Central Concepts of Pathophysiology: Innate Immunity (Inflammation)

Physiologic Mechanisms of Defense

  • First Line
    • Physical, mechanical, and biochemical barriers along with the normal microbiome.
  • Second Line
    • Innate immunity, also known as inflammation or the inflammatory response to injury or infection.
  • Third Line
    • Adaptive immunity, also known as the immune response.

First Line of Defense – Natural Barriers

  • Mechanical
    • Skin
    • Epithelial layers
    • Gastrointestinal peristalsis
    • Bronchopulmonary cilia
  • Biochemical
    • Tears
    • Sweat
    • Saliva
    • Nasal secretions

Human Microbiome

  • Normal flora of bacteria and fungi coexist on skin and within various body sites.
  • Normal flora do not normally produce disease but can produce opportunistic infections with immune compromise.

Second Line of Defense – Inflammation

  • Inflammation is the body’s most immediate response to injury, infection, or allergy.
  • Its purpose is to destroy or decrease the effects of invading pathogenic microorganisms.
  • Purposes of inflammation include:
    • To limit the extent of tissue damage
    • To protect against infection
    • To initiate repair of damaged tissue

Inflammation versus Immunity

  • Inflammation and immunity are sometimes confused but they are not the same entity.
  • Inflammation follows a predictable stepwise physiological response.
  • Inflammation is activated before the body’s total immune response, also known as adaptive immunity.

Third Line of Defense Adaptive (Acquired) Immunity

  • Immune responses involved humoral and cell-mediated actions.
  • Adaptive Immunity develops in active and passive manner.
  • Topic to be described in a following module.

The Inflammatory Response

  • Initiated by either cellular injury or pathogenic invasion.
  • Initial response involves mast cell degeneration, activation of the complement system, clotting, and kinin systems, and the release of end - products from damaged cells.
  • The body further responds with actions directed at the inflammatory site and widely accepted as visible signs of inflammation:
    • Vasodilation (redness, heat)
    • Increased vascular permeability (edema or swelling)
    • Thrombosis (clotting)
    • Stimulation of nerve endings (pain)
    • Cellular infiltration (pus)

Exudate

  • Serous – watery fluid that contains proteins and a few white blood cells, such as in a blister.
  • Fibrous – thick and clotted fluid with white blood cells, such as from the lungs.
  • Purulent – known as pus that contains a large or ongoing deposit of white blood cells at the injury site.
  • Hemorrhagic – containing blood – red blood cells.

Inflammatory Response

  • Etiologies of cellular damage
    • Infection
    • Mechanical damage
    • Ischemia
    • Nutrient deprivation
    • Temperature extremes
    • Radiation exposure
  • Inflammation occurs in vascularized tissue.
  • Classic or cardinal localized signs and symptoms
    • Redness (rubor)
    • Heat (calor)
    • Swelling (tumor)
    • Pain (dolor).

Inflammatory Response – Vascular and Cellular

  • Tissue Injury
    • Local vasodilation
    • Increased vascular permeability
    • Diapedesis
    • White blood cells adhere to vessel wall and migrate through vessels to site of injury

Plasma Protein Systems

  • Complement System
    • Contains different plasma proteins (10%) of circulating proteins.
    • Directly destroys pathogens.
    • Activates and integrates with all other immune components.
    • These pathways converge to activate the complement system
      • Classical pathway
        • Acquired immunity – Antigen/Antibody complex
      • Lectin pathway – Bacterial carbohydrates
      • Alternative pathways – Gram negative bacteria and fungal wall polysaccharides

Plasma Protein Systems

  • Clotting System
    • Plasma proteins form a fibrinous mesh at site of tissue injury:
      • Prevents the spread of infection to adjacent tissues.
      • Traps microorganisms and foreign bodies at the inflammatory site so they can be removed by infiltrating cells.
      • Forms a clot that stops any bleeding, and
      • Provides a framework for tissue repair and healing.
    • Intrinsic and extrinsic clotting pathways converge.
    • Result is a fibrin mesh of insoluble protein as the end-product of the clotting cascade.

Plasma Protein Systems

  • Kinin System – Bradykinin production augments inflammation
    • Dilation of blood vessels (redness, heat)
    • Acting with prostaglandin to stimulate nerve endings and produce pain (pain)
    • Contraction of smooth muscle cells
    • Increased vascular permeability (swelling)
    • Increased leukocyte chemotaxis.
      • Biologic process by which certain cells direct their movement according to chemicals in their environment.
      • Bradykinin directs the leukocytes to the area of injury.

Cellular Response

  • Two major cellular components involved
    • Granulocytes
      • Neutrophils
      • Eosinophils
      • Basophils
    • Monocytes

Cellular-Mediated Inflammatory Response

  • Plasma protein system
  • Chemical mediators released by cell destruction
  • Cells are recruited and activated by:
    1. Cellular receptors
    2. Mast cells
    3. Phagocytosis
    4. Neutrophils
    5. Monocytes and macrophages
    6. Basophils
    7. Natural killer cells
    8. Thrombocytes (platelets)

Cellular-Mediated Inflammatory Response Cellular Receptors

  • Each cell has receptors on the cell surface that bind to soluble substances that are produced during tissue damage or infection
  • Receptors on cell surface bind soluble substances produced during inflammation
  • Receptor binding activates intracellular signaling pathways - Triggers inflammatory response

Cellular-Mediated Inflammatory Response Mast cells

  • Activation:
    1. Physical injury
    2. Chemical injury
    3. Immune response (anaphylactic reaction)
    4. Toll-like receptors (bacteria and fungi)
  • Action:
    • Chemical mediators released by these processes:
      • Degranulation (Histamine, neutrophils, and eosinophils
      • Mediated synthesis (Leukotrienes, prostaglandins, platelet activating factor

Significant Chemical Mediators

  • Activated mast cells stimulate production of chemical mediators obtained from lipids in cell membranes with clinically significant effects.
  • Leukotrienes – produced from arachidonic acid released from cell membranes have effects similar to histamine although they are released later and have longer effects than histamine.
    • Airway constriction
    • Increased vascular permeability
  • Prostaglandins – also produced from arachidonic acid and with different groups
  • Platelet activating factor –produced by mast cells, neutrophils, monocytes, endothelial cells, and platelets (thrombocytes).
    • Effects are considered identical to leukotrienes

Cellular-Mediated Inflammatory Response Phagocytosis

  • Process when an immune system cell engulfs or ingests cellular debris or foreign material.
  • Most phagocytes are circulating in the blood, so they must leave the blood stream and advanced to the injured site.
  • Once at the site of injury they engulf the undesired material, then fuse with lysosome granules to help destroy the material.
  • When the phagocytic cell fulfills its purpose, it begins to break apart.
  • When liberated from the now dead phagocytic cell, enzymes contribute to increase inflammation and the cycle begins again.

Cellular-Mediated Inflammatory Response Neutrophils, Monocytes, & Macrophages

  • Neutrophils
    • Phagocytosis begins 6-12 hours after injury
    • Sensitive to acidic environment
    • Lifespan peak of about 24 hours
    • Become a component of purulent exudate
  • Monocytes & Macrophages
    • Larger cells than neutrophils with slower and longer onset of action
    • Activity usually begins about 3-7 days after tissue injury
    • These cells divide and replicate

Cellular-Mediated Inflammatory Response Basophils, Natural Killer Cells, Thrombocytes

  • Basophils
    • Similar to mast cells
    • Elevated with asthma and allergic reactions
  • Natural Killer Cells
    • Recognize and eliminate viral-infected cells
    • Site of action is mostly in the circulation, not tissues
    • Can differentiate infected or tumor cells from normal cells
  • Thrombocytes
    • Coagulation
    • Degranulation

Cellular Products

  • Soluble factors that contribute to the inflammatory response.
  • Are either pro-inflammatory or anti-inflammatory.
    • Cytokines
    • Interleukins
    • Interferons
    • Tumor necrosis factor - α
    • Chemokines

Inflammation – Local Manifestations

  • What are the classic or cardinal signs/symptoms of acute inflammation?
    • Redness
    • Heat
    • Swelling
    • Pain
  • You should be able to explain the rationale for these findings.

Inflammation – Systemic Manifestations

  • Acute Inflammation
    • Fever
    • Leukocytosis
    • Increased plasma proteins
      • Interleukin -1
      • Interleukin-4
      • Fibrinogen
      • C-reactive protein
  • Chronic Inflammation
    • Occurs when acute inflammation unresolved.
    • Macrophages, lymphocytes, and fibrous tissue build up in sites of chronic inflammation