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what is wilson's disease?
excessive accumulation of copper
how is wilson's disease inherited?
autosomal recessive
what is the mutation that causes Wilson's
mutation of the ATP7B gene on chromosome 13
what are some of the main clinical features of Wilson's disease? (7)
- Kayser-Fleischer rings
- Sunflower cataracts
- acute liver failure
- hepatitis
- cirrhosis
- haemolytic anaemia
- behavioural changes
- blue nails
what are Kayser-Fleischer rings? (2)
- brownish-gold rings around the iris
- caused by copper deposition

what are sunflower cataracts?
copper deposits affecting the lens

if wilson's disease causes liver disease, what sign could be seen?
jaundice
what is the first line treatment for Wilson's disease?
penicillamine - chelates copper