></li><li><p class="">Associated with <strong><u>advanced maternal age</u></strong> and <strong><u>infants with chromosomal anomalies</u></strong> (trisomy 13, 18, and 21; Beckwith-Wiedemann Syndrome).</p></li><li><p class="">Defects are usually larger than gastroschisis.</p></li></ul><p></p>
34
New cards

Gastroschisis & Omphalocele: Nursing Care

Gastroschisis:

  • Cover the exposed viscera with a bowel bag to maintain temperature and prevent fluid losses.

  • Observe the bowel for decreased perfusion (dusky, cool appearance).

  • Position to the left if there is concern for vascular compromise.

  • Insert an OGT and place it to suction.

  • Position the infant on the right side to reduce tension on the mesentery.

  • Resuscitate with IVF bolus, then administer MIVFs at a regular rate.

  • Administer antibiotics and maintain strict I&Os.

  • Prepare for silo replacement (staged closure) or operative intervention (primary repair).

  • Post-Operative Care:

    • Pain management.

    • OGT until return of bowel function (ROBF).

    • Advance feedings once bowel function returns.

    • Strict I&Os.

    • Monitor for signs and symptoms of abdominal compartment syndrome.

Omphalocele:

  • Cover the sac with sterile gauze or a bowel bag up to the infant’s chest.

  • Observe the bowel for decreased perfusion (dusky, cool appearance).

  • High risk for intestinal atresia.

  • Insert an OGT and place it to suction.

  • Administer IVFs and antibiotics; maintain strict I&Os.

  • ‘Paint and wait’ technique is used if the defect is too large for a primary repair or if the infant is too unstable for surgery.

    • Application of bacitracin ointment to the sac allows eschar formation, then epithelialization over time → eventual ventral hernia that can be repaired later in life.

  • Prepare for silo placement (staged closure) or operative intervention (primary repair).

  • Post-Operative Care:

    • Pain management.

    • OGT suction until ROBF.

    • Advance feedings once bowel function returns.

    • Strict I&Os.

    • Monitor for signs and symptoms of abdominal compartment syndrome.