L22

B Cells

  • Naïve B cells require help from CD4+ T helper cells for full activation.
    • They present antigens as peptides bound to MHC II, activating CD4+ helper T cells, which then stimulate the B cell.
  • Plasma cells, or activated B cells, secrete antibodies that perform various functions such as:
    • Neutralization
    • Opsonization
    • Complement activation
  • Memory B cells provide a long-lived response.

Antigen Specificity

  • Antigens are toxins or foreign substances that induce an immune response.
  • Specificity refers to the ability of an antibody to bind to one, but not another, member of a family of related substances.

B Cells and Antibodies

  • Each B cell is specific for one antigen, recognizing a specific region on a protein.
  • Antigens are recognized by immunoglobulin (Ig) molecules.
  • One B cell expresses one Ig sequence.
  • Surface-bound Ig on B cells is called the B cell receptor (BCR).
  • Soluble, secreted Ig is called an antibody.

Structure of an Immunoglobulin Molecule

  • The immunoglobulin molecule consists of:
    • An N terminus, which is the variable region that binds to the antigen.
    • A C terminus, which is the constant region that binds to Fc receptors and mediates Ig functions.
    • Two heavy chains and two light chains joined by disulfide bonds.

Antigen Binding Sites

  • Immunoglobulin molecules bind to regions on the protein, recognizing conformational shapes.

Diversity in Antigen Receptors

  • Diversity is generated through the combination of immunoglobulin gene segments:
    • Variable (V)
    • Diversity (D)
    • Junctional (J)
    • Constant (C)
  • During B cell development, these gene elements rearrange through VDJ recombination.
  • The diversity region is in contact with the antigen.
  • Different combinations of these genes enable diversity, with approximately 5 \times 10^{13} possible combinations.

B Cell Development

  • Lymphocytes develop immunocompetence in the primary lymphoid organs.
  • B cells mature in the bone marrow.
  • Rearrangement of Ig gene elements generates a B Cell Receptor (VDJ recombination).
  • Any self-reactive cell is deleted during development through negative selection.
  • Immature B cells leave the bone marrow ready to scan the body.

Negative Selection

  • The immune system must respond to foreign proteins but not self-proteins.
  • Self/non-self discrimination is crucial.
  • It is important to delete any B cells that are specific for a self-protein.
  • An array of self-antigens is expressed in the bone marrow to facilitate this process.

Activation of B Cell/Antibody Response

  • The B cell receptor (surface-bound immunoglobulin) binds to the antigen.
  • The B cell presents a peptide to antigen-specific CD4+ T helper cells via MHC II.
  • CD4+ T cells provide co-stimulation to the B cell.
  • B cell activation induces proliferation and differentiation into antibody-secreting plasma cells and memory cells.
  • Microbial constituents, such as bacterial polysaccharides, can stimulate B cells independently of T cells.

T Cells Activate B Cells

  • T cells activate B cells via membrane-bound and secreted molecules.
    • Membrane-bound: CD40 (co-stimulation) for B cell activation.
    • Soluble: Cytokines for B cell differentiation.

B & T Cell Activation

  • B and T cell activation occurs in secondary lymphoid organs, such as lymph nodes and spleens.
  • B and T cells interact at border zones within these organs (B-cell follicle and T cell zone).

B Cell Response Refinement in Germinal Center

  • Once activated, B cells migrate into follicles and form a germinal center where immunoglobulin modifications occur, supported by accessory immune cells.
  • Somatic hypermutation (Ig gene editing) takes place to improve antibody affinity (binding strength).
  • Class-switching occurs to generate different immunoglobulin isotypes (different functional roles).
  • Selection of high-affinity B cells ensures a faster and more effective response upon second exposure to the antigen.

Germinal Centers

  • Germinal centers are responsible for:
    • The generation of memory B cells.
    • The generation of high-affinity plasma cells.
  • Antibody-secreting plasma cells migrate to and reside in the bone marrow under homeostatic conditions.

Summary of B Cells

  • Each B cell expresses a unique immunoglobulin molecule, making it antigen-specific.
  • Immunoglobulin molecules are composed of a combination of Ig genes (VDJ and constant region).
  • B cells produce antibodies (secreted immunoglobulin molecules).
  • B cells are APCs that express MHC II.
  • B cells activate CD4+ T cells and receive co-stimulation.
  • They need help from CD4+ T cells for full activation.
  • Activation leads to the generation of plasma and memory cells.
  • B cells mediate the humoral immune response.

Antibody Functions

  • Antibodies perform a variety of functions:
    • Neutralize pathogens by binding to their surface and blocking entry into cells.
    • Opsonize pathogens by coating them with antibodies, targeting them for destruction by other immune cells (e.g., macrophages, NK cells, mast cells, and eosinophils).
    • Activate the complement pathway.
  • These functions are performed by the constant region on the immunoglobulin.
  • A variety of immunoglobulin isotypes perform these functions, with the same variable region but a different constant region.

Immunoglobulin Isotypes

  • Isotypes are determined by the constant region on the heavy chain:
    • IgA (IgA1, IgA2)
    • IgD
    • IgE
    • IgG (IgG1, IgG2a, IgG2b, IgG3, IgG4)
    • IgM
  • IgD and IgM can be expressed as surface-bound receptors on naïve B cells.
  • Somatic recombination (during B cell differentiation) leads to class switching and the production of different Ig isotypes.

Role of Cytokines

  • Cytokines induce switching to different isotypes.

Class Switching

  • Class switching leads to the activation of the heavy chain C-region gene.

Immunoglobulin Isotypes Trigger Different Responses

  • Functional activities of different isotypes include neutralization, opsonization, sensitization for killing by NK cells, sensitization of mast cells, and activation of the complement system.

The Humoral Immune Response

  • The humoral immune response involves:
    • B-cell activation by antigen and helper T cells.
    • Antibody secretion by plasma cells.
    • Neutralization, opsonization, and complement activation.

Neutralization: Bacterial/Parasitic Toxins

  • Pre-existing antibody is necessary.
  • It takes a while to initiate the adaptive immune responses, making it necessary to respond to toxins quickly.

Common Diseases Caused by Bacterial Toxins

  • Examples include tetanus (tetanus toxin), diphtheria (diphtheria toxin), gas gangrene (clostridial toxin), cholera (cholera toxin), anthrax (anthrax toxic complex), botulism (botulinum toxin), and others.

Neutralization: Viral Entry

  • Pre-existing antibody is necessary.
  • This is the basis for some vaccinations against viruses (e.g., COVID vaccines induce antibodies to spike protein).

Neutralization: Intracellular Bacterial Entry

  • This applies to atypical bacteria such as Chlamydia and mycoplasma species.
  • Antibodies prevent the attachment of bacteria to the cell surface.

Antibody-Dependent Cellular Cytotoxicity (ADCC)

  • IgG-coated target cells activate Fc receptors on NK cells, leading to the release of membrane-puncturing granules such as granzyme and perforin.

IgE-Mediated Degranulation

  • Mast cells and basophils bind IgE via high-affinity Fc epsilon receptors.
  • Antigen binds to mast cell-bound IgE, resulting in crosslinking of IgE and release of mediators by mast cells.
  • This is part of the anti-parasitic response and Type I Hypersensitivity (e.g., asthma and allergy).

Opsonization

  • Antibodies bound to the pathogen bind to receptors on phagocytic cells (macrophages), triggering phagocytosis and pathogen engulfment.

Opsonization Definition

  • Coating of a pathogen by antibodies and/or complement proteins to facilitate phagocytosis and destruction of the pathogen.

Opsonization Mechanism

  • Opsonization can occur through IgG:Fc binding or C3b:CR1 binding.
  • The bacterium is coated with complement and IgG antibody.
  • When C3b binds to CR1 and antibody binds to Fc receptor, bacteria are phagocytosed.
  • Macrophage membranes fuse, creating a membrane-enclosed vesicle, the phagosome.
  • Lysosomes fuse with these vesicles, delivering enzymes that degrade the bacteria.

Complement Activation

  • The complement system enhances the activation of phagocytes and pathogen uptake.

Complement System

  • The complement system is a component of the innate immune system that complements the action of antibodies.
  • It is a collection of plasma proteins (>30), many of which are pro-enzymes (zymogens) that are activated by proteolysis.
  • Activation causes a cascade of reactions leading to the destruction of pathogens.
  • It needs to be tightly regulated to prevent host damage.

Complement System: Three Pathways

  • The three pathways are:
    • The lectin pathway.
    • The classical pathway.
    • The alternative pathway.
  • All pathways converge on C3.

Complement System: Three Functions

  • Some complement proteins initiate inflammation (e.g., C3a, C5a).
  • Phagocytes have complement receptors (CR) and can bind "flagged" pathogens (i.e., opsonized).
  • C3b can bind to CR1.
  • Formation of the membrane-attack complex (MAC) can lyse certain pathogens.

Antibody:Antigen Binds to C1q

  • Complement activation is initiated when antibodies attached to the surface of a pathogen bind C1q.
  • C1q cannot bind IgM or IgG in serum.
  • IgM must undergo a conformational change to expose binding sites.
  • IgG molecules must be adjacent to create 2 binding sites and sufficient affinity for C1q.

Antibody:Antigen Complexes

  • Antibody:antigen complexes may have too few molecules of IgG to efficiently bind to Fc receptors.
  • Antigen can be coated with complement and transported to relevant organs (e.g., spleen) for destruction.
  • This can lead to insoluble immune complex deposition and complement activation, leading to chronic inflammation in autoimmune diseases and serum sickness (Type III hypersensitivity).
  • Complement receptors are important in the removal of immune complexes from the circulation.

Summary

  • B cells present antigen to CD4+ Helper T cells to ensure full activation.
  • This leads to proliferation and differentiation into plasma or memory B cells.
  • Cytokines released by CD4+ T cells promote isotype class switching.
  • Germinal center reactions ensure maturation of the B cell response, resulting in higher affinity antibodies and isotype class switching.
  • B cells secrete immunoglobulin molecules (antibodies) that mediate effector functions:
    • Neutralization
    • Opsonization
    • Activation of complement pathway