RS

Haemostasis and Bleeding in Dental Practice Lecture - Dr Allameddine Allemedine

Page 1: Introduction

  • Subject: Medicine & Surgery 2023

  • Instructor: Prof. Mark Greenwood

  • Focus Area: Haematology

Page 2: Anaemia

  • Definition: Low Hemoglobin (Hb) due to decreased red cell mass

  • Normal Range:

    • Female: 110-180 g/l

    • Male: 130-180 g/l

Page 3: Normal FBC Appearance

  • Components:

    • Platelets

    • Neutrophils

    • Red cells

Page 4: Iron Deficiency Anaemia

  • Characteristics:

    • Hypochromic, microcytic red blood cells

    • Low Hemoglobin (Hb)

    • Low Mean Corpuscular Volume (MCV)

    • Low Serum Ferritin levels

Page 5: FBC - Normal Values

  • Haemoglobin:

    • Male: 130-180 g/l

    • Female: 110-180 g/l

  • Haematocrit: 0.35-0.50

  • Mean Corpuscular Volume (MCV): 77-87 fl

  • Mean Corpuscular Hemoglobin (MCH): 25-33 pg

  • White Cell Count: 4.5-10 x 10^9/l

  • Platelets: 150-400 x 10^9/l

Page 6: Terminology

  • Terms:

    • Cytosis: Too many cells

    • Paenia: Not enough cells

    • Examples:

      • Platelets: Too many = Thrombocytosis; Not enough = Thrombopaenia

Page 7: Main Types of Anaemia

  • Categories:

    • Microcytic hypochromic (Iron deficiency)

    • Normocytic (Chronic disease)

    • Macrocytic (B₁₂, Folate deficiency)

Page 8: Causes of Iron Deficiency

  • Factors:

    • Dietary Deficiency

    • Malabsorption

    • Chronic Blood Loss (GI Tract, Menorrhagia)

Page 9: B12 and Folate Deficiency

  • Impact: Leads to Macrocytic Anaemia

  • Folate Supply:

    • Approx. 4 months' supply in the body (found in leafy greens, liver, fruits)

    • Absorbed in small intestine

  • B12 Supply:

    • 2-6 years' supply in the body (found in animal proteins)

    • Requires intrinsic factor for absorption in the terminal ileum

Page 10: Folate Deficiency Causes

  • Causes Include:

    • Reduced Intake (e.g., Elderly)

    • Alcoholism

    • Increased Requirements (e.g., pregnancy, haemolysis)

    • Malabsorption (e.g., Coeliac disease)

    • Drugs (e.g., Methotrexate)

Page 11: B12 Deficiency Aetiology

  • Factors:

    • Inadequate Intake

    • Low Gastric Acid (10-30% patients post-gastrectomy)

    • Intrinsic Factor Antibodies (Pernicious Anaemia)

    • Abnormal absorption in terminal ileum

Page 12: Pernicious Anaemia

  • Definition: Malabsorption of vitamin B12 due to decreased intrinsic factor

  • Associations: Thyroid disease, Vitiligo, Addison's disease

  • Symptom: Decreased Hemoglobin (Hb)

Page 13: Diagnosis of B12 and Folate Deficiency

  • Tests:

    • Red Cell Folate Levels

    • Serum Vitamin B12 Levels, Intrinsic Factor Antibodies

  • Treatment:

    • Identify underlying cause

    • Oral Folate Replacement or lifelong injections of Vitamin B12 every 3 months

Page 14: Other Causes of Macrocytic Anaemia

  • Drug-related (e.g., Methotrexate)

  • Alcohol

  • Myelodysplasia

Page 15: Blood Transfusions

  • Recommendation: Avoid if possible

  • Indication for Transfusion: Hb < 70 g/l or symptomatic

  • Blood Matching:

    • O Rhesus negative = Universal Donor

    • AB positive = Universal Recipient

Page 16: White Cell Count

  • Normal Values: 4.5-10 x 10^9/l

Page 17: Neutrophils

  • Increase: Bacterial infections, Trauma, Surgery

  • Decrease: Viral infections, Certain drugs

Page 18: Lymphocytes

  • Increase: Viral infections, Chronic Lymphocytic Leukaemia (CLL)

  • Decrease: Steroid treatment, Systemic Lupus Erythematosus (SLE)

Page 19: Eosinophils

  • Increase: Observed in some allergic disorders

Page 20: Platelet Abnormalities

  • Normal Platelet Count: 150-400 x 10^9/l

  • Thrombocytopaenia:

    • Count <50 x 10^9/l is a concern

    • Associated with Von Willebrand's disease

Page 21: Petechiae

  • Signifies reduced number of platelets

Page 22: Causes of Petechiae

  • Primary Causes:

    • Immune Thrombocytopenia (ITP)

    • Disseminated Intravascular Coagulation (DIC)

Page 23: Additional Causes of Petechiae

  • Recent Infections

    • Infectious Mononucleosis

    • Bone Marrow Infiltration

    • Acute Leukaemia

    • Bone Marrow Failure Syndromes (e.g., Aplastic Anaemia, Myelodysplastic Syndromes)

Page 24: Sickle Cell Anaemia

  • Types:

    • Homozygote = Disease

    • Heterozygote = Trait

  • Mechanism: Cells sickle under low oxygen tension leading to infarction

Page 25: Sickle Cell Depiction

Page 26: Thalassaemias

  • Definition: Group of disorders with decreased production of one or more globin chains

  • Types: Alpha and Beta types refer to decreased Alpha and Beta chain production respectively

Page 27: Care with Sickle Cell/Thalassaemia

  • Consideration: Increased care during decreased oxygen tension, particularly in sedation/GA

Page 28: Leukaemia

  • Definition: Cancer of blood cells; type depends on affected cells (bone marrow or lymphatic system)

  • Prevalence: Most common in adults; prevalent cancer in children; some forms are now treatable

Page 29: Types of Leukaemia

  • Progression Speed:

    • Acute: Blast cells, fast progression

    • Chronic: More mature cells, slow progression

  • Cell Type Affected:

    • Lymphocytic

    • Myelogenous (affects RBC, WBC, platelets)

Page 30: Symptoms of Acute Leukaemias

  • Presentation:

    • Short history of bruising, bleeding, infection, sometimes skin rash

    • Lymphadenopathy, gingival hypertrophy, recurrent nosebleeds

Page 31: Additional Symptoms of Acute Leukaemias

  • Symptoms:

    • Fever, chills, weakness, fatigue, unintentional weight loss

    • Enlarged lymph nodes, liver, and/or spleen

Page 32: Treatment of Acute Leukaemia

  • Dependent on Subtype: Often involves clinical trials

  • Options: May include bone marrow transplantation

  • Survival: 30-70% at five years depending on leukaemia type and treatment; prognosis worse in elderly

Page 33: Bone Marrow Failure

  • Outcome: Leads to pancytopaenia

  • Myeloma: Plasma cell neoplasm leading to marrow infiltration and osteolytic deposits

Page 34: Myelodysplastic Syndrome (MDS)

  • Pathophysiology: Immature cells fail to mature into useful blood cells

  • Discovery: Often found on blood tests while asymptomatic

  • Symptoms: May present with signs of anaemia

  • Management: Control rather than treatment; use of stem cell transplants, chemotherapy, and other therapies as needed

Page 35: Multiple Myeloma

  • Characteristics: Plasma cells in bone marrow

  • Common Treatment: Nearly all patients use bisphosphonates

  • Median Age: 67 years at presentation

  • Symptoms: Anaemia, bone pain, infection, constipation, stomach issues due to hypercalcaemia

Page 36: Multiple Myeloma Findings

  • Types of Anaemia: Normochromic normocytic anaemia

  • Detection: Paraprotein (Bence Jones protein) in urine

  • Indicators: Raised ESR, non-specific

Page 37: (Empty Page)

Page 38: Lymphoma

  • Definition: Cancer of the lymphatic system

  • Types:

    • Non-Hodgkin lymphoma

    • High-grade lymphoma

    • Low-grade lymphoma

    • Hodgkin lymphoma characterized by Reed-Sternberg cells

Page 39: Symptoms of Lymphoma

  • Common Signs:

    • Painless lymph node swelling (often in neck)

    • Fever, fatigue

    • Night sweats, pruritus

    • Unexplained weight loss

Page 40: Non-Hodgkin Lymphoma (NHL)

  • Incidence: 3-4 times as common as Hodgkin’s lymphoma

  • Trend: Increasing incidence

  • Varieties: Around 50 different subtypes

  • Importance: Expert pathology service is crucial

Page 41: NHL Treatment

  • Options: Chemotherapy, radiotherapy, monoclonal antibody treatment, stem cell transplants

Page 42: Bleeding/Coagulation Problems

  • Types of Disorders: Inherited and acquired

Page 43: Bleeding Disorders

  • Categories:

    • Vascular Defects (congenital or acquired)

    • Platelet Disorders

Page 44: Coagulation Disorders

  • Examples:

    • Haemophilia A: Factor VIII replacement, DDAVP

    • Haemophilia B: Factor IX replacement

    • Anti-fibrinolytics: Tranexamic acid

Page 45: Haemophilia A

  • Characteristics: Factor VIII deficiency, X-linked inheritance

  • Symptoms: Range in severity; prolonged APTT, normal PT

  • Treatment:

    • Factor VIII replacement (or support)

    • Possible use of Desmopressin (DDAVP) in mild cases

    • Tranexamic acid may be recommended

Page 46: Haemophilia B (Christmas Disease)

  • Characteristics: Factor IX deficiency; similar inheritance to A

  • Symptoms: Range in severity; prolonged APTT, normal PT

  • Treatment: May need Factor IX; DDAVP ineffective

Page 47: von Willebrand Disease (VWD)

  • Definition: Most common inherited bleeding disorder (1% UK population)

  • Cause: Deficiency of von Willebrand Factor (vWF)

  • Inheritance: Usually autosomal dominant; can be sex-linked recessive or acquired (e.g., autoimmune disorder)

Page 48: VWD Mechanism

  • Function: vWF is present in platelets and endothelial cell walls; affects platelet adhesion and migration (primary platelet plug formation)

Page 49: VWD Subtypes

  • Range of Severity: Varying clinical significance

  • Subtypes:

    • 1: Mildest and most common (autosomal dominant)

    • 2: Normal amount of vWF but dysfunctional

    • 3: No vWF and low Factor VIII levels

Page 50: VWD Management

  • Dependent on: Severity, planned procedures, previous history, subtype

  • Possibilities: DDAVP, VWF factor replacement, Factor VIII supplementation, antifibrinolytic drugs

Page 51: Factor V Leiden Thrombophilia

  • Mechanism: Hypercoagulability due to abnormal Factor V

  • Prevalence: Affects about 5% of Europeans; inherited

Page 52: Principles of Management

  • Considerations: Range from no intervention needed to factor replacement

  • Collaboration: Maintain liaison with a haematologist

  • Local Measures: Suturing, resorbable oxidized cellulose, tranexamic acid mouthwash

Page 53: Bleeding Disorders and Medications

  • Contraindications: Avoid NSAIDs

  • Types of Bleeding Disorders: Inherited (e.g., Haemophilia A, B, von Willebrand’s Disease) and acquired (e.g., liver disease causing deficiencies in various clotting factors, anticoagulant therapy)

Page 54: Liver Problems

  • Impact: Decreased Vitamin K leads to reduced clotting factors II, VII, IX, and X

Page 55: X-linked Conditions

  • Overview: Congenital deficiencies in Factor VIII (Haemophilia A) and Factor IX (Haemophilia B)

  • Consequences: Inability to stabilize the platelet plug

Page 56: Patient Management in Haemophilia

  1. Close liaison with Haemophilia Centre

  2. DDAVP infusion for mild haemophilia

  3. Factor VIII/IX replacement for moderate/severe cases (check levels)

Page 57: Continuing Management

  1. Atraumatic techniques

  2. Local haemostatic measures

  3. Oral tranexamic acid or mouthwash

Page 58: Management of VWD Patients

  1. Liaison with Haemophilia Centre

  2. DDAVP infusion for type I VWD

  3. VWD replacement

  4. Atraumatic technique

  5. Local haemostatic measures

  6. Oral tranexamic acid or mouthwash

Page 59: Managing Low Platelet Counts

  • Approach: Determine underlying cause and assess reversibility

  • Surgery:

    • Delay non-urgent surgery if platelet count is <50 x 10^9/l

  • Functional Defects: May need treatment like platelet transfusions or DDAVP

Page 60: Management of Platelet Abnormalities

  1. Close liaison with Haemophilia Centre

  2. Potential need for platelet transfusion or DDAVP

  3. Atraumatic techniques

  4. Local haemostatic measures

  5. Oral tranexamic acid or mouthwash

Page 61: Drug Management

  • Warfarin: Maintain INR at 4 or less with local haemostatic measures

  • Heparin: Measured by APTT

  • Low Molecular Weight Heparins: Monitor as appropriate

Page 62: Direct Oral Anticoagulants (DOACs)

Page 63: Dabigatran

  • Function: Thrombin inhibitor

  • Monitoring: Not reflected in INR, linear dose-response

Page 64: Other DOACs - Rivaroxaban

  • Mechanism: Direct Factor Xa inhibitor

Page 65: DOACs - Low Risk Procedures

  • Recommendations: Safe for simple extractions, incision and drainage, perio exams, restorations with sub-gingival margins

Page 66: DOACs - Higher Risk Procedures

  • Considerations: Higher risk during complex/adjacent extractions, flap raising, gingival re-contouring, biopsies

Page 67: Higher Risk Management - Dabigatran

  • Treatment: If twice daily, miss morning dose and give evening dose >4 hours after haemostasis

Page 68: Higher Risk Management - Rivaroxaban

  • Dosage: Delay morning dose, give >4 hours post-haemostasis

Page 69: Evening Dosing for Rivaroxaban

  • Process: For evening doses, give at regular timing if >4 hours from haemostasis

Page 70: Erythrocyte Sedimentation Rate (ESR)

  • Definition: Non-specific indicator of disease presence

  • Age-dependent calculations:

    • Men: Age divided by 2

    • Women: (Age + 10) divided by 2

Page 71: Summary

  • Conclusion: Haematological issues impact dental practice; liaison with haematologist is crucial during uncertain cases.