The Endomembrane System and Protein Sorting

Becker’s World of the Cell Tenth Edition: Chapter 12 - The Endomembrane System and Protein Sorting

The Endomembrane System (1 of 2)

  • Definition: An appreciation of eukaryotic cells depends on understanding the role of intercellular membranes and the compartmentalization of function within organelles.

  • Trafficking: Movement of lipids and proteins between organelles (called trafficking) must be tightly regulated.

Components of the Endomembrane System

  • Endoplasmic Reticulum (ER): The endoplasmic reticulum and the Golgi complex are sites for protein synthesis, processing, and sorting.

  • Endosomes: Endosomes carry and sort material brought into the cell.

  • Lysosomes: Lysosomes digest ingested material and unneeded cellular components.

  • Structure: These organelles contribute to forming the endomembrane system.

The Endoplasmic Reticulum (1 of 2)

  • Structure: The endoplasmic reticulum (ER) is a continuous network of flattened sacs, tubules, and vesicles through the cytoplasm of a eukaryotic cell.

  • Components: The membrane-bound sacs are called ER cisternae (singular: ER cisterna), and the space inside them is referred to as the ER lumen.

Functions of the ER

  • Protein Synthesis:

    • Enzymes associated with the ER are involved in the biosynthesis of proteins for:

    • Incorporation into the plasma membrane or into the organelles of the endomembrane system.

    • Export from the cell.

  • Lipid Synthesis: The ER is also involved in lipid synthesis.

Types of Endoplasmic Reticulum

  • Rough ER (RER):

    • Characterization: Characterized by ribosomes on the cytosolic side of the membrane.

    • Transitional Elements (TEs): A subdomain of rough ER that plays a role in the formation of transition vesicles, shuttling lipids and proteins from the ER to the Golgi complex.

  • Smooth ER (SER):

    • Characteristics: Lacks ribosomes and has roles in processing and storing nonproteins.

Distinguishing Rough and Smooth ER

  • Rough ER Structures:

    • Rough ER membranes form large flattened sheets.

  • Smooth ER Structures:

    • Smooth ER membranes form tubular structures.

    • Transitional elements of the rough ER resemble the smooth ER, contrary to the overall structure of the two.

  • Continuity: The lumenal spaces of rough and smooth ER are continuous.

Variation in ER

  • Presence: Both types of ER are present in most eukaryotic cells, but there's variation in relative amounts.

  • Prominence of Rough ER: Cells involved in the synthesis of secretory proteins have pronounced rough ER networks.

  • Extensive Smooth ER: Cells producing steroid hormones tend to have extensive networks of smooth ER.

Rough ER and Protein Biosynthesis (1 of 2)

  • Ribosome Function: Ribosomes on the cytosolic side of the rough ER membrane synthesize both membrane-bound and soluble proteins for the endomembrane system.

  • Synthesis Mechanism: Newly synthesized proteins are inserted into the endomembrane system through a pore complex as they are synthesized, a process called cotranslationally insertion.

Rough ER and Protein Biosynthesis (2 of 2)

  • Initial Steps: The rough ER is the site for:

    • The initial stages of adding carbohydrates to glycoproteins.

    • The folding of polypeptides.

    • Recognition and removal of misfolded proteins.

    • Assembly of multimeric proteins.

Rough ER and Quality Control

  • Misfolding Response: Proteins that are incorrectly folded, modified, or assembled are exported for degradation in cytosolic proteasomes.

Smooth ER Functions

  • Roles:

    • Involved in drug detoxification, carbohydrate metabolism, calcium storage, and steroid biosynthesis.

    • Primarily involved in processing or storing non-protein molecules within cells.

Drug Detoxification

  • Hydroxylation Process:

    • Adding hydroxyl groups to hydrophobic drugs increases their solubility, making them easier to excrete from the body.

  • Cytochrome P-450: Hydroxylation is catalyzed by cytochrome P-450 proteins, also known as monooxygenases.

Hydroxylation Mechanism

  • Electron Transport:

    • Electrons from NADPH or NADH are transferred to a heme group in cytochrome P-450.

  • Chemical Reaction:


    • RH+NAD(P)H+O<em>2ightarrowROH+H</em>2O+NAD(P)+R-H + NAD(P)H + O<em>2 ightarrow R-OH + H</em>2O + NAD(P)^+

Drug Tolerance

  • Phenobarbital Effect: Injection of phenobarbital into rats causes rapid increases in barbiturate detoxifying enzymes and proliferation of smooth ER, leading to drug tolerance.

Smooth ER in Drug Detoxification

  • Aryl Hydrocarbon Hydroxylase:

    • One cytochrome P-450 is part of a complex that metabolizes polycyclic hydrocarbons, producing more toxic byproducts, some linked to spontaneous cancers.

  • Effect of Cigarette Smoke: A potent inducer of aryl hydrocarbon hydroxylase.

Pharmacogenetics

  • Study Field: Investigates how inherited differences in genes like P-450 can cause variable responses to drugs and medications.

Carbohydrate Metabolism (1 of 2)

  • Liver Cell Involvement: Smooth ER in liver cells breaks down stored glycogen, containing glucose-6-phosphatase.

  • Biochemical Reaction:

    • Glucose-6-phosphate is hydrolyzed to yield free glucose.

    • C<em>6H</em>13O<em>9P+H</em>2O<br>ightarrowC<em>6H</em>12O6+PC<em>6H</em>{13}O<em>9P + H</em>2O <br>ightarrow C<em>6H</em>{12}O_6 + P

Carbohydrate Metabolism (2 of 2)

  • Glycogen Storage: Liver stores glucose as glycogen in granules associated with smooth ER.

  • Release Mechanism: Glycogen is broken down by phosphorolysis, producing glucose-6-phosphate, which must be converted to free glucose for entry into the bloodstream.

Role of the Smooth ER in the Catabolism of Liver Glycogen (1 of 2)

  • Catabolism Insight: Figure 12.2 illustrates role of smooth ER in liver glycogen catabolism.

Role of the Smooth ER in the Catabolism of Liver Glycogen (2 of 2)

  • Biochemical Process: Smooth ER regulates breakdown of glycogen for energy release in liver cells.

Calcium Storage

  • Specialization: Sarcoplasmic reticulum in muscle cells specializes in calcium storage.

  • Calcium Dynamics: ER contains high concentrations of calcium-binding proteins; calcium ions are pumped into the ER via ATP-dependent calcium ATPases and released for muscle contraction.

Steroid Biosynthesis (1 of 2)

  • Functionality: Smooth ER synthesizes cholesterol and steroid hormones.

  • Cell Types: Large amounts found in cells synthesizing steroid hormones; also associated with chloroplasts in some plants.

Steroid Biosynthesis (2 of 2)

  • Cholesterol Relation: Cholesterol, cortisol, and steroid hormones share a four-ring structure with variations in carbon side chains and hydroxyl groups.

  • Enzymatic Step: Hydroxymethylglutaryl-CoA reductase (HMG-CoA reductase) is the committed step in cholesterol biosynthesis and is targeted by statin drugs.

Central Role of the ER in Membrane Biosynthesis

  • Composition: The ER is the primary source of membrane lipids, with exceptions including mitochondria, peroxisomes, and chloroplasts.

Membrane Biosynthesis (1 of 2)

  • Mechanism: Fatty acids for membrane phospholipids are synthesized in the cytoplasm, incorporated into the ER membrane, and transferred to the lumenal side by phospholipid translocators (flippases).

  • Membrane Asymmetry: The type of phospholipid transferred depends on the translocator present, leading to membrane asymmetry.

Membrane Biosynthesis (2 of 2)

  • Transfer to Organelles: Distinct compositions of cytosolic and lumenal monolayers are established in the ER and transferred to other cellular membranes.

  • Phospholipid Exchange Proteins: Facilitate conveyance of specific phospholipids to mitochondria, chloroplasts, or peroxisomes.

Composition of the ER and Plasma Membranes of Rat Liver Cells

  • Weight Percentages:

    • Carbohydrate: 10% in both ER and plasma membranes.

    • Protein: 62% (ER), 54% (plasma).

    • Total Lipid: 27% (ER), 36% (plasma).

  • Lipid Types:

    • Major lipids such as phosphatidylcholine (40% ER, 24% plasma), phosphatidylethanolamine (17% ER, 7% plasma), and more, as shown in Table 12.1.

The Golgi Apparatus

  • Definition: Functionally and physically linked to the ER.

  • Role: Glycoproteins and membrane lipids from the ER undergo further processing and are sorted and packaged for transport.

  • Central Role: Plays a major role in membrane and protein trafficking in eukaryotic cells.

Structure of the Golgi Apparatus

  • Composition: Series of flattened membrane-bound cisternae.

  • Golgi Stack: A series of cisternae, usually three to eight, is called a Golgi stack.

    • Variation: Some cells have one large stack, while secretory cells may have hundreds or thousands of stacks.

Transport Vesicles

  • Surrounding Structures: Both ER and the Golgi complex are surrounded by numerous vesicles that transport lipids and proteins between them.

  • Intracisternal Space: Golgi complex lumen is part of the endomembrane system.

Two Faces of the Golgi Stack

  • Cis Face: Oriented toward the ER; compartment called the cis-Golgi network (CGN).

  • Trans Face: Opposite side of the stack, referred to as the trans-Golgi network (TGN).

Golgi Network

  • Vesicle Budding: Proteins and lipids leave the Golgi in transport vesicles that bud from the tips of the TGN.

  • Processing: Between CGN and TGN are medial cisternae, where most protein processing occurs.

  • Distinct Biochemical Environment: Each compartment contains specific receptor proteins unique to its section.

Models of Golgi Function

  • Stationary Cisternae Model:

    • Each cisterna is stable; transport of materials between cisternae is mediated by shuttle vesicles.

  • Cisternal Maturation Model:

    • Golgi cisternae are transient compartments, change from CGN to TGN with enzymes returned in vesicles.

Integration of Models

  • Experimental Evidence: Suggests both models are valid as they facilitate the movement of cargo targeted for various destinations.

  • Research Tools: Time-lapse fluorescence microscopy and tracking substances aid in understanding these processes.

Anterograde and Retrograde Transport (1 of 2)

  • Anterograde Transport: Movement toward the plasma membrane, involves secretory granules fusing with the membrane via exocytosis.

    • Cell membrane must balance the flow of lipids.

Anterograde and Retrograde Transport (2 of 2)

  • Retrograde Transport: Flow of vesicles from Golgi back to the ER, maintaining lipid balance and providing materials for new vesicle formation.

ER and Golgi in Protein Processing

  • Processes: Includes protein folding, quality control, and glycosylation (addition of carbohydrate side chains to form glycoproteins).

Glycosylation Types

  • N-linked Glycosylation: Addition of oligosaccharides to the nitrogen atom of specific asparagine residues.

  • O-linked Glycosylation: Addition of carbohydrates to the hydroxyl group of serine, threonine, or rarely tyrosine residues.

## Protein Folding and Quality Control in the ER