Lipoprotein Handling_RF2025
Barts and The London School of Medicine and Dentistry
Presentation Title: Lipoprotein Handling
Presenter: Dr. Robert Formosa
Learning Objectives
Describe the structure and composition of the main classes of lipoprotein, including very-low density lipoproteins (VLDL).
Outline the process of lipogenesis and its control.
Describe the role of lipoprotein lipase.
Discuss the role of low-density lipoproteins (LDL).
Describe the contribution of LDL to atherogenesis and clinical treatments to lower serum LDL-cholesterol levels.
Discuss the significance of high-density lipoproteins (HDL).
Topics to be Covered
Overview of lipoproteins
Lipoprotein lipase
Chylomicrons
LDLs
Cholesterol & CVD
HDLs
Atherosclerosis
Summary & learning objectives
What Are Lipoproteins?
Lipoproteins are particles of proteins and lipids found in plasma.
Functions:
Transport hydrophobic lipids: triacylglycerides (TAG/TG) & cholesterol between liver, intestine, and all body tissues.
Transported TAG depends on the body’s energy needs.
Transported cholesterol is part of an extracellular pool for cells.
Consequences of Mismanagement:
Potential development of atherosclerosis, cardiovascular disease, stroke, and peripheral vascular disease.
Importance of Lipoproteins
Global Causes of Death:
Cardiovascular diseases rank high among causes of death from 2000 to 2019.
Risk Factors:
Behavioral: Alcohol & drug use, dietary risks, tobacco smoke, low physical activity.
Metabolic: High body mass index, high systolic blood pressure, high total cholesterol, high fasting plasma glucose.
Environmental: Air pollution and various diseases (cirrhosis, diabetes, cancers).
Lipoprotein Overview
Majority of fatty acids come from diet in forms of triglycerides (90%), cholesterol, cholesterol esters, phospholipids, or free fatty acids.
Fatty acids can be synthesized in the liver during periods of excess energy intake.
Triglycerides and cholesterol are hydrophobic and cannot be transported in blood directly; they must be packaged in lipoprotein coats.
Lipoprotein Structure:
Outer Coat (Hydrophilic):
Phospholipids (amphiphatic), free cholesterol, and apoproteins.
Inner Core (Hydrophobic):
Contains cholesterol, cholesterol esters, triglycerides, and some vitamins (A and E).
Classes of Lipoproteins
Lipoproteins serve as transport systems for fats and cholesterols across various body systems, differing in size, fat content, and apoprotein types.
Key Lipoprotein Classes:
Chylomicrons: Formed in the gut, transport lipids from the GI to peripheral tissues.
VLDL: Formed in the liver, distribute triglycerides to peripheral tissues.
IDL: Result from partially absorbed VLDLs.
LDL: Deliver cholesterol from liver to peripheral cells.
HDL: Scavengers of excess cholesterol, returning it to the liver.
Chylomicron Metabolism
Chylomicrons are formed from absorbed fats and cholesterol in the GI tract, moving to the lymphatic system before entering blood.
Interact with HDL to receive ApoC2 and ApoE, crucial for determining their fate.
Functionality:
ApoC2: Activates triglyceride donation to peripheral cells.
ApoE: Permits remnant uptake by the liver.
VLDL Formation
Similar to chylomicron formation; produced in the liver and requires proteins from HDL.
VLDL remnants either re-absorbed by the liver or develop into LDL.
Lipoprotein Lipase (LPL)
Acts as the primary regulator for triglyceride transfer from VLDL and chylomicrons to target cells.
Functionality:
Breaks down triglycerides in chylomicrons and VLDLs into free fatty acids for cellular uptake.
Activity Regulation:
Highest in muscle during starvation (energy use) and in adipose cells post-meal (fat storage).
Low-Density Lipoproteins (LDL)
Function to deliver cholesterol to peripheral cells, formed as remnants of VLDL after triglyceride distribution.
IDLs transition to LDL via hepatic TAG ligase action.
Key Component:
ApoB100 enables receptor-mediated endocytosis in target cells.
Cholesterol Overview
Fundamental for cell membranes, steroid hormone biosynthesis, and bile acid formation.
Cells can synthesize cholesterol from acetyl CoA via HMG-CoA reductase.
Regulation:
High cholesterol levels induce negative feedback to reduce synthesis and uptake.
Cholesterol & Fat Metabolism Pathways
Key enzymes in the metabolic pathway from Acetyl-CoA to cholesterol.
High-Density Lipoprotein (HDL)
Functions include apoprotein exchange and reverse cholesterol transport.
Formation:
Produced by the liver as precursors (ApoA1 rich) that collect excess cholesterol from peripheral cells.
Delivers excess cholesterol esters back to liver via scavenger receptors.
Summary of Lipoproteins and Cardiovascular Disease
Role of LDL: Associated with increased cardiovascular disease risk; HDL considered protective.
Lifestyle choices impact CVD risk due to ratios of HDL to LDL.
Key Learning Points
Understand the mechanics of lipoprotein transport and regulation in the body.
Recognize the distinct functions of chylomicrons, VLDLs, IDLs, LDLs, and HDLs.
Recognize the role of lipoprotein lipase and cholesterol synthesis pathways in maintaining lipid homeostasis.
Familial Hypercholesterolemia
Condition Description: Autosomal dominant genetic disease with mutations affecting LDL receptor pathways, leading to elevated cholesterol and increased cardiovascular risk.
Impact: Increased LDL in the blood heightens chances for coronary heart disease (CHD).
Atherosclerosis and LDL Pathology
Process involving LDL oxidation, macrophage accumulation, and plaque formation, potentially culminating in cardiovascular events.