Cystic Fibrosis Kahoot Questions

Week 13 -> Dr. G

When discussing pancreatic enzymes, which digestive enzyme will be used to evaluate dose?

• Lipase

• Protease

• Amylase

• Lactase

• Lipase

What statement is most appropriate for counseling a parent of a child starting a CFTR modulator?

• Your child should take their modulator on an empty stomach.

• The provider will want to see you every 6 months for monitoring of LFTs.

• Give the modulator three times daily, at the same times every day.

• Schedule regular visits to your child’s eye doctor for cataract checks.

• Schedule regular visits to your child’s eye doctor for cataract checks.

Which of the following is true regarding cystic fibrosis?

• Cystic fibrosis is a disorder in which CFTR is not produced

• Cystic fibrosis is typically diagnosed between 18-24 years old

• Cystic fibrosis can be diagnosed by just sweat testing

• Many cystic fibrosis treatment options have orphan drug designation

• Many cystic fibrosis treatment options have orphan drug designation

Which of the following is TRUE regarding chronic antibiotic use in CF?

• Tobramycin is first line in patients attempting to become pregnant

• Azithromycin may be used in patients without P. aeruginosa

• Prep and store Colistin in the fridge for up to 1 week before administering

• Dose Azithromycin TID continuously in people colonized with P. aeruginosa

• Azithromycin may be used in patients without P. aeruginosa

Which of the following is true regarding cystic fibrosis pathophysiology?

• Cystic fibrosis leads to infertility in 98% of female patients

• Patients should supplement vitamin C due to malabsorption

• Degraded neutrophil builds up in lungs, causing inflammation and infection

• Cystic fibrosis often leads to neuropathy

• Degraded neutrophil builds up in lungs, causing inflammation and infection

What is the benefit of using ALYFTREK over other medications in its class?

• It showed substantial improvement in outcomes vs. others in its class

• It is a once daily medication

• It requires no monitoring

• Side effects were decreased by 50%

• It is a once daily medication