TOPIC 1.3 - 1.4 - Carbohydrate Metabolism - Glycogen Synthesis Degradation
Glycogen Synthesis, Degradation and Reciprocal Regulation
Dr. Nigel Austin
Page 1: Overview of Glycogen
Glycogen is a storage form of glucose.
Composed of long glucose polymers with approximately 10 residues per branch.
Contains two primary types of bonds:
α - 1,4 glycosidic bonds: Found in the backbone.
α - 1,6 glycosidic bonds: Located at the branch points.
Branching in glycogen allows for rapid breakdown due to multiple terminal ends, enabling quick energy release.
Page 2: Importance of Glycogen Storage
Storage Sites: Primarily stored as granules in the cytoplasm of liver cells (hepatocytes).
Function: Helps regulate blood glucose concentration, crucial for tissues, especially the brain and erythrocytes which rely heavily on glucose for energy.
Muscle Storage: Stored in skeletal and cardiac muscle cells, quickly mobilized during sudden or strenuous activities to provide energy.
Page 3: Glycogen Breakdown (Glycogenolysis)
Process Overview: Glycogen breakdown is termed glycogenolysis and occurs in three main steps using four different enzymes.
Page 4: Glycogenolysis – Step 1: Phosphorylysis
Definition: The first step involves phosphorolysis, the cleavage of a terminal glucose residue from glycogen.
Key Enzyme: Glycogen phosphorylase recognizes and removes the free -OH group on terminal glucose residues, adding inorganic phosphate (Pi), resulting in glucose-1-phosphate.
Page 5: Glycogenolysis – Step 2: Glycogen Remodeling
Limitation of Glycogen Phosphorylase: Can only cleave α - 1,4 glycosidic bonds and stops 4 residues before the branch point.
Enzyme Activation: At this stage, a bifunctional debranching enzyme is needed:
Transferase Activity: Moves 3 glucose residues to another terminal end.
α - 1,6 Glycosidase Activity: Cleaves the glucose residue at the branch point into a free glucose molecule.
Page 6: Glycogenolysis – Step 3: Conversion of Glucose-1-Phosphate
Final Step: The enzyme phosphoglucomutase converts glucose-1-phosphate into glucose-6-phosphate.
Page 7: Glycogenesis - Glycogen Synthesis
Requirement: Synthesis (glycogenesis) of glycogen needs a primer.
Primer Formation: Glycogenin synthesizes a primer of 7 glucose residues using UDP-glucose.
Elongation: After primer formation, glycogen synthase extends the glucose chain using α - 1,4 glycosidic bonds, while branching enzyme introduces α - 1,6 glycosidic bonds.
Page 8: Reciprocal Regulation of Glycogen
Glucagon's Role: Glycogen degradation stops glycogen synthesis.
Insulin's Role: Insulin prevents glycogen degradation by:
Inhibiting the phosphorylation and activation of glycogen phosphorylase.
Activating phosphodiesterase which converts cAMP to AMP, reversing glucagon's effects.
Page 9: WACE Questions (Assessment)
Main Function: Why store glucose as glycogen rather than free glucose? (1 mark)
Glycogen Remodeling: Purpose of glycogen remodelling? (2 marks)
Fate of Glucose-6-Phosphate: a) In liver cells? (2 marks)b) In active muscle cells? (2 marks)
Anaerobic Conditions: Pathway for ATP release from glycogen and its final product during rapid activity? (1 mark)
Catabolism: What compound are amino acids and fats catabolized into for energy release? Which pathways metabolize this compound? (2 marks)
Importance of Glycogen Breakdown: Why is glycogen breakdown essential in skeletal muscles compared to fats and amino acids? (2 marks)
Example context: Running away from an enraged dog.