Diagnostic Imaging 2- Exam 3- Benign Tumors- part 3

A benign fibrosis-osseous developmental anomaly of the mesenchymal precursor of bone, manifested as a defect in Osteoblastic differentiation and maturation

Fibrous dysplasia

When does fibrous dysplasia occur

1st and 2nd demands of life

Types of fibrous dysplasia

Monoatomic form (one spot)= ribs, proximal femur, and craniofacial bones

Polyostotic form (this is Paget's)

Polyostotic with endocrine abnormalities

Signs and symptoms of fibrous dysplasia

Dependent on type of disease

Usually asymptomatic while others have pain secondary to deformity or fracture

What is Polyostotic fibrous dysplasia that has Cafe au lait spots

McCabe- Albright syndrome

-endocrine dysfunction- in early onset puberty in females

Radiological features of fibrous dysplasia

Most medullary cavities are lucent, loculated or trabeculae with thick rim of sclerosis= RIND SIGN

Thinning of Cortex, widening of shaft

INTERNAL MATRIC IS USUALLY CLOUDY= GROUND GLASS APPEARANCE

Radiological features of fibrous dysplasia in the skull

Oven ares have increased density along convexity of anterior fossa

Unilateral overgrowth of facial bones

Expansion in skull bones and ribs

Possible complications of fibrous dysplasia

Leg length discrepancy y

Shepards crook or Sabre shin deformities

Cranial nerve compromise

Protusio acetabuli

Proptosis (Bulging eyes)

Fibrous dysplasia in the femur

I'll not refer to orthopedic cause it doesn't hurt or effect the cortex

Another example of fibrous dysplasia in the proximal femur

Fibrous dysplasia showing the ground glass appearance

Example of fibrous dysplasia causing a Shepards crook deformity and explain why its not Paget's

Not Paget's because it doesn't have thickened cortex, no accentuated trabeculation and this is a kid, Paget's is in 20-40 ur old people

Difference between Enchondroma, fibrous dysplasia and simple bone cyst

Fibrous dysplasia of the skull and facial bones