Organization, Cellular Components, and Topography of the CNS

ORGANIZATION, CELLULAR COMPONENTS, AND TOPOGRAPHY OF THE CNS

MODULE 1, PART 1

INTRODUCTION

  • How does the Nervous System work?

    • Begins with the Neuron.

    • Neurons:

    • Respond to stimuli.

    • Convey signals.

    • Process neurological information.

    • Neurological signals (impulses) enable:

    • Awareness of “self.”

    • Memory.

    • Learning.

    • Speech.

    • Muscle coordination.

    • Glandular secretion.

NERVOUS CIRCUITS

  • Types of nervous circuits:

    • Sensory circuit:

    • Initiated by sensory stimulus.

    • Reflex circuit:

    • Involves a movement or response (e.g., secretion).

    • Relay circuit:

    • Leads to sensory perception from sensory stimuli.

    • Overlapping circuits can combine elements from the above types to enhance response mechanisms.

FUNCTIONAL PATHS

  • Functional paths consist of numerous nerve cell bodies and axons.

  • Nerve cell bodies:

    • May form groupings known as nuclei or ganglia.

  • Axons in a functional path typically form bundles termed tracts, fasciculi, or nerves.

  • The nervous system includes functional paths where neuronal cell bodies reside in nuclei, ganglia, or laminae, with axons in tracts or nerves.

CENTRAL NERVOUS SYSTEM VS. PERIPHERAL NERVOUS SYSTEM

  • Central Nervous System (CNS):

    • Comprises the brain and spinal cord.

  • Peripheral Nervous System (PNS):

    • Comprises cranial nerves, spinal nerves, autonomic nerves, and their ganglia.

CNS VS PNS CONT.

  • Functions of the CNS:

    • Integrates, processes, and controls the entire nervous system.

    • Receives input about changes in the internal and external environments.

    • Interprets and integrates information.

    • Provides output signals for activities such as movement or secretion.

  • Functions of the PNS:

    • Connects the CNS to body tissues and organs.

    • Responsible for conveying input and output signals to and from the CNS.

    • Signals going to the CNS are termed Afferent (A for “Arriving” at the spinal cord; Sensory).

    • Signals departing the CNS are termed Efferent (E for “Exiting” the spinal cord; Motor).

SUPPORT AND PROTECTION

  • Protection of the CNS:

    • The brain is safeguarded by the skull.

    • The spinal cord is shielded by vertebrae.

    • All of the CNS is enveloped by meninges.

MENINGES

  • The meninges consist of three layers (superficial to deep):

    • Dura mater:

    • Outermost layer; strong and fibrous.

    • Consists of two layers with a venous sinus between them.

    • Includes Dural Folds:

      • Falx cerebri: longitudinally separates cerebral hemispheres.

      • Falx cerebelli: longitudinally separates cerebellar hemispheres.

      • Tentorium cerebelli: separates the posterior cerebral hemispheres from the cerebellum.

      • Diaphragm sellae: covers the sella turcica where the pituitary gland resides.

    • Arachnoid:

    • Thin, delicate layer surrounding the brain and spinal cord with cobweb-like projections (trabeculae) connecting to the pia mater.

    • Pia mater:

    • Thin, highly vascular layer.

    • Contains small blood vessels supplying the brain and spinal cord.

MENINGEAL SPACES

  • Epidural space: Located between the bone and the dura mater.

  • Subdural space: Found between the dura and arachnoid layers.

  • Subarachnoid space: Located between the arachnoid and pia mater; contains Cerebrospinal fluid (CSF).

    • In case of trauma to the head, blood vessels passing through these spaces may tear, leading to a hematoma.

    • Pooling of blood between the dura and arachnoid layer results in a subdural hematoma.

CLINICAL CONNECTION

  • Viral or Bacterial Meningitis:

    • Potentially life-threatening; causes inflammation of meningeal layers.

    • Signs & Symptoms (S/S):

      • Neck stiffness (nuchal rigidity).

      • Headache.

      • Fever.

      • Altered consciousness.

      • Vomiting.

      • Aversion to bright light or loud noises.

      • In children, potential for deafness.

    • Diagnosis: Conducted via lumbar puncture if no elevated intracranial pressure is present.

SUPPORTING CELLS IN THE CNS

  • Astrocytes:

    • Exclusive to the CNS; most numerous cells in the CNS.

    • Form the glial membrane and surround capillaries.

    • After injuries (ischemia, trauma), astrocytes can form scars that impair their functional capacity.

  • Endothelial cells:

    • Form the blood-brain barrier (BBB), selectively regulating substances entering the CNS.

  • Oligodendrocytes:

    • Exclusive to the CNS; responsible for formation and maintenance of myelin in the CNS.

    • Wrap around nerves, facilitating rapid transmission of nerve impulses and supporting CNS nerves.

    • Disorders such as multiple sclerosis (MS) involve autoimmune attacks on myelin sheaths.

SUPPORTING CELLS IN THE PNS

  • Schwann cells:

    • Unique to the PNS; perform functions similar to oligodendrocytes but only in the PNS.

    • Small gaps between Schwann cell wrappings are referred to as Nodes of Ranvier.

    • Autoimmune reactions (e.g., Guillain-Barre Syndrome) attack PNS myelin.

    • Regeneration ability:

    • If an axon is severed, it can regrow unmyelinated immature rootlets to reconnect the two ends of the cut nerve.

    • Note: Axonal regeneration is restricted to the PNS (not the CNS).

NEURONS

  • Neurons:

    • Smallest functional unit of the nervous system.

    • Composed of:

    • Cell body: Contains the nucleus and cytoplasm (including mitochondria).

    • Dendrites.

    • Axon.

    • The area devoid of rough endoplasmic reticulum (Nissl bodies) is termed the Axon Hillock.

    • For comparisons of axon and dendrite functions, refer to Table 1-1 in the textbook.

3 MAIN CLASSIFICATIONS OF NEURONS

  1. Unipolar neurons:

    • Located in ganglia of spinal nerves.

    • Physiological dendrites; cell body positioned between dendrite and axon.

  2. Bipolar neurons:

    • Operate as sensory nerves.

    • Possess true dendrites; cell body situated between dendrite and axon.

  3. Multipolar neurons:

    • Comprise the majority of nerve cells.

    • Multiple dendrites interfacing directly with the cell body, with impulses sent down the axon.

RESTING CELL MEMBRANE POTENTIAL

  • Ion distribution:

    • Na+ (sodium) ions predominantly extracellular (outside the cell).

    • K+ (potassium) ions predominantly intracellular (inside the cell).

  • Ion channels: Allow passive flow of Na+ and K+ ions across the cell membrane.

  • Resting membrane potential determined by the concentrations of Na+ enclosed with the cell and K+ outside, along with the activity of the Na+/K+ pump (which requires ATP).

    • The pump moves 3 Na+ ions out and 2 K+ ions into the cell with each cycle.

ACTION POTENTIALS OF NEURONS

  • Action potentials initiate when a membrane threshold is attained, leading to the opening of Na+ channels along the cell membrane.

  • This allows for an influx of sodium ions into the cell, resulting in depolarization (increase in positive charge).

  • Depolarization and repolarization propagate in one direction down the axon toward the terminal branches or synapse.

    • Speed increases with axon diameter and myelination.

MYELINATED VS UNMYELINATED NEURONS

  • Myelinated neurons:

    • Exhibit faster conduction speeds of nerve impulses.

    • Thicker myelin sheaths (larger diameters) result in expedited impulse conduction.

    • Myelination enables Saltatory Conduction, where impulses can “jump” between nodes on the axon.

  • Unmyelinated neurons:

    • Typically possess smaller diameters; impulse transmission is slower.

    • In this case, impulses undergo nonsaltatory conduction.

SYNAPSES

  • The junction wherein an axonal ending meets a neuron, muscle cell, or gland is termed a Synapse.

  • A synpatic cleft consists of an axon, a synapse, and endpoint tissue (neuron, muscle, or gland).

  • Impulses crossing the synaptic cleft consistently propagate in one direction across it.

  • Neurotransmitters: These chemicals traverse the synaptic cleft to influence the postsynaptic neuron, gland, or muscle.

    • At the neuromuscular junction (NMJ), neurotransmitters are typically excitatory, facilitating muscle contraction or gland secretion.

PATHOLOGICAL DISEASES OF NEUROTRANSMISSION

  • Pathological conditions may arise from either a reduction in presynaptic release of Acetylcholine (ACh) or by impairing postsynaptic actions of ACh.

MYASTHENIA GRAVIS

  • An autoimmune disease impacting acetylcholine receptors.

  • Consequences include muscle weakness in various regions:

    • Orbital.

    • Oropharyngeal.

    • Skeletal musculature.

  • Nerve fibers and ACh release remain normal; however, antibodies attack acetylcholine receptors at postjunctional folds.

  • This leads to diminished strength (amplitude) of the action potential signal, resulting in weakened muscle action.

GUILLAIN-BARRE SYNDROME

  • Acquired acute onset inflammatory peripheral demyelinating neuropathy with axonal sparing.

  • Mechanism: Myelin is stripped from PNS axons, significantly reducing nerve conduction velocities.

  • Manifests as gradually progressive weakness starting in the legs and ascending to arms, often described as “ascending paralysis.”

  • Common symptoms include difficulty in walking and rising from a chair.

  • If left untreated, may progress to respiratory muscles, posing a risk of respiratory failure.

MULTIPLE SCLEROSIS (MS)

  • The most common acquired demyelinating disease of the CNS of immunologic origin.

  • Resembles Guillain-Barre Syndrome, but affects the CNS rather than the PNS.

  • Hallmark Sign: Presence of demyelinating plaques that obstruct or slow nerve impulses.

  • Characterized by cycles of relapse and remission:

    • Remission phases show improved symptoms indicating partial remyelination of impaired axons.

    • Relapse phases reflect ongoing demyelination and degradation of symptoms.

OTHER COMMON DISORDERS

NERVE COMPRESSION (ENTRAPMENT)

  • Most frequently observed in median nerve during carpal tunnel syndrome.

  • Leads to muscle weakness in the hand and numbness, tingling, burning pain along the thumb and first 2.5 fingers on the palmar surface.

  • Caused by repetitive hand movements inflaming surrounding structures, compressing the median nerve.

    • Other contributing factors: obesity & pregnancy can raise pressure on the median nerve.

  • Common Treatments:

    • Splinting.

    • Steroid injections.

    • Surgical intervention (carpal tunnel release) if severe.

DISEASE-BASED NEUROPATHIES

  • Generally bilateral, affecting sensorimotor axons in distal lower and upper extremities.

    • Example: foot numbness in diabetic patients.

  • Initial Symptoms:

    • Burning sensations, tingling, numbness, and muscle weakness.

  • Chronic Symptoms:

    • Loss of sensation, decreased muscle bulk, abnormal reflexes, muscle fasciculations.

  • Referred to as polyneuropathies.

  • Diabetes Mellitus is the most prevalent cause of polyneuropathies.

AXON REGENERATION

  • Most body cells have regenerative abilities except for nerve cells.

  • Once a neuron cell body is lost, it cannot be replaced.

  • Axons can regenerate and regain functionality if the cell body remains intact.

  • Crucially, axon regeneration occurs exclusively in the PNS (not in the CNS).

  • Damage to neuron cell bodies in the CNS (like those in the brain and spinal cord) is irreparable.

THE END!