HIRSCHSPRUNG’S DISEASE (AGANGLIONIC MEGACOLON)

HIRSCHPRUNG’S DISEASE

absence of ganglionic innervation to the muscle of a section of the bowel

• chronic constipation

• ribbon-like stools

Hirschsprung’s disease results in — or —

HIRSCHPRUNG’S DISEASE

occur at a greater incidence in siblings of a child with the disorder

abnormal gene on chromosome

Hirschsprung’s disease is caused by an —

6 to 12 months

symptoms in newborn

• duration of constipation

• what do parents mean by constipation

• consistency of the stool

• is the child ill in any way

careful history taking to document illness:

• assist in anorectal manometry

• assist in temporary colostomy followed by bowel repair at 12 to 18 months of age

• before surgery, the child may be prescribed daily enemas (using PNSS) to achieve bowel movements

HIRSCHSPRUNG’S DISEASE NURSING MANAGEMENT

anorectal manometry

assist in —

• temporary colostomy

• bowel repair

• 12 to 18 months

assist in — followed by — at — of age

enemas (using PNSS)

before surgery, the child may be prescribed daily — to achieve bowel movements