Class 4: Functional Genomics

Rhodopsin and TB12 Mice

  • Rhodopsin: A light-sensitive receptor protein involved in visual phototransduction.

  • In TB12 mice: These mice are blind due to a genetic defect that impedes the production of rhodopsin.

  • The number of rhodopsin molecules in rod cells of TB12 mice is less than that in wild-type mice.

  • Discussion Prompt: Potential gene mutation in TB12 mice impacting rhodopsin production; students encouraged to discuss with neighbors.

Understanding Retinal

  • Retinal: A pigment, not a protein, hence there is no specific "retinal gene".

  • It is a product of a biosynthetic pathway initiated by beta-carotene.

  • Parents often encourage carrot consumption as a source of beta carotene.

  • Genetic defects may impact retinal production through enzymes involved in its biosynthesis (blue arrows represent these enzyme-catalyzed steps).

Proteins and Cofactors

  • Opsin: The protein component that combines with retinal to form rhodopsin; referred to as an apoprotein.

  • Cofactor: Retinal acts as a cofactor for opsin; it is essential for opsin's functionality.

  • Numerous proteins require cofactors to function, while others operate without post-translational modifications.

Genetics: Phenotype and Genotype Link

  • Important domain in biology is linking phenotype (observable traits) with genotype (genetic makeup).

  • Reverse Genetics: Begins with a specific gene to explore its functions and impacts when mutated. (play with it and see what it does)

  • Forward Genetics: Starts with a known phenotype to identify the genotype and underlying genetic cause. (finding the mutant genes in people with cystic fibrosis)

Mutagenesis Techniques in Research

  • Importance of identifying mutant phenotypes in genetics, particularly for rare diseases like cystic fibrosis.

  • Example: Cystic fibrosis has been recognized for centuries with a distinct phenotype, yet its genotype was mapped only in recent history.

Clammy as a Model System

  • Ciliopathies Lab: The lab works with clammy (likely Chlamydomonas reinhardtii) to study flagella development.

  • The lab employs insertional mutagenesis to create a pool of mutant geniuses by inserting DNA that disrupts normal gene function.

  • Bleomycin Resistance: As a result of mutagenesis, cells gain resistance to the antibiotic bleomycin, aiding in identifying mutants.

Screening for Mutant Phenotypes

  • Strategy involves screening multiple mutants in a 96 well plate format for specific phenotypic characteristics, such as flagella defects.

  • Wild-type cells clump due to tangled flagella, providing a visual cue to differentiate them from mutants lacking functional flagella.

Genetic Complementation

  • To confirm a gene's role in a phenotype, researchers perform genetic complementation by introducing a wild-type gene copy in a mutant cell to restore/functionality.

  • The restoration of the phenotype (e.g., flagella formation) indicates the gene is essential for the trait being studied.

Future Directions and Discussions

  • Students are encouraged to engage in discussions, seek clarifications after class, and explore the implications of these genetic studies.