Hirschsprung’s Disease (Aganglionic Megacolon)

Week 6 (MIDTERMS)

Hirschsprung’s Disease

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also called congenital megacolon or \n congenital aganglionic megacolon

Hirschsprung’s Disease

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is a form of megacolon that occurs when \n part or all of the large intestine or \n antecedent parts of the gastrointestinal \n tract have no ganglion cells and \n therefore cannot function.

Hirschsprung’s Disease

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is a condition that affects the large intestine \n (colon) and causes problems with passing \n stool.

Hirschsprung’s Disease

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it is present when a baby is born (congenital) \n and results from missing nerve cells in the \n muscles of part or all of the baby's colon.

Anorectal manometry

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is a test performed \n to evaluate patients with constipation or \n fecal incontinence. This test measures \n the pressures of the anal sphincter \n muscles, the sensation in the rectum, and \n the neural reflexes that are needed for \n normal bowel movements.

Anorectal manometry

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the doctor inflates \n a small balloon inside \n the rectum. Normally, \n the rectal muscles will \n relax. If the muscles \n don't relax, \n Hirschsprung disease \n may be the problem. \n This test is most often \n done in older children \n and adults.