peds: hirschprung's disease

what is hirschprung's disease?

disorder that occurs when all or part of the large intestine has no nerves and therefore cannot function

(the affected segment of the colon cannot contract and therefore pass stool through the colon, creating an obstruction)

what is hirschprung's disease also called?

congenital aganglionic megacolon

hallmark of hirschprung's disease in newborns

failure to pass meconium within 24-48 hours after birth

how will the abdomen look in babies with hirschprung's disease?

distended

do babies with hirschprung's disease vomit?

definitely, the stool has nowhere to go

do babies with hirschprung's disease want to eat?

no

how do children with hirschprung's disease present?

chronic constipation

ribbon like stools

abdominal distension

visible peristalsis

how is hirschprung's disease confirmed?

rectal biopsy- absence of ganglion cells

do kids with hirschprung's disease have a history of diarrhea or constipation?

constipation

what type of diet do kids with hirschprung's disease need?

high protein, high calorie, low fiber

for kids with hirschprung's disease, what is often needed for before surgery?

temporary colostomy (so the stool can come out)

what might a child need to suction out the gastrointestinal secretions and prevent abdominal distention?

NG tube