13 - lens

describe why the embryology of the lens leads to lens fibers being unrecognized as self by the immune system

the lens fibers develop entirely within the confines of the lens capsule, which is basement membrane of the epithelial cells

because lens fibers never have contact with the immune system, self-tolerance never develops for them

list factors that contribute to transparency of the lens

  1. avascularity

  2. lack of pigmentation

  3. no keratinization

  4. precise arrangement

  5. minimal organelles

  6. precise protein ratios

  7. low hydration

  8. precise regulation of hydration level

what is the normal function of the lens

focus light rays onto the retina → optimal vision and image processing

what is a cataract? what is nuclear sclerosis? how are the two differentiated?

cataract

increased opacity of the lens

occurs when osmotic effects break lens fibers, insoluble proteins outnumber soluble proteins

leads to vision loss

nuclear sclerosis

highly compacted nuclear lens fibers

blue-grey opalescent appearance to center of lens

usually bilaterally symmetric

differentiation

cataract is opaque → light is disorganized or blocked, prevents view of retina, tapetal reflection is lost in mature stages, may be unilateral or bilateral

nuclear sclerosis is transparent, retina is visible with ophthalmoscope, tapetal reflection is maintained, usually bilaterally symmetric

describe cataracts by stage of development

incipient → earliest and smallest visible cataract. <10% of lens is opaque

immature → >10% of lens is opaque. tapetal reflection may be seen and some retinal detail observable

mature → solid, opaque, white marble. no tapetal reflection or retinal detail seen. PLRs remain normal as long as retina is normal

hypermature → lens starting to shrink and reabsorb. capsule is wrinkled with ragged edges

morgagnian → nucleus liquefies, may sink to bottom of lens

list causes of cataract formation

3 types: hereditary, senile, ocular manifestation of systemic disease

genetic

diabetic

secondary to Progressive retinal atrophy

secondary to uveitis

traumatic, electric shock

nutritional

radiation

secondary to iris-to-lens persistent pupillary membranes

secondary to hyaloid artery/tunica vasculosa lentis

how are PLRs affected by mature cataracts

they’re not, as long as the retina is undamaged

why lens-induced uveitis occurs, how it is treated, and why it must be treated chronically

cataract causes inflammation due to leakage of lens proteins

tx: topical anti-inflammatories

chronic uveitis can lead to secondary glaucoma, retinal detachment, posterior synechiae and keratitis

what is the pathogenesis of diabetic cataract formation

elevated blood glucose → elevated aqueous glucose → elevated lens glucose → normal anaerobic glycolysis (by aldose reductase) is overwhelmed → metabolism shunted to sorbitol pathway → increased osmolality → fluid sucked into lens fibers → swell and break

identify the only treatment option for restoring vision to patients blinded by cataracts

surgical removal of cataract

what breed of dog is genetically predisposed to primary lens luxation? what is the genetic defect that leads to primary lens luxation

Jack Russell terriers & related breeds

know the differences between primary and secondary lens luxation

primary

due to genetic defect → zonular dysgenesis → instability in lens position

secondary

loss of zonules caused by intraocular disease → uveitis, claucoma, neoplasm, trauma

know the difference between lens subluxation and lens luxation

subluxation

lens is only partially dislocated

some zonules remain attached to lens

diagnose via presence of aphakic crescent

luxation

lens is completely dislocated from its normal position

all zonular attachments lost

almost always preceded by subluxation

can be anterior or posterior (posterior less painful)

know the definition of aphakic crescent

space between lens equator and pupillary margin