Patho - PPT2 (slides 1-42) and PPT3 (slides 1-7)

Metaplasia and its mechanism

  • Definition: metaplasia is when one normal cell type is substituted for another type due to stressors.

  • Common example discussed: columnar ciliated epithelium being replaced by squamous epithelial cells in response to a chronic irritant.

  • Mechanism emphasized:

    • A stressor (e.g., smoking) causes chronic irritation and inflammation.

    • Stem cells in the tissue get reprogrammed, leading to a change in cell lineage (metaplasia).

  • Key takeaway: metaplasia arises from stress-induced stem cell reprogramming, not from a single isolated event.

Glutathione as an endogenous antioxidant

  • Glutathione (GSH) is your endogenous antioxidant found throughout the body.

  • Function: protects cells from free radicals by donating electrons and becoming oxidized.

  • Reduced form: GSHGSH (the active form).

  • Oxidized form: GSSGGSSG (glutathione disulfide).

  • Recycling/reduction process: enzymes convert GSSGGSSG back to GSHGSH, restoring antioxidant capacity.

  • Important nuance: the reduced form GSHGSH is the active antioxidant, and the cycle restores GSHGSH from GSSGGSSG.

  • Clinical note mentioned: the body produces a limited amount of glutathione; deficiency in recycling can sensitize cells to oxidative damage (e.g., G6PD deficiency discussed later).

  • Specific reaction example (glutathione recycling):

    • extGSSG+NADPH+H+<br>ightarrow2GSH+NADP+ext{GSSG + NADPH + H^+ <br>ightarrow 2 GSH + NADP^+}

  • Mention of G6PD deficiency (in spring module): patients with this deficiency have impaired ability to recycle glutathione and may have increased vulnerability to oxidative damage.

Causes of cellular injury

  • Physical (mechanical) injury: crushing, tearing, cutting; disruption of cellular membrane.

  • Thermal injury: burns, freezing; temperature extremes denature proteins.

    • Analogy: denaturation of proteins when cooking an egg; similar processes in cells under heat or cold stress.

  • Toxic exposures: chemicals causing cellular damage, including DNA damage and pH-induced protein denaturation.

  • Pathogens: bacteria, viruses, fungi can injure cells.

  • Nutritional imbalances: both excess and deficiency can injure tissues (no such thing as a truly “too good” thing in excess).

    • Examples discussed:

    • Water intoxication: rapid excessive water intake can be fatal.

    • Vitamin C excess: anecdote of GI bleeding from megadoses of vitamin C (acidic irritation of GI lining).

    • Iron deficiency anemia as a deficiency example.

  • Radiation: DNA damage (strand breaks, kinks) and potential neoplasia.

  • Summary: injuries can arise from multiple pathways; the same tissue can be damaged by different insults.

Consequences of cellular injury

  • Biochemical changes: cells may attempt to reestablish homeostasis; some changes are difficult to detect visually.

  • Morphological changes (visible under microscope) usually occur with more severe injury:

    • Cellular swelling (hydropic changes) due to ion channel disruption, leading to increased Na^+ influx and water entry.

    • Fatty changes (lipid accumulation) in tissues like the liver when stressed; fatty liver disease.

  • Liver-specific example:

    • Fatty liver (steatosis) with triglyceride accumulation; concern increases with ongoing stress.

    • Progression from steatosis to cirrhosis (scar tissue replaces dead hepatocytes) is not always reversible; cirrhosis is generally irreversible.

    • Liver regeneration capacity: the liver is highly regenerative; a liver lobe transplant can regenerate to restore function, but cirrhosis limits this.

  • Fibrosis: scar tissue formation that holds tissue together but does not restore function (stopgap rather than functional replacement).

  • Relevance to other tissues: heart and brain have limited regenerative capacity; damage here leads to lasting functional deficits.

Cell death: apoptosis vs necrosis

  • Apoptosis (programmed cell death):

    • Clean, organized, energy-dependent process that eliminates single cells with minimal disruption to neighboring cells.

    • No inflammation typically associated with apoptotic death.

    • Mechanistic hallmarks: activation of caspases; DNA fragmentation; cell shrinkage; formation of apoptotic bodies; phosphatidylserine exposure on the outer membrane as an "eat me" signal for phagocytes.

  • Necrosis:

    • Unregulated, messy cell death often due to severe injury or toxin exposure.

    • Leads to leakage of cell contents, inflammation, and potential damage to surrounding tissue.

    • Necrosis tends to cause more necrosis if not contained, creating a spreading inflammatory environment.

  • Visual differences and consequences:

    • Necrosis: swelling, rupture, release of lysosomal enzymes, inflammation.

    • Apoptosis: cell fragments into apoptotic bodies; contained and cleared with minimal inflammation.

  • Signals and triggers: increased intracellular calcium can trigger apoptosis; multiple signals can converge on caspases.

Apoptosis: pathways and features

  • Two main pathways:

    • Extrinsic pathway (external signals): death receptors on the cell surface bind ligands (death ligands) leading to caspase activation.

    • Intrinsic pathway (internal signals): cellular stress (DNA damage, ROS, hypoxia) triggers mitochondrial cytochrome c release and caspase activation; p53 tumor suppressor plays a key role when DNA damage is detected.

  • Extrinsic pathway details:

    • Death receptors include various ligands such as inflammatory mediators; binding activates a cascade of caspases (caspases 9, 3, 6, 7, etc.; order not required to memorize).

    • Activation leads to mitochondrial cytochrome c release and downstream effector caspases.

  • Intrinsic pathway details:

    • Triggered by ROS, DNA damage, hypoxia, low ATP, etc.

    • Mitochondria release cytochrome c, activating caspases.

    • p53 responds to DNA mutations by halting cell division and promoting repair; if irreparable, it promotes apoptosis via mitochondrial pathway.

  • Common apoptotic features:

    • ATP-dependent process; organized dismantling of cellular components.

    • Phosphatidylserine flips from inner to outer leaflet of the plasma membrane, marking the cell for phagocytosis.

  • Relevance to disease and therapy:

    • Apoptosis acts to prevent cancer by eliminating damaged cells.

    • Cancer cells often evade apoptosis, contributing to unchecked growth.

  • Brief on practical visualization:

    • Apoptosis shows membrane changes and apoptotic bodies without inflammation; necrosis shows leakage and inflammation.

Necrosis: types and clinical implications

  • Liquefactive necrosis: enzymatic digestion leading to liquefied tissue; commonly seen in brain infarcts or abscesses due to active lysosomal enzymes.

  • Coagulative necrosis: protein denaturation forms a gel-like mass; typically seen in hypoxic injury in solid organs (e.g., heart); tissue architecture is preserved for a time.

  • Fat necrosis: adipocytes die and fat tissue decomposes; can appear as soapy appearance; clinically observed with certain fat-late injuries or drug effects (e.g., warfarin-associated necrosis).

  • Caseous necrosis: cheese-like appearance; characteristic of pulmonary tuberculosis.

  • Infarction: tissue death due to ischemia; heart muscle infarction due to atherosclerotic blockage; scar tissue forms and regeneration is limited.

  • Gangrene: widespread necrosis with tissue decay; three types:

    • Dry gangrene: dry, with definite line of demarcation; typically not infection-associated.

    • Wet gangrene: tissue appears wet and has poor demarcation; often accompanied by infection and foul odor; high risk of sepsis.

    • Gas gangrene: infection with anaerobic bacteria (e.g., Clostridium perfringens) producing gas; rapidly progressive and life-threatening; often requires amputation and aggressive antibiotics.

  • Management of necrosis:

    • Debridement (removal of necrotic tissue) and possible amputation depending on extent.

    • Antibiotics (usually IV for severe infection) and monitoring for sepsis.

    • In some cases, maggot therapy uses medical-grade larvae to selectively consume necrotic tissue while sparing healthy tissue.

  • Sequelae of necrosis:

    • Local loss of function depending on affected tissue.

    • Infection spread and sepsis risk.

    • Release of intracellular enzymes (e.g., CK, LDH) into the bloodstream indicating cell death.

    • Potential systemic consequences including somatic death in extreme cases.

  • Containment strategy by the body:

    • Wall off necrotic tissue with fibrous connective tissue and calcification to limit spread (tuberculosis example with calcifications).

Pathologic calcification and stones

  • Dystrophic calcification: calcification in necrotic tissue with normal serum calcium levels; body walls off damaged tissue.

  • Metastatic calcification: calcification in otherwise healthy tissue due to hypercalcemia (e.g., parathyroid hormone excess) irrespective of local tissue necrosis.

  • Calculi (stones):

    • Gallstones: can form in the gallbladder; bile acids may compose stones; rapid weight loss or familial predisposition increases risk; stones may block bile ducts.

    • Kidney stones: typically calcium oxalate; stones can deposit in nephrons and cause severe pain; block filtrate flow.

Aging theories and somatic death

  • Theories of aging (overview):

    • Programmed/teleomere theory: telomere shortening limits cell division.

    • Lipofuscin accumulation: aging pigment accumulating in cells disrupts function.

    • Accumulated damage theory: lifelong exposure to free radicals causes cumulative cellular damage.

    • Cross-linking theory: glycation cross-links proteins, impairing function.

    • Neuroendocrine theory: hormonal changes with age contribute to aging.

    • Likely a combination of multiple factors, including genetics and lifestyle.

  • Somatic death:

    • Brain electrical activity ceases; brain death defined by flat EEG.

    • Not all cells die at once; some persist longer which allows for organ transplantation windows.

  • Postmortem changes:

    • Rigor mortis: muscles stiffen due to ATP depletion, preventing detachment of myosin from actin.

    • Temperature decrease toward ambient temperature.

    • Blood pooling and eventual autolysis and putrefaction.

Neoplasia and cancer biology

  • Neoplasia concept: abnormal, uncontrolled cell proliferation forming a tumor.

  • Variability in mitosis by cell type:

    • Some cells divide rapidly (e.g., hair, mucosal epithelial cells, bone marrow).

    • Some cells do not divide (e.g., neurons, cardiac muscle); regeneration capacity varies (neural/neurogenesis in limited brain regions).

  • Cancer therapy relevance:

    • Chemotherapy targets rapidly dividing cells (reason for side effects like alopecia, mucositis, bone marrow suppression).

  • Cell turnover balance:

    • In normal tissue, cell production roughly equals cell loss to maintain homeostasis.

  • Gene regulation of cell division:

    • Proto-oncogenes: normal genes that promote cell division; mutation converts them to oncogenes, driving excessive division.

    • Oncogenes: mutated, constitutively active drivers of proliferation.

    • Growth factor signaling: growth factors bind receptors (often tyrosine kinase receptors) to stimulate division via intracellular cascades.

    • EGFR (HER1): a common receptor amplified in cancer, increasing sensitivity to growth signals; some receptors become constitutively active, driving growth without ligand.

    • Autocrine signaling in cancer: tumor cells may secrete growth factors that stimulate their own receptors, promoting self-sustained division.

    • Tumor suppressor genes (e.g., p53): act as brakes on cell cycle; mutations disable braking, allowing unchecked division.

    • Contact inhibition: normal cells stop dividing when touching neighbors; cancer cells often lose this signal and continue to proliferate.

  • Multi-hit model of cancer:

    • Cancer typically requires multiple mutations in several division-control genes; no single mutation is sufficient for full malignant transformation.

  • Practical implications and visuals:

    • A quick explanatory video described the interplay between proto-oncogenes and tumor suppressor genes in regulating division; cancer arises when signals to divide dominate over inhibitory controls.

    • The lecture emphasizes that cancer development is gradual, often spanning years with cumulative genetic changes.

Practical clinical connections and takeaways

  • Smoking and metaplasia: smoking induces metaplastic changes via chronic irritation and inflammation.

  • Alcohol and fatty liver: sustained stress can lead to fatty degeneration and progression to cirrhosis; cirrhosis is irreversible.

  • Ischemia and infarction: lack of blood flow causes tissue death; heart tissue does not regenerate well, leading to scar formation and functional loss.

  • Chemo side effects:

    • Alopecia (hair loss) due to rapid turnover of hair follicle cells.

    • Mucositis due to rapidly dividing mucosal cells.

    • Bone marrow suppression leading to infection risk due to reduced white blood cell production.

  • TB and calcification: caseous necrosis is typical in pulmonary TB and can lead to calcified granulomas in the lung.

  • Debridement and infection control: removal of necrotic tissue reduces spread and supports healing; maggot therapy is an uncommon but approved method for selective debridement.

Quick recap: key terms to remember

  • Metaplasia: replacement of one adult cell type by another.

  • Glutathione redox cycle: active antioxidant system with GSH and GSSG, recycling via specific enzymes.

  • Apoptosis vs necrosis: programmed, orderly cell death vs uncontrolled, inflammatory cell death.

  • Extrinsic vs intrinsic apoptosis pathways: external death receptors vs internal mitochondrial signals.

  • Types of necrosis: liquefactive, coagulative, fat, caseous; infarction and gangrene variants (dry, wet, gas).

  • Calcification types: dystrophic, metastatic; calculi (kidney/gallstones).

  • Aging theories: telomere shortening, lipofuscin, cross-linking, oxidative damage, neuroendocrine changes.

  • Neoplasia and cancer biology: proto-oncogenes vs oncogenes, tumor suppressor genes (p53), growth factor signaling (EGFR), autocrine loops, and multi-hit carcinogenesis.

  • Clinical implications of rapidly dividing tissues in cancer therapy and the rationale for side effects.