Carbohydrate Metabolism Notes

Digestion and Absorption of Carbohydrates

  • Digestion: Breakdown of food molecules via hydrolysis into simpler units for metabolic use.

  • Carbohydrate Digestion:

    • Begins in the mouth with salivary alpha-amylase.

    • Alpha-amylase hydrolyzes alpha-glycosidic linkages in starch and glycogen, yielding smaller polysaccharides and maltose.

  • Limited carbohydrate digestion in the mouth due to quick swallowing.

  • Stomach:

    • Minimal carbohydrate digestion.

    • Lacks carbohydrate digestion enzymes.

    • Salivary amylase is inactivated due to stomach acidity.

  • Small Intestine:

    • Primary site for carbohydrate digestion.

    • Pancreatic alpha-amylase breaks down polysaccharides into maltose (a disaccharide).

  • Intestinal Mucosal Cells:

    • Final digestion step occurs on outer membranes.

    • Disaccharidase enzymes convert disaccharides (maltose, sucrose, lactose) into monosaccharides (glucose, fructose, galactose).

      • Maltase: maltose to glucose.

      • Sucrase: sucrose to glucose and fructose.

      • Lactase: lactose to glucose and galactose.

  • Absorption:

    • Monosaccharides (glucose, galactose, fructose) absorbed into bloodstream via intestinal wall.

    • Intestinal villi contain blood capillaries facilitating active transport of monosaccharides.

    • ATP hydrolysis and protein carriers mediate monosaccharide passage through cell membranes.

    • Galactose and fructose are converted to products of glucose metabolism in the liver.

Glycolysis

  • Six-Carbon Stage (Steps 1-3): Energy-consuming phase where phosphate derivatives of glucose and fructose are formed via ATP coupling.

  • Step 1: Formation of Glucose-6-Phosphate

    • Glucose phosphorylation: ATP transfers a phosphate group to carbon 6 of glucose.

    • Catalyzed by hexokinase.

    • Endothermic reaction fueled by ATP hydrolysis.

  • Step 2: Formation of Fructose-6-phosphate

    • Glucose 6-phosphate isomerized to fructose-6-phosphate.

    • Enzyme: phosphoglucoisomerase.

  • Step 3: Formation of Fructose 1,6-bisphosphate

    • Further phosphorylation of fructose-6-phosphate.

    • Endothermic, powered by ATP hydrolysis.

    • Enzyme: phosphofructokinase.

  • Three-Carbon Stage (Steps 4-10): Intermediates are derivatives of glycerol and acetone, all phosphorylated derivatives of dihydroxyacetone, glyceraldehyde, glycerate, or pyruvate.

  • Step 4: Formation of Triose Phosphates

    • Six-carbon molecule splits into two three-carbon molecules: dihydroxyacetone phosphate and glyceraldehyde 3-phosphate.

    • Enzyme: aldolase.

  • Step 5: Isomerization of Triose Phosphates

    • Dihydroxyacetone phosphate is isomerized to glyceraldehyde 3-phosphate.

    • Enzyme: triosephosphate isomerase.

  • Step 7: Formation of 3-Phosphoglycerate

    • Diphosphate converted back to monophosphate; ATP-producing step.

    • High-energy phosphate group from 1,3-bisphosphoglycerate transferred to ADP, forming ATP.

    • Enzyme: phosphoglycerokinase.

    • Two ATP molecules produced per original glucose molecule.

  • Step 8: Formation of 2-phosphoglycerate

    • Isomerization of 3-phosphoglycerate to 2-phosphoglycerate.

    • Phosphate group moved from C-3 to C-2.

    • Enzyme: phosphoglyceromutase.

  • Step 9: Formation of Phosphoenolpyruvate

    • Alcohol dehydration reaction creating another high-energy phosphate compound.

    • Enzyme: enolase.

  • Step 10: Formation of Pyruvate

    • High-energy phosphate transferred from phosphoenolpyruvate to ADP, producing ATP and pyruvate.

    • Enzyme: pyruvate kinase.

    • Two ATP molecules produced per original glucose.

    • Steps 1, 3, and 10 are control points for glycolysis.

  • Net ATP Production: A net gain of two ATP molecules for every glucose molecule processed in glycolysis.

  • Overall Glycolysis Equation:
    Glucose+2NAD++2ADP+2Pi2Pyruvate+2NADH+2H++2ATP+2H2OGlucose + 2NAD^+ + 2ADP + 2Pi \rightarrow 2Pyruvate + 2NADH + 2H^+ + 2ATP + 2H_2O

  • Entry of Galactose and Fructose: Both converted in the liver to intermediates that enter the glycolysis pathway.

    • Fructose: Phosphorylated by ATP to fructose 1-phosphate, then converted to glyceraldehyde (phosphorylated to enter glycolysis) and dihydroxyacetone phosphate.

    • Galactose: Phosphorylation by ATP yields glucose 1-phosphate, isomerized to glucose 6-phosphate.

  • Regulation of Glycolysis:

    • Control points: Steps 1, 3, and 10.

    • Step 1 (glucose to glucose 6-phosphate via hexokinase): Inhibited by glucose 6-phosphate (feedback inhibition).

    • Step 3 (fructose 6-phosphate to fructose 1,6-bisphosphate via phosphofructokinase): Inhibited by high ATP and citrate concentrations.

    • Step 10 (phosphoenolpyruvate to pyruvate via pyruvate kinase): Inhibited by high ATP concentrations. Pyruvate kinase and phosphofructokinase are allosteric enzymes.

Fates of Pyruvate

  • Oxidation to Acetyl CoA

    • Under aerobic conditions, pyruvate is oxidized to acetyl CoA by pyruvate dehydrogenase complex.

    • Acetyl CoA enters the mitochondrial matrix for processing in the citric acid cycle.

    • Most pyruvate from glycolysis is converted to Acetyl CoA.

  • Lactate Fermentation

    • Enzymatic anaerobic reduction of pyruvate to lactate, primarily in muscles.

    • Purpose: Converts NADH to NAD+ to increase the rate of glycolysis.

    • Lactate reconverted to pyruvate when aerobic conditions return.

    • Muscle fatigue from strenuous activity is due to lactate buildup.

  • Ethanol Fermentation

    • Enzymatic anaerobic conversion of pyruvate to ethanol and carbon dioxide.

    • Occurs in yeast and bacteria to regenerate NAD+.

    • Involves pyruvate decarboxylation (pyruvate decarboxylase) and acetaldehyde reduction to ethanol (alcohol dehydrogenase).

    • CO2 release during baking causes bread to rise.

    • Beer, wine, and alcoholic drinks are produced by ethanol fermentation of sugars.

    • Overall Reaction: Glucose+2ADP+2Pi2Ethanol+2CO<em>2+2ATP+2H</em>2OGlucose + 2 ADP + 2 Pi \rightarrow 2Ethanol + 2 CO<em>2 + 2 ATP + 2H</em>2O

  • Regeneration of NAD+ from NADH: Critical for continuing glycolysis under anaerobic conditions via lactate or ethanol fermentation.

ATP Production for Complete Glucose Oxidation

  • NADH from glycolysis (step 6) cannot directly enter the electron transport chain because mitochondria are impermeable to NADH and NAD+.

  • Glycerol 3-phosphate-dihydroxyacetone phosphate transport system:

    • Shuttles electrons from NADH (not NADH itself) across the mitochondrial membrane.

    • Dihydroxyacetone phosphate and glycerol phosphate freely cross the membrane.

    • Interconversion shuttles electrons from NADH to FADH2.

  • ATP Totals:

    • Muscle and nerve cells: 30 ATP molecules.

      • 26 from oxidative phosphorylation.

      • 2 from glucose to pyruvate.

      • 2 from GTP to ATP.

    • Heart and liver cells: 32 ATP molecules (using a more complex shuttle system).

  • Aerobic oxidation is more efficient than anaerobic processes by a factor of 15.

Glycogen Synthesis and Degradation

  • Glycogen: Branched polymer of glucose; storage form of carbohydrates in animals.

    • Muscle: Glucose source for glycolysis.

    • Liver: Maintains normal blood glucose levels.

    • Produced by glycogenesis.

  • Glycogenesis: Metabolic pathway for glycogen synthesis from glucose; involves three steps:

    • Formation of glucose 1-phosphate.

    • Formation of UDP glucose.

    • Glucose transfer to a glycogen chain.

  • Steps of Glycogenesis:

    • Step 1: Formation of glucose 1-phosphate from glucose 6-phosphate (from first step of glycolysis) via phosphoglucomutase.

    • Step 2: Formation of UDP glucose. UTP (uridine triphosphate) activates glucose 1-phosphate to UDP-glucose.

    • Step 3: Glucose transfer to glycogen chain. UDP-glucose glucose unit attached to the end of glycogen chain, producing UDP, which reacts with ATP to form UTP and ADP.

    • Adding one glucose unit to glycogen requires two ATP molecules (one for glucose 6-phosphate formation and one for UTP regeneration).

  • Glycogenolysis: Breakdown of glycogen to glucose-6-phosphate.

    • Not the reverse of glycogenesis; does not require UTP or UDP.

    • Two-step process: phosphorylation of a glucose residue and glucose 1-phosphate isomerization.

  • Steps of Glycogenolysis:

    • Step 1: Phosphorylation of a glucose residue. Glycogen phosphorylase removes an end glucose residue from glycogen as glucose 1-phosphate.

    • Step 2: Glucose 1-phosphate isomerization. Phosphoglucomutase isomerizes glucose 1-phosphate to glucose 6-phosphate (reverse of glycogenesis step one).

  • Glucose 6-phosphate enters glycolysis pathway.

    • Low glucose stimulates glycogenolysis in liver cells.

    • Glucose 6-phosphate is ionic and cannot cross the membrane.

    • Enzyme glucose 6-phosphatase (in liver, kidneys, intestine) converts glucose 6-phosphate to glucose.

    • Not present in muscle and brain tissues.

    • Free glucose transported to muscle and brain via blood.

Gluconeogenesis

  • Metabolic pathway for glucose synthesis from non-carbohydrate sources; not an exact reversal of glycolysis.

  • Glycogen stores depleted within 12-18 hours of fasting or less with heavy activity.

  • Maintains normal blood-glucose levels during inadequate carbohydrate intake.

  • 90% of gluconeogenesis occurs in the liver.

  • Noncarbohydrate Starting Materials: Pyruvate, lactate (from muscles and red blood cells), glycerol (from triacylglycerol hydrolysis), certain amino acids (from dietary protein hydrolysis or muscle protein during starvation).

  • Overall Reaction: 2Pyruvate+4ATP+2GTP+2NADH+2H2O»Glucose+4ADP+2GDP+6Pi+2NAD+2 Pyruvate + 4ATP + 2GTP + 2NADH + 2H_2O \rightarrow »Glucose + 4ADP + 2GDP + 6Pi + 2NAD^+

  • Requires 4 ATP and 2 GTP, occurring at the expense of other ATP-producing processes.

  • Cori Cycle: Utilizes lactate as a pyruvate source.

    • Lactate from muscle cells enters the bloodstream and is transported to the liver.

    • Lactate dehydrogenase converts lactate to pyruvate in the liver.

    • Pyruvate is converted to glucose via gluconeogenesis.

    • Glucose enters bloodstream and is transported to muscles.

Terminology for Metabolic Pathways

  • Glycogenesis: Glycogen synthesis from glucose 6-phosphate (2 steps).

  • Gluconeogenesis: Pyruvate conversion to glucose (11 steps).

  • Glycolysis: Glucose conversion to pyruvate (10 steps).

  • Glycogenolysis: Glycogen conversion to glucose 6-phosphate.

  • "Lysis" = Breakdown, "Genesis" = Synthesis

Pentose Phosphate Pathway

  • Metabolic pathway using glucose to produce NADPH, ribose 5-phosphate (a pentose phosphate), and other sugar phosphates.

  • NADPH: Reduced form of NADP+ (nicotinamide adenine dinucleotide phosphate); phosphorylated version of NAD+/NADH; essential for biosynthetic pathways.

  • Two Stages:

    • Oxidative stage: Glucose 6-phosphate to ribulose 5-phosphate and CO2 (three steps).

    • Nonoxidative stage: Ribulose 5-phosphate (ketose) isomerized to ribose 5-phosphate (aldose).

  • Cellular Roles:

    • When ATP demand is high, end products enter glycolysis.

    • When NADPH demand is high, intermediates are recycled to glucose 6-phosphate for further NADPH production.

    • Generates ribose 5-phosphate for nucleic acid and coenzyme production.

Hormonal Control of Carbohydrate Metabolism

  • Second major control method (besides enzyme inhibition).

  • Three major hormones: Insulin, Glucagon, Epinephrine.

  • Insulin:

    • Produced by beta cells of the pancreas.

    • 51 amino acid polypeptide.

    • Promotes glucose utilization by cells; lowers blood glucose levels; involved in lipid metabolism.

    • Release triggered by high blood-glucose levels.

    • Mechanism: Binds to protein receptors on cell surfaces, facilitating glucose entry and increasing glycogen synthesis rate.

  • Glucagon:

    • Produced in the pancreas by alpha cells.

    • 29 amino acid peptide hormone.

    • Released when blood glucose levels are low.

    • Increases blood-glucose concentration by speeding up glycogenolysis in the liver.

    • Opposite effects of insulin.

  • Epinephrine:

    • Also called adrenaline.

    • Released by adrenal glands in response to anger, fear, or excitement.

    • Similar function to glucagon; stimulates glycogenolysis with a primary target of the muscle cells.

    • Promotes energy generation for quick action and functions in lipid metabolism.