Pulmonary Arterial Hypertension and Cystic Fibrosis

Specific medications, brand names, and therapeutic classes.

Ambrisentan

Letairis

Letairis therapeutic class

endothelin receptor antagonists

Bosentan

Tracleer

Tracleer therapeutic class

endothelin receptor antagonist

macitentan

Opsumit

Opsumit therapeutic class

endothelin receptor antagonist

sildenafil

Revatio

Revatio therapeutic class

phosphodiesterase-5 inhibitors

tadalafil

Adcirca

Adcirca therapeutic class

phosphodiesterase-5 inhibitor

riociguat

Adempas

Adempas therapeutic class

soluble guanylate cyclase stimulator

selexipag

Uptravi

Uptravi therapeutic class

prostacyclin receptor agonist

iloprost

Ventavis

Ventavis therapeutic class

inhaled prostacyclin

treprostinil

Tyvaso, Orenitram, Remodulin

Tyvaso therapeutic class

inhaled prostacyclin

Orenitram therapeutic class

oral prostacyclin

epoprostenol

Flolan, Veletri

Flolan therapeutic class

parenteral prostacyclins

Remodulin therapeutic class

parenteral prostacyclin

ivacaftor

Kalydeco

Kalydeco therapeutic class

potentiator

lumacaftor therapeutic class

corrector

lumacaftor/ivacaftor

Orkambi

tezacaftor therapeutic class

corrector

elexacaftor therapeutic class

corrector

Tobi

aerosolized tobramycin

Cayston

inhaled aztreonam

Arikace

inhaled liposomal amikacin

Bronchitol

inhaled mannitol

sotatercept

Winrevair

Winrevair therapeutic class

activin signaling inhibitor