6.2. Exam I- Intro, Lymphatic, Immune, Inflam, Cardio, Pulm COMBINED

Introduction to Pathology

Objectives

  • Define key terms related to pathology.

  • Analyze the models of health and illness.

  • Determine the 4 aspects of the biopsychosocial model of pain.

  • Clarify the genetic aspects of health and illness.

  • Explain the lifestyle factors that affect health.

  • Describe health promotion and disease prevention and physical therapy practice implications.

  • Assess epigenetics and implications for PT practice.

  • Compare and contrast the increased health risks with obesity and physical therapist practice implications.

  • Define stress and describe the impact of stress on the organism.

  • Define and describe various psychiatric disorders.

  • Discuss the impact of these disorders on the provision of healthcare services to the patient/client.

  • Describe the role of the physical therapist in addressing the needs of the patient/client with these disorders.

Terms and Definitions: Disease vs. Illness

  • Disease:

    • Biologic/Psychologic changes leading to organ or system malfunction.

    • Biomedical condition(s) indicating disturbances in normal health.

    • Objective changes.

    • Can occur without a person being aware of the illness.

  • Illness:

    • Perception/response of a person to not being well.

    • Biologic, personal, interpersonal, & cultural reactions to disease.

    • A person can feel ill without an obvious pathologic process identified.

Illness: Acute, Subacute, and Chronic

  • Acute:

    • Rapid onset & short duration.

    • Usually self-limiting.

    • Responds to specific treatment.

  • Subacute:

    • Time course between acute & chronic.

    • Present for > few days, but < several months.

  • Chronic:

    • Permanent impairment or disability.

    • Residual physical or cognitive disability.

    • Need for rehabilitation and/or long-term medical management. Characterized by several of the above features.

Terms and Definitions: Incidence vs. Prevalence

  • Incidence:

    • Measurement of the # of new cases of a disease during a particular period of time.

    • Measures rate of occurrence of disease.

    • Leads to probability (risk) of being diagnosed with a disease during a given period of time.

  • Prevalence:

    • Refers to the total # of cases of a disease in a population during a specific time period.

    • References how widespread a disease has become.

    • Indicates impact of disease on population.

    • Includes length of time disease has been encountered & includes old/new cases.

Etiology and Clinical Manifestations

  • Etiology: Cause(s) of a disease or condition.

  • Clinical Manifestations:

    • Symptoms (subjective).

    • Signs (objective).

Morbidity, Premorbidity, and Comorbidity

  • Morbidity: Diseased state or symptom.

  • Premorbidity: State of function prior to disease.

  • Comorbidity: > 1 disease at the same time.

Mortality and Mortality Rate

  • Mortality: Death.

  • Mortality rate: # of deaths due to disease/total population.

    • Taken according to age, sex, area, type of disease.

    • Several types: infant, perinatal, child, maternal, crude, standardized, & age-specific.

Disability (WHO Definition)

  • Physical and/or cognitive condition that limits a person’s movements, senses, or activities.

  • World Health Organization (WHO) Definition Covers:

    • Impairments: problems in body function/structure.

    • Activity limitations: Difficulty in executing a task/action.

    • Participation restrictions: Difficulty with involvement in life situations.

Health Promotion

  • Built on the principles of self-responsibility, nutritional awareness, stress reduction and management, and physical fitness.

Disease Prevention

  • More cost-effective than treating disease.

  • 3 branches of preventive medicine:

    • Primary – Remove or ↓ disease risk factors.

    • Secondary – Promote early detection, initiate preventive measures for complications.

    • Tertiary – Limit impact of established disease.

Primary, Secondary, and Tertiary Prevention Examples

  • Primary:

    • Good nutrition, calcium & D3 intake, regular weight-bearing exercises, not smoking to prevent osteoporosis.

  • Secondary:

    • Skin tests for TB, mammography, colonoscopy, routine cervical Pap smear.

  • Tertiary:

    • Rehabilitation to return to the highest level of function.

Disease Prevention & Physical Therapy

  • Earlier PT intervention → decreased acute care length.

  • Major roles in secondary & tertiary care.

    • Secondary: Wide range of settings from hospitals to preschools.

    • Tertiary: highly specialized, complex, & technologically based settings.

  • Prevention/Wellness Role:

    • Prevention/wellness activities.

    • Screening programs.

    • Promotion of positive health behaviors.

Impact of Physical Therapy

Clinical Models of Health

Biomedical Model
  • Model for centuries.

  • All illness due to disease and physiologic processes.

  • Psychologic, social and spiritual influences independence of disease.

  • Focuses on internal factors only.

  • Illness is a deviation of the healthy state.

Biopsychosocial Model
  • Biologic, psychologic, and social variables are key factors in health and illness.

  • Mind and body cannot be separated.

  • Psychologic factors include cognition, emotion, motivation, along with biologic/environmental factors = various health states.

  • Family, community, and society interactions influence health outcomes.

Biopsychosocial-Spiritual Model
  • Developed with the advent of holistic health.

  • Recognizes the healing potential of faith, spirituality, and religious beliefs.

  • Social and spiritual support are important for the promotion of health, decreasing susceptibility to disease, and facilitating recovery.

Social-Ecologic Model
  • Theoretical principles for understanding interrelations among diverse personal and environmental factors in health and illness.

  • Health is affected by the interaction between the individual, group/community, and physical, social, political environments.

Epigenetics: Behavioral, Social, Environmental Factors and Health Implications

  • Epigenetics: Study of how behaviors and environment can cause changes that affect the way genes function.

    • Based on the Social-Ecological Model of Health.

  • Describes heritable mechanisms that are reversible.

    • Occurs without alteration of underlying DNA sequence.

    • The expression of DNA and subsequent reading of the gene can be altered or manipulated.

    • The mind is considered the "master controller" of gene expression.

    • Change occurs by becoming aware of individual perceptions, beliefs, and attitudes, behaviors, and lifestyle choices.

  • Goodman and Fuller Chapter 2.

Epigenetics and Role of Physical Therapist

Epigenetics: Lifestyle Factors Influencing Health

  • Cultural influences

  • Socioeconomic status

  • Generational Differences

  • Adverse childhood experiences

  • Physical activity

  • Nutrition

  • Obesity

  • Smoking/tobacco use

  • Alcohol/drugs

  • Domestic abuse

Epigenetic Factors Influencing Health

  • Individual

  • Family

  • Community

  • Society

Physical Therapist Practice Implications

  • Co-morbidity with referral to PT.

  • Understanding & sensitivity of symptoms.

  • Understanding and removal of biases.

  • Plan of care and goals.

  • Include patient in goal setting.

  • Repetition of intervention implications.

  • Recognize for referral when not diagnosed.

Lymphatic System

Overview

  • The lymphatic system plays a key role in:

    • The immune system.

    • Fluid balance.

    • Absorption of fats and fat-soluble nutrients.

  • It moves fluid from the periphery to central circulation, maintaining fluid balance between blood and tissues (fluid homeostasis).

  • It is part of the body’s immune system and:

    • Fights infection.

    • Assists in the removal of cellular debris and waste products.

  • It absorbs fats/fat-soluble nutrients from the digestive system and transports these fats to blood circulation.

Function

  • 90% of extracellular fluid re-enters circulation via the venous capillary system.

    • Approximately 2 liters of fluid leak from the cardiovascular system into body tissues daily.

  • The remaining 10% returns to the heart via the lymphatic system.

    • This includes fluid and larger protein molecules too large for the venous system (lymph).

    • It operates as a pressure-driven system based on osmotic diuresis.

      • Fluid is drained progressively towards larger vessels to lymphatic ducts.

  • Disruptions to the normal lymphatic transport mechanism lead to accumulations of water/protein in tissue space.

Lymph Nodes

  • All lymph passes through lymph nodes.

    • Lymph nodes act as filters to cleanse the lymph of waste products and cellular debris.

    • Nodes produce lymphocytes and macrophages critical for immune function; they destroy foreign bacteria, viruses, and cancer cells and filter waste products.

    • Vessels distal to nodes are called afferent lymph vessels, while vessels leaving lymph nodes are called efferent lymph vessels.

Lymphatic Ducts

  • Lymph empties into the Right Lymphatic Duct and Thoracic Duct.

  • Lymph returns to the bloodstream via the Left and Right Subclavian Veins.

Cervical Lymph Nodes

  • Located throughout the head and neck.

  • Drains fluid from the head and neck.

  • There are approximately 300 cervical lymph nodes.

Axillary Lymph Nodes

  • Located around the axillary region.

  • Drains from upper extremities (UEs) and the upper quadrant.

  • There are approximately 30 axillary lymph nodes.

Inguinal Lymph Nodes

  • Located in the upper inner thigh.

  • Drains fluid from lower extremities (LEs), external genitalia, and the lower quadrant.

  • There are approximately 12 inguinal lymph nodes.

Lymphatic Organs

  • Thymus:

    • Produces mature T-lymphocytes important for adaptive immunity response.

  • Spleen:

    • Processes damaged blood cells and microorganisms.

    • Supports immunity.

  • Tonsils & Adenoids:

    • Trap pathogens that enter the mouth/nose.

    • Produce leukocytes.

  • Peyer’s Patches:

    • Small masses of lymphatic tissue that monitor intestinal bacteria.

    • Carries leukocytes and may store beneficial gut bacteria.

Disorders of the Lymphatic System

  • Lymphangitis: Inflammation of a lymphatic vessel.

  • Lymphadenitis: Inflammation of one or more lymph nodes.

  • Lymphadenopathy: Enlargement of lymph nodes.

  • Lymphedema: Increased amount of lymph fluid in the soft tissues.

  • Lipedema: Deposition and hypertrophy of subcutaneous fat.

Lymphangitis vs. Lymphadenitis

Lymphadenitis
  • Acute or chronic inflammation of one or more lymph nodes.

  • Often painful.

    • Acute:

      • Nodes asymmetrically enlarged, tender, warm, reddened.

    • Chronic:

      • Nodes are firm, scarred with fibrous connective tissue, without tenderness or pain.

Lymphangitis
  • Acute inflammation of subcutaneous lymphatic channels that causes pain and streaks.

  • Spreads away from the original infection site toward the lymph node.

  • Mandibular, cervical, inguinal, and axillary regions are most often involved (in order).

  • Nodes are generally tender to palpation and enlarged.

  • Systemic manifestations include fever, chills, malaise, and anorexia.

Lymphadenopathy

  • Swelling/enlargement of lymph nodes.

    • Secondary to a wide range of bacterial, viral, or fungal infections, autoimmune disease, and malignancy.

  • Not always inflamed or painful.

  • Can be localized or regional (enlargement in a particular body area) or generalized (enlargement of 2 or 3 noncontiguous lymph node groups).

  • Dermatopathic: associated with skin disease.

  • Treatment depends on the underlying cause (infections, lymphomas, leukemia).

Lymphedema

  • Swelling of soft tissues from the accumulation of protein-rich fluid in extracellular spaces.

  • Caused by decreased lymphatic transport capacity and/or increased lymphatic load.

  • Most common in extremities.

  • Two broad categories:

    • Primary (idiopathic).

    • Secondary (acquired).

  • Severity graded using a scale from the International Society of Lymphology.

Stages of Lymphedema
  • Stage 0 (Latent Lymphedema):

    • Lymph transport capacity reduced.

    • No clinical edema is present.

  • Stage I:

    • Accumulation of protein-rich, pitting edema.

    • Reversible with elevation: the area affected may be a normal size upon waking in the morning.

    • Increases with activity, heat, and humidity.

  • Stage II:

    • Accumulation of protein-rich, nonpitting edema with connective scar tissue.

    • Irreversible; does not resolve overnight; increasingly more difficult to pit.

    • Clinical fibrosis is present.

    • Skin changes present in severe Stage II.

  • Stage III (Lymphostatic Elephantiasis):

    • Accumulation of protein-rich edema with a significant increase in connective and scar tissue.

    • Severe nonpitting fibrotic edema.

    • Atrophic changes (hardening of dermal tissue, skin folds, skin papillomas, hyperkeratosis).

Primary vs. Secondary Lymphedema
  • Primary:

    • Approximately 15% present at birth.

    • Most common form occurs from adolescence to midlife.

    • The exact cause is unknown and NOT linked to any significant traumatic event.

    • Most likely the result of malformation of lymphatic vessels is present at birth, with 3 types of malformation:

      • Aplasia: lymphatic collectors are so few and considered absent.

      • Hypoplasia: < normal expected # in the affected region, or collectors are present but not functional (most common).

      • Hyperplasia: grossly dilated & enlarged lymphatics.

  • Secondary:

    • Results from damage to lymphatic vessels or nodes from a known entity.

    • The most common cause worldwide is filariasis (a parasitic infection carried by mosquitoes in Africa, South America, India, and Malaysia).

    • The most common cause where the filaria parasite does not exist is invasive procedures used in the diagnosis & treatment of cancer, regional lymph node dissection, or local radiation treatment.

    • Other causes: bacterial/viral infections, multiple abdominal surgeries, trauma or surgery that impairs lymphatics, repeated pregnancies.

    • Crush injuries, compound fractures, severe lacerations, degloving injuries.

Clinical Manifestation of Lymphedema
  • Swelling of part or all of the affected part.

  • A feeling of heaviness or skin tightness.

  • Restricted range of motion: decreased flexibility.

  • Aching, discomfort, burning, and pain.

  • Recurring infections.

  • Hardening and thickening of the skin (fibrosis).

  • Increased circumferential limb girth.

  • Postural changes.

  • Neuromuscular deficits.

  • May lead to functional changes.

Complications of Lymphedema
  • Progression of lymphedema leads to thickening of the dermal skin layer, which causes the skin to dry and crack, often leading to ulcerations.

  • Decreased oxygen delivered to body parts.

  • Decreased ability to heal.

  • Skin folds and tissue flaps can develop, leading to the development of fungal and bacterial infections, further skin damage, and a new portal of entry for bacteria.

  • Increased girth and weight lead to changes in gait pattern with increased fatigue and inactivity, leading to decreased functional ROM and strength.

Physical Therapy Examination and Evaluation

  • Past Medical History VERY important.

  • Description of skin integrity (more to be learned from Dr. Gibbs’ integumentary lecture); presence of edema or fibrosis; location & condition of scars, fibrotic areas, open wounds; evidence of healed ulcerations.

  • Signs/symptoms of cording.

  • Photographs help detail changes.

  • Evaluation of function, strength, ROM, balance, and gait.

  • Circumferential measurements.

  • Volume measurements.

  • Bioimpedance spectroscopy.

Physical Therapy Interventions

  • Manual Lymph Drainage (MLD).

  • Compression Bandaging (More detail from Dr. Gibbs on bandaging and garments).

  • Compression garments.

  • Exercise.

  • Intermittent Pneumatic Compression Pumps.

  • Patient Education (basic anatomy, skin/nail care, self-MLD, self-bandaging, garment care, infection management).

  • Home Program.

  • Guidelines for Job & Lifestyle Modifications.

  • Psychologic & emotional support.

Immune System

Learning Objectives

  • Identify terms/definitions associated with the immune system.

  • Discuss types of immunity and related functions.

  • Explain immune system responses.

  • Recognize organs of the immune system and their functions.

  • Compare and contrast different classifications of immune disorders and their signs/symptoms, including clinical applications.

Terms & Definitions

  • Immunology: Study of physiologic mechanisms allowing the body to recognize and neutralize/eliminate pathogens & other foreign components.

  • Immune System: Network of specialized organs peripherally and centrally providing immediate warning & action against pathogens and foreign substances.

    • Purpose:

      • Control or eradicate pathogens/foreign substances.

      • Protect from disease.

  • Immunity: Protection against infectious disease (innate & adaptive).

  • Pathogen: Foreign organism capable of producing disease (bacteria, viruses, fungi).

  • Phagocytes: Leukocytes that protect the body by ingesting (phagocytosing) harmful foreign particles, bacteria, and dead or dying cells.

  • Phagocytosis: Process used by cells to engulf and ingest particles of nutrients or bacteria.

  • Antigen: Molecule attached to a pathogen, located in the pathogen cell wall, stimulating the production of an antibody.

  • Antibody: "Immunoglobulins" produced by B-lymphocytes (plasma cells). Antigen-specific, binding to and destroying specific antigens (lock & key method).

Innate Immunity

  • Present prior to exposure; encoded in genome.

  • Mediates the first line of immunological defense against pathogens (quick response).

  • Provides a broad range of protection and recognizes any invading pathogen.

  • Non-specific interaction with different antigens.

  • Receptors recognize general patterns of common pathogens.

  • Lacks immunologic memory.

External & Internal Innate Immunity response
  • Exterior Defenses:

    • Skin, mucosa, secretions, nasal hair, ear wax.

  • Internal Defenses:

    • Soluble Factors:

      • Complement system, immune mediators.

    • Cellular components: phagocytes (leukocytes: white blood cells)

      • Produced in bone marrow.

      • Neutrophils, macrophages/Monocytes, basophils, mast cells.

      • Natural Killer Cells.

Soluble Factors
  • Complement System (complement cascade):

    • 3030 small proteins synthesized by the liver.

    • Mark pathogens, attracting WBCs and other immune cells from the blood = “complements" their ability to destroy pathogens.

    • Dissolve cell walls of bacteria → cell death.

    • Destroy virus envelopes.

    • Destroy cells infected by viruses.

    • Enhance strength/activity of innate & adaptive responses.

  • Functions:

    • Enhances the ability of antibodies/phagocytic cells to clear microbes.

    • Promotes inflammation.

    • Attacks pathogen’s cell membrane → cell lysis.

  • Final outcomes:

    • Final smaller proteins of cascade attach to the surface of the pathogen → increased inflammatory response.

    • Opsonization: Tag pathogen → more susceptibility to phagocytosis.

    • Forms membrane attach complex → attaches to pathogen membrane → causes pathogen lysis.

    • Enhances removal of immune complexes formed by antibody/antigen binding.

Soluble Factors: Immune mediators
  • Restrict proliferation of pathogens.

    • Cytokines: Cell signaling soluble proteins → signal the immune system to activate.

      • Stimulate movement of cells towards sites of inflammation, infection, trauma.

    • Chemokines: Small cytokines → migration of leukocytes & enhance inflammation.

      • Actions of cytokines/chemokines: ↑ vascular permeability, ↑ vascular epithelial tissue activation, change blood flow & leukocyte migration, chemotactic properties.

    • Type I interferons:

      • Cytokines produced by infected cells.

      • Limit spread of infection → Protect uninfected cells.

Major Cellular Components of Innate System
  • Neutrophil

  • Basophil

  • Mast Cells

  • Monocyte

  • Natural Killer Cell

  • Macrophage

Cellular Components of Innate System
  • Neutrophils:

    • First responder against pathogens.

    • Increased with infection & inflammation → indicates acute infection.

  • Monocytes:

    • Largest of WBCs.

    • Respond to infections/inflammation → mature into macrophages.

    • Neutrophils kill pathogens → macrophages “filter” the debris (phagocytosis), kill any large bacteria.

    • (Neutrophils and Monocytes) Classified as leukocytes (principal families of professional phagocytes)

  • Eosinophils:

    • Activated with antigens too large for neutrophils (↑ allergies & parasitic infections).

  • Basophils:

    • Granulocytes releasing histamine (vasodilator).

    • Major role in certain allergic responses.

  • Mast cells:

    • Release histamine.

    • Major role in allergy & anaphylaxis.

    • Active in wound healing.

  • Dendrites (Antigen-presenting cell (APC)):

    • Located in tissue in contact with the external environment.

    • Skin, nose, lungs, stomach, intestines.

    • Messengers between innate & adaptive systems.

    • Processes antigen material → attract adaptive system components.

  • Natural Killer Cells:

    • Large cytotoxic granular lymphocyte.

    • Attacks viral and tumor cells.

    • Membrane to membrane contact.

    • Releases enzymes & bores pores in the cell membrane.

    • Proteins enter → cell death.

Adaptive Immunity

  • Activated if innate immune response fails to control and eliminate pathogen.

    • The threat continues at a certain level for a certain amount of time: activation threshold.

  • Antigen-Specific & has memory.

  • Goal: recognize threat, promote immune response, destroy invader, establish long-term memory → continually develops throughout lifetime.

  • Result of active or passive immunity.

    • Active: Introduction of antigen into the body (naturally and artificially (vaccination)).

    • Passive: Immune products from immune person transferred to nonimmune person.

      • Transplacental transfer.

      • Breast milk.

Immune System Response: 3 Lines Of Defense
  • First line of defense (innate).

    • Mechanical & Chemical Barriers.

    • Inhibits invasion of pathogens.

  • Second line of defense (innate).

    • Inflammatory response & phagocytosis.

  • Third line of defense (adaptive).

    • Specific immune responses (T & B Lymphocytes).

Adaptive Immunity
  • Composed of T-lymphocyte & B- Lymphocyte cells.

  • Two categories:

    • Humoral Immunity (B-cell immunity).

      • Antibody-mediated.

    • Cell-mediated immunity (T-cell immunity).

Humoral Immunity

  • Protects extracellular spaces.

  • Mediated by antibodies produced by B lymphocytes.

  • B cells develop in bone marrow, migrate to blood, spleen & lymph nodes.

  • Each B-cell is specific for a particular antigen outside the cell → destruction of pathogen.

  • Rely on Helper T-cells for optimal function.

    • Help activate B-Cells to secrete antibodies.

B-Cell Immune Response
  • B-Cells: lymphocytes.

  • B-Cell function: recognize antigens.

  • Mature into antibody-producing plasma B-cells or into memory B- cells.

  • Antibodies: Y-shaped proteins that bind to antigen.

  • B-Cell breaks down antigen.

  • Antigen-specific antibodies → neutralize or destroy antigens.

    • Activate complement system → lysis of pathogen.

    • Neutralize viruses/toxins released by bacteria.

    • Stimulates phagocytoses of antigen.

  • Memory cells enable faster production of antibodies to specific antigens in the future.

Cell-Mediated Immunity (T-Cells)

  • T-cells: produced in bone marrow and then released to mature in thymus.

  • Mature T-cells recirculate through the bloodstream & peripheral lymphoid organs constantly.

  • T-Cells encounter antigen → attach and divide into 4 different variations.

  • T-cells bind with antigens rather than release antibodies as B-cells do.

  • Protects against infection by intracellular pathogens (rather than in blood).

  • Each T-cell makes only 1 kind of T-cell antigen receptor.

Cellular Immune Response
  • Helper T-cell binds to antigens on cell surface → chemical messengers are released that acitvate:

    • Activates cytotoxic T-cells, B-cells, macrophages.

    • Required for most adaptive immune responses.

  • Cytotoxic T-cells (Killer T-Cells) are activated & bind with antigen → release potent chemical, perforin, that perforates cell membrane.

    • Cell death by lysis results.

  • Infection brought under control → regulatory or suppressor T-Cells deactivate Killer T-Cells.

  • Memory T-cells produced for quick response in the future.

Humoral/Cell Mediated Immunity Differences

Humoral

Cell-Mediated

B-cells

T-cells

Antibodies secreted

Antibodies not secreted

Cells, themselves, bind to antigens

Destroys extracellular microorganisms

Destroys intracellular organisms

Antibodies used for defense

Receptors used for defense

Immunodeficiencies

  • Immune response is absent or depressed.

  • Categories:

    • Primary Immunodeficiency Diseases.

    • Secondary Immunodeficiency Disorders.

    • Iatrogenic Immunodeficiency.

    • Human immunodeficiency virus (HIV).

    • Chronic Fatigue syndrome.

Immunodeficiencies types
  • Primary Immunodeficiency:

    • Group of over 450450 rare, chronic disorders.

    • Congenital defect involving T cells, B cells, or lymphoid tissues, NK cells, phagocytic cells, and complement proteins.

    • Failure of organ development necessary for lymphocyte maturation or born without certain antibody types.

    • Indications: Infection that is severe, persistent, unusual, recurrent, or runs in the family.

  • Secondary Immunodeficiency:

    • Also referred to as Acquired Deficiencies.

    • More frequent than Primary Immunodeficiencies.

    • Results from underlying disease or factor that depresses/blocks immune response: not genetic.

    • Can occur in malnutrition, stress, CA treatment, leukemia, chronic diseases such as DM & renal failure, undergoing chemotherapy, later stages HIV.

  • Iatrogenic Immunodeficiency:

    • Induced by immunosuppressive drugs, radiation therapy, or splenectomy.

Human Immunodeficiency Virus (HIV)

  • Infection or gradual weakening of the immune system.

  • Occurs with the exchange of body fluids.

  • Progressive destruction of T4 (Helper T-cells) lymphocytes (CD4 cells): major regulators of immune response.

  • HIV unique: some virus escapes despite immune responses.

  • Slow growth of the virus between acute infection & onset of symptoms.

  • Untreated → profound immunosuppression results → susceptibility of opportunistic infections (ex. Unusual cancers, tuberculosis, etc.).

  • Advanced or late-stage HIV disease → formally known as acquired immune deficiency syndrome (AIDS).

  • Immunodeficiency → infections & unusual malignancies.

  • Pain Syndromes, musculoskeletal & Neuromuscular/neurologic, cardiopulmonary, integumentary diseases.

  • No cure but considered the manageable chronic condition (with RX) with medications.

HIV & Rehabilitation
  • May not be diagnosed: Importance of examination/evaluation.

  • Standard precautions.

  • Plan of Care based on HIV disease status & impairments.

  • Focus on the management of specific impairments & functional limitations.

    • Pain management.

    • Balance & Gait training.

    • Posture, body mechanics.

    • Stretching & strengthening → do not over fatigue.

    • Exercise à Improve function.

Chronic Fatigue Syndrome

  • 0.230.42%0.23-0.42\% prevalences among adults in the US.

  • Fatigue may worsen with physical/mental activity, does not improve with rest.

  • Cause: unknown → difficult to diagnose.

  • Theories: triggered by a combination of factors -- hormonal imbalances (thyroid, cortisol), viral infections (Epstein Barr), weakened immune system, psychological stress.

  • Treatment focuses on symptom relief.

  • Medical tests are needed to rule out other health problems.

CFS Diagnosis Criteria
  1. Severe chronic fatigue for > 66 consecutive months not due to ongoing exertion or other medical conditions associated with fatigue (These other conditions must be ruled out after diagnostic testing).

  2. Fatigue significantly interferes with daily activities/work.

  3. Individual concurrently has 44 or more of 88 symptoms. These symptoms must have been persistent or recurred during > 66 months of illness and did not predate fatigue.

8 Symptoms that must be concurrent with the first 3 criteria:
  • Post-exertion malaise lasting > 2424 hours.

  • Nonrestorative sleep.

  • Significant impairment of short-term memory/concentration.

  • Muscle pain.

  • Joint(s) pain without swelling/redness.

  • Headaches of new type/pattern/severity.

  • Tender lymph nodes neck/armpit.

  • Sore throat that is frequent/recurring.

Exercise & Chronic Fatigue Syndrome
  • Controlled and graded moderate exercise.

  • Home exercise program: Begin with low-level, intermittent physical activity throughout day = 3030 minutes/day.

  • Assess conditioning, breathing patterns, posture, biomechanics.

  • Stretching, strengthening, cardiovascular training.

  • Progress slowly as indicated by tolerance of plan of care.

  • Monitor vital signs.

Hypersensitivity Disorders

  • Exaggerated or inappropriate immune response.

  • Type I – typical allergies → anaphylactic hypersensitivity.

  • Type II – cytotoxic reaction; rejection of blood transfusions or autoimmune hemolytic anemia.

  • Type III – immune complex mediated.

  • Type IV – Delayed hypersensitivity response: contact dermatitis, poison ivy, latex.

Type I Hypersensitivity
  • Hypersensitivity response produced in response to an allergen.

  • Allergen: Special class of antigens that cause allergic response.

  • Examples: hay fever, allergic rhinitis, urticaria (hives), extrinsic asthma, and anaphylactic shock.

  • Typically genetic predisposition; Reaction occurs within 3030 min of exposure. Due to histamine release.

  • Typical Symptoms: redness, swelling, itching, rhinorrhea.

  • Most pronounced symptoms present in the upper respiratory tract, GI tract, and dermis.

Anaphylaxis
  • Widespread release of histamine à systemic response to an allergen that leads to systemic vasodilation, bronchospasm, increased mucus secretion, and edema à anaphylaxis.

  • LIFE THREATENING!!! Must have injection of epinephrine to restore blood pressure, strengthen heartbeat and restore airway clearance.

  • The most common trigger of anaphylaxis: bee stings (other triggers = penicillin, foods, animal dander, latex).

Type II Hypersensitivity
  • 2 types: self-recognized as non-self & cross-reaction.

  • Self-recognized as non-self:

    • An immune response that is disproportionate or exaggerated relative to the triggering factor.

    • Excessive & undesirable cytotoxic reactions to self-antigens.

    • Cellular membrane of normal tissues is disrupted & destroyed.

    • Usually limited to one type of tissues or organ.

    • Disorders: blood transfusion reactions, newborn hemolytic disease, some forms of anemia, certain platelet disorders, some types of tissue transplant rejection.

  • Type II Hypersensitivity: Cross-Reaction:

    • Cross-reaction between exogenous pathogens & endogenous body tissues.

    • Examples:

      • Immune system attacks hemolytic streptococci but also misinterprets mitral valve as foreign streptococci microorganism.

      • Attack of peripheral nervous system as nonself, as in Guillain-Barre syndrome.

    • Signs/symptoms:

      • General: malaise, weakness.

      • Dermal: hives, erythema.

      • Respiratory: sneezing, rhinorrhea, dyspnea.

      • Airway: hoarseness, stridor, tongue and pharyngeal edema, dyspnea, bronchospasm, asthma, chest tightness, wheezing.

      • Gastrointestinal: increased peristalsis, vomiting, dysphagia, nausea, abdominal cramps, diarrhea.

      • Cardiovascular: tachycardia, palpitations, hypotension, cardiac arrest.

      • CNS: anxiety, seizures.

Type III Hypersensitivity
  • “Immune Complex Disease”: antigen-antibody complexes are deposited in tissues rather than cleared from the body.

    • Produces inflammatory response and cause local tissue injury.

  • Common sites of Deposition: skin (urticaria), joints causing synovitis (RA), vasculature (vasculitis), kidneys (nephritis), pleura (pleuritis), and pericardium (pericarditis).

  • Underlying contributor to systemic lupus erythematous (LUPUS) Inflammatory disorder of connective tissue.

  • Signs/symptoms:

    • Headache.

    • Chest pain.

    • Back pain.

    • Tachycardia/hypotension.

    • Hematuria.

    • Nausea/vomiting.

Type IV Hypersensitivity
  • Delayed hypersensitivity response.

  • Examples: contact dermatitis (cosmetics, detergents, poison ivy, adhesives); transplant rejection.

  • PT related Possibilities: gels for ultrasound, lotions for soft tissue manipulation, latex gloves.

  • General signs/symptoms:

    • Itching, erythema, vesicular lesions on the skin.

    • Fever.

    • Arthralgias.

    • Lymphadenopathy.

    • Urticaria.

    • Anemia.

Autoimmune Conditions

  • Definition: category of conditions with inability of body to distinguish self from non-self, causing the immune response to attack the body’s own tissues – the mistaken reaction of the immune system toward body’s own tissues.

  • Disruption of immunoregulatory mechanism.

  • Underlying hypersensitivities may contribute to autoimmune diseases.

  • Hypersensitivity refers to an immune response that is disproportionate or exaggerated relative to the triggering factor.

Most Common Examples of Autoimmune Diseases
  • Rheumatoid arthritis

  • Psoriasis

  • Systemic lupus erythematosus

  • Graves’ disease

  • Inflammatory bowel disease

  • Hashimoto’s thyroiditis

  • Multiple sclerosis

  • Myasthenia gravis

  • Type I diabetes

  • Fibromyalgia

  • Guillain-Barre syndrome

  • Addison’s disease

Etiology of Autoimmune Diseases
  • Genetic Predisposition: multiple genes underlie multiple autoimmune diseases

  • Gender-Specific Hormones Imbalances

  • Exposure to Certain Viruses: carry structurally similar antigens to self- antigens

  • Environment: infection, climate, stress, occupation, cigarette smoking

  • Cross-Reactive Antibodies: antibody for one specific antigen has affinity toward a different one

  • Silicone Gel Breast Implants

Autoimmune Diseases

  • Over 5656 autoimmune diseases identified.

  • Spectrum of disorders: single organ involvement (pancreas in type 1 DM) to multi-system involvement (Multiple sclerosis).

Pathogenesis
  • Disruption of immunoregulatory mechanism → normal cell-mediated & humoral immune responses to turn self-destructive → tissue damage.

  • Genetic, hormonal, environmental influences.

Clinical Manifestations
  • Synovitis, pleuritis, myocarditis, endocarditis, pericarditis, vasculitis, myositis, skin rash, alterations of connective tissues, & nephritis.

  • Fatigue, malaise, myalgias, arthralgias.

Organ Specific Autoimmune Disorders

  • Addison’s Disease: adrenal cortex insufficiency – too little hormones released widespread metabolic disturbances (hypoglycemia, exhaustion, nausea/vomiting, anorexia, hypotensive).

  • Graves’ disease:

    • Hyperthyroid condition.

    • Autoantibodies stimulate the thyroid → hypermetabolic state.

    • Symptoms: ↑ sympathetic nervous system, tachycardia, heat intolerance, lipid depletion, ↑ appetite but with weight loss, nutritionally deficient state, and exophthalmos.

Systemic Autoimmune Diseases

  • Multiple Sclerosis:

    • Chronic neurodegenerative disorder of the central nervous system (CNS).

    • Autoimmune cells damage myelin cells → inability to transmit action potentials.

    • Sclerotic plaques develop throughout CNS.

  • Myasthenia Gravis:

    • Fluctuating weakness & fatigability of skeletal muscles.

    • Receptors at the neuromuscular junction normally receive acetylcholine.

      • An action potential occurs that leads to muscle contraction.

    • Antibodies block/destroy acetylcholine receptors at the neuromuscular junction.

    • Muscle weakness results.

    • Most common muscles affected: eyes, mouth, throat, face, swallowing.

  • Systemic Lupus Erythematosus (Lupus):

    • Definition: Autoimmune, chronic, systemic inflammatory rheumatic connective tissue disease characterized by multiple autoantibodies.

    • Cause: Exact unknown. Interrelated immunologic, environmental, hormonal, & genetic factors

Clinical Manifestations of Lupus
  • Musculoskeletal: arthralgias & arthritis.

  • Cutaneous & membranous lesions:

    • Skin rash in areas exposed to sunlight (butterfly rash).

    • Raised, red, scaling plaques.

    • Vasculitis.

    • Hair loss (temporary or permanent).

    • Ulcer in the mouth, vagina, and nasal septum.

  • Cardiopulmonary: pleuritis, pericarditis, dyspnea, tachycardia, myocarditis, pneumonitis (acute/chronic).

  • CNS: headache, depression, irritability, emotional instability, psychosis, seizures, CVA, cranial neuropathy, peripheral neuropathy, organic brain syndrome, cognitive dysfunction.

  • Renal: 50% have renal disease.

Injury, Inflammation, Healing and Repair

Learning Objectives

  • Describe the mechanisms of cell/tissue injury.

  • Compare the different means of cellular adaptation.

  • Explain the cellular responses associated with inflammation.

  • Describe the process of tissue healing.

  • Define factors that affect tissue healing.

  • Compare & contrast the phases of healing.

Cell Injury

  • Reversible or irreversible.

  • Factors affecting return to homeostasis:

    • Mechanism of injury.

    • Length of time injured without intervention.

    • Severity of injury.

Mechanism of Cell Injury

  • Ischemia

  • Infectious Agents

  • Immune Reactions (Hypersensitivity, Autoimmune)

  • Genetic Factors

  • Nutritional Factors

  • Physical Factors

  • Mechanical Factors

  • Chemical Factors

Mechanisms of Cell Injury - Ischemia

  • Blood flow below the minimum necessary to maintain cell homeostasis and metabolic function.

    • blood flow

    • metabolism

  • Reduction in oxygen supply (partial: hypoxia, total: anoxia).

  • nutrients

  • waste removal

  • Arterial obstruction and narrowing by atherosclerosis and/or intravascular clot called thrombus.

Mechanisms of Cell Injury - Infectious Agents

  • Bacteria, viruses, mycoplasma, fungi

Mechanisms of Cell Injury - Immune Reactions

  • Hypersensitivities

    • Overactive immune reactions → mild allergy reaction or life-threatening anaphylactic reactions.

  • Autoimmune

    • Immune system attacks self.

Mechanisms of Cell Injury - Genetic Factors

  • Alters the structure or # of chromosomes that leads to multiple abnormalities (Down’s Syndrome/ Trisomy 21).

  • Single mutations of genes: changes in the amount or functions of proteins (Sickle Cell Disease).

  • Multiple gene mutations: interact with environmental factors and multifactorial disorders result. (Hypertension, Type II DM).

Mechanisms of Cell Injury - Nutritional Factors

  • Imbalances in essential nutrients → cell injury or death.

  • Abnormal levels of vitamins/minerals, protein malnutrition (kwashiorkor), reduced (anemia) or excessive (free radicals) iron.

Mechanisms of Cell Injury - Physical Factors

  • Trauma: blunt trauma (massive brain contusions, internal organs, blood loss …)

  • Physical agents: extremes of temperature (burn, frostbite), radiation, electricity

Mechanisms of Cell Injury - Physical Stress

  • Physical stress exceeds tolerance of the tissue.

  • Overstretch, compression, friction, anoxia

Mechanisms of Cell Injury - Chemical Injury

  • Toxic substances lead to chemical injury

  • Mercury poisoning, agents used in chemotherapy, drug overdose

Types of Cell Injury

  • Reversible injury: when stress is small and duration is short à cell is able to cover homeostasis after stress removal

  • Irreversible injury: when stress is of sufficient magnitude or duration à cell is unable to adapt

Adaptation

  • The ability to alter mechanisms and regain homeostasis in the altered environment by cells or tissues

  • Alterations with sub-lethal stress over a period of time

  • Cellular adaptation characteristics:

    • Change in cell size, #, or function

    • Increases ability to survive

Cellular Adaptations

  • Common cellular adaptations

    • Atrophy: Reduction in cell and organ size due to vascular insufficiency, reduction in hormone levels, malnutrition, immobilization, and pain

    • Hypertrophy: Increase in size (skeletal muscle, cardiac cell hypertrophy)

    • Hyperplasia: Increase in # of cells → increased tissue size (uterus during pregnancy, skin callus, prostate enlargement)

    • Metaplasia: Conversion of an adult cell; change in form or function (smoker respiratory epithelium)

    • Dysplasia: Pre-neoplastic alteration; ↑ in number with altered cell morphology, and loss of histological organization (chronically injured area)

Inflammation

  • Normal secondary response to cell injury followed by healing & repair

  • Viral role in host defense mechanism against pathogens protecting host from infection/injury

  • Purpose: mobilize & transport the body’s defenses essential for healing to occur

    • Removal of injurious agent

    • Removal of cellular debris (dead cells)

    • Initiation of healing process

  • Intertwined with process of repair

    • Stimulates response for healing

  • Involves complex set of vascular, neurologic, & cellular responses

Acute Versus Chronic Inflammation

  • Acute Inflammation

    • Sudden onset with short duration; self limiting

    • Exudation of fluid and plasma protein (edema), migration of leukocytes (neutrophil)

    • Clinical manifestations: redness, swelling, increased temperature, pain, decreased function, increased Muscle Tone or Spasm

  • Chronic Inflammation

    • Long duration: weeks, months, or years

    • Causes:

      • Extensive necrosis

      • Underlying cause not addressed

      • Chronic overuse

      • Repeated trauma

      • Low-grade, persistent immune reactions

      • Autoimmune diseases

    • Hallmark in tissue: accumulation of macrophages, lymphocytes, & plasma cells

    • Much greater scar formation

Components of Inflammatory Response - Vascular alterations

  • Vasoconstriction of small arteries supplying injured area

    • Due to neural reflex

    • Short duration, ~ 10 minutes

  • Vasodilation

    • Long duration

    • blood flow to injured area (thus blood volume) → hydrostatic pressure

    • Transudation results: leakage of low-protein fluid from vasculature into the injured tissue (transudate)

    • Erythema, warmth, and edema

    • Exudation: extravascular fluid with high-protein

Components of Inflammatory Response - Leukocyte Accumulation

  • protein & fluid in vasculature (due to transudation) → engorgement of red blood cells in vessels → stasis

  • Stasis: slowing or cessation of blood flow

  • During stasis, leukocytes accumulate and adhere to endothelial cells of blood vessel walls at injury site (margination)

  • Actively pass through the vascular walls, migrating out of vessel into interstitial space without damage to vessel wall (diapedesis or oozing)

  • Diapedesis due to leukocytes attraction to chemotactic agents in interstitial space at site of injury (chemical stimulus)

  • Leukocyte locomotion process: chemotaxis

Summary of Inflammatory Response

  • Tissue Injury → Vaso Constriction → Vasodilation → Transudation → Stasis → Margination → Diapedesis → Chemotaxis → Phagocytosis

Chemical Mediators

  • Responsible for the vascular & leukocyte responses with acute inflammatory response

  • Released from inflammatory cells or plasma

    • Cell-derived – generated from inflammatory cells

    • Plasma-derived – generated by plasma protease (enzymes that act as catalyst in breakdown of proteins)

  • Multi-functional effects on blood vessels, inflammatory cells, other body cells

  • Vasodilation, vasoconstriction, vascular permeability change, activation of inflammatory cells, chemotaxis, cytotoxicity, affect fever & pain

Cell-Derived Mediators

  • Histamine

    • Endothelial Contraction - Increased membrane permeability

    • Vasodilator (Strong)

    • Potent bronchoconstrictor

    • Stored in mast cells, basophils, platelets

  • Serotonin

    • Vasoconstriction

    • Effects overridden by histamine

  • Cytokines

    • Wide range of inflammatory actions & systemic actions

    • Moderate activity/function of other cells

  • Prostaglandins

    • Lipids made at sites of tissue damage with hormone-like effects

    • Mediators of fever/pain responses associated with inflammation, constriction or dilation blood vessels

    • Clot formation

  • Chemokines

    • Specific types of cytokines

    • Chemoattractants for leukocytes, neutrophils, monocytes (direct the leukocytes to the pathogen)

Plasma-Derived Mediators

  • Blood Coagulation Cascade

    • Plasma proteins bandage injuries with clots (coagulation)

    • Disassemble (lyse)

    • Thrombin → Fibrinogen to fibrin

  • Fibrinolytic System

    • Activated by fibrinolysin

    • Dissolves clots

  • Bradykinin

    • Inflammatory Mediator

    • Peptide that causes vessel dilation and pain

  • Complement System

    • Plasma proteins dormant in blood, interstitial fluid, & mucosal surfaces

    • Activated by foreign protein & antigen-antibody complex

    • Vasodilation, leukocytes migration, opsonization

Tissue Healing

  • Begins soon after tissue injury/death

  • Tissue healing occurs either by regeneration (regrowth of original tissue) or by repair (formation of a connective tissue scar)

  • Complex and influenced by many components

  • Components

    • Fibronectin

    • Proteoglycans

    • Elastin

    • Collagen

Fibronectin

  • One of the first proteins to provide structural support that stabilizes the healing tissue - most common type of cell in connective tissue

  • Most important functions:

    • Formation of scaffold

    • Provision of tensile strength

    • “glues” other substances/cells together

  • Binds to fibrin: protein that makes up blood clots present in injured tissue

  • Attracts fibroblasts & macrophages by chemotaxis

  • Stimulated fibroblasts secrete more fibronectin

  • Binds to proteoglycans and collagens à stabilizes healing tissues

Proteoglycans & Elastin

  • Proteoglycans

    • Proteins secreted by fibroblasts early during tissue repair reaction

    • Bind to fibronectin & collagen: helps stabilize the healing tissue

    • Aid in hydration of tissue

Collagen

  • Most important protein to provide structural support and tensile strength most tissues and organs à Give stability to healing tissues

  • 28 different types: each type has special function

    • Type I: most common form, found in all body tissues, structurally very strong, predominant in tendons/bones & mature scars

    • Type II: predominant in cartilaginous tissue & bone physis (growth plate)

    • Type III: provides support for developing capillaries / makes tissues strong but supple, & elastic

    • Type IV: forms basement membrane to which other cells are anchored

Factors Affecting Tissue Healing

  • Growth Factors

    • Proteins that regulate several cellular reactions involved in healing: cell proliferation, differentiation, & migration

  • Nutrition: vitamin A, vitamin B, vitamin C, zinc, protein, and carbohydrates

  • Vascular supply

  • Presence of Infection

  • Immune reactions

  • Age

  • Comorbidities / medications

  • Smoking

Phases of Healing

  • Within 24 hours after dead tissue removal:

    • Hemostasis

    • Inflammation

    • Proliferation

    • Remodeling (maturation)

Hemostasis

  • Hemostasis is the first step, occurring immediately after acute injury as body tries to stop bleeding

  • Vessels constrict to restrict the blood flow

  • Platelets plug formation

  • Coagulation cascade: formation of blood clot – thrombus

Inflammation

  • Serves vital role in healing process

  • Protective and curative features

  • Begins once blood clot forms

  • Suffix = “-itis”

  • Functions

    • Inactivate injurious agent

    • Breakdown/remove dead cells

    • Initiate tissue healing

Proliferation

  • Reconstruction step with endothelial cell proliferation

  • Purpose: establish vascular network to transport O2O_2 & nutrients & support metabolism of healing tissue

  • Characterized by formation of granulation tissue, angiogenesis, wound contraction and process of epithelialization

  • Occurs 3-5 days following injury

  • Overlaps with inflammatory phase

  • Angiogenesis: formation of new blood vessels, involving the migration, growth, and differentiation of endothelial cells, which line the inside wall of blood vessels

Remodeling (Maturation)

  • OCCURS AFTER 2-3 WEEKS – 2 YEARS

  • SCAR TISSUE REDUCED & REMODELED: SMOOTHER, STRONGER, LESS DENSE, LESS RED TISSUE

  • COLLAGEN FIBERS REMODELED: PRODUCED, BROKEN DOWN, REARRANGED – GROWING STRONGER (BUILD TENSILE STRENGTH AND ELASTICITY OF THE SKIN)

  • 3 MAIN REMODELING STEPS: TISSUE CONTRACTION & CONTRACTURE, TISSUE REGENERATION, TISSUE REPAIR

Tissue Contraction & Contracture

  • Extracellular matrix draws together: healing tissue contracts

  • Tissue defect size is shrinking

  • Due to specialized fibroblasts: myofibroblasts that accumulate in wound margins

  • Tissue contraction approximates the margins of the healing tissue – wound closing

  • Contracture: excessive shrinkage – can limit mobility

Tissue Regeneration

  • Regeneration: The process of replacement of dead cells by new cells

  • Regrowth of original tissue

  • Restores normal tissue structure and function

  • Occurs due to healthy cell mitosis (cell division)

Tissue Repair

  • Most healing involves regeneration & tissue repair

  • Tissue repair: replacement by connective tissue scar

  • Dense, irregular laying down of collagen

  • Occurs with damage beneath epidermis

  • Scar tissue: 70-80% as strong as original tissue, less vascular

  • Scar function dependent upon stresses applied during healing

Physical Therapy & Scar Tissue

  • EXERCISE!

    • Scar remodeling occurs with stress (stretch/strengthening exercises)

    • Realignment of collage fibers to become stronger

  • Pressure

  • Myofascial release

  • Deep transverse friction tissue mobilization

  • Lubrication

  • Stretching

  • Kinesiology tape

  • Therapeutic Pulsed Ultrasound

Cardiac Disease

Learning Objectives

  • Define normal structure, circulation, and function of the heart.

  • Recognize signs, symptoms, and risk factors of cardiovascular disease.

  • Compare and contrast etiology, risk factors, pathogenesis, and clinical manifestations of diseases.

  • Describe rehabilitation implications for each of the diseases affecting heart muscle.

  • Discuss differences between sexes in cardiovascular disease.

  • Conclude when it is appropriate to refer patients with cardiac disease.

Layers of the Heart

  • Pericardium

  • Myocardium

    • Middle muscular layer of the heart.

    • Primary mover of the heart.

  • Epicardium

    • Thin layer of elastic connective tissues and fat.

    • Contains the coronary arteries.

  • Endocardium

    • Most inner layer of the heart.

    • Lining of the chambers of the heart.

Coronary Arteries

  • Originate from the aorta and supply blood to the heart.

    • Left main

    • Left anterior descending

    • Circumflex

    • Right main

    • Posterior descending

Anatomic Region of Heart & Coronary Artery Association
  • Inferior: Right coronary artery

  • Anteroseptal: Left anterior descending

  • Anteroapical: Left anterior descending (distal)

  • Anterolateral: Circumflex

  • Posterior: Right coronary artery

Circulation of Blood through the Heart

  • Lungs

  • Pulmonary Veins

    • Only veins with oxygenated blood

  • Left Atrium

    • Bicuspid/Mitral Valve

  • Left Ventricle

    • Aortic Semilunar Valve

  • Aorta

  • Body Tissues

  • Vena Cava

  • Right Atrium

    • Tricuspid AV Valve

  • Right Ventricle

    • Pulmonary Semilunar Valve

  • Pulmonary Arteries

Valves of the Heart

Atrioventricular
  • Tricuspid and Bicuspid (Mitral)

  • Located between the atria and corresponding ventricle.

Bicuspid (Mitral)

  • Located between the left atrium and ventricle.

Tricuspid

  • Located between the right atrium and ventricle.

  • Anterior, Septal, and Posterior cusps

Semilunar
  • Pulmonary and Aortic

  • Located between ventricles and corresponding artery.

Pulmonary

  • Located between the right ventricle and pulmonary trunk.

  • Left, right, anterior cusps

Aortic

  • Located between the left ventricle and ascending aorta.

  • Left, right, posterior cusps

Conduction System

  • Goal is sequential atrioventricular contraction

    • SA Node

    • Internodal Pathways

    • Atria Contracts

    • AV node

    • Ventricles

    • Bundle of His

    • Purkinje Fibers

    • Ventricles contract

Electrocardiogram (ECG)

  • P wave

    • Atrial contraction

  • PR Interval

    • Seconds from the beginning of the P wave to the QRS segment

  • PR segment

    • Conduction through atria and delay of AV node

  • QRS Complex

    • Ventricular contraction

  • T Wave

    • Ventricular recovery/relax

  • QT Interval

    • Time of ventricular contraction and relaxation

Key Terms and Definitions

  • Blood Pressure

    • Cardiac Output×Total Peripheral ResistanceCardiac\ Output \times Total\ Peripheral\ Resistance

    • TPRTPR = diameter of vessels and viscosity of blood

  • Systolic Pressure

    • Highest arterial pressure of cardiac cycle

    • Immediately after contraction of left ventricle

  • Diastolic Pressure

    • Lowest arterial pressure of cardiac cycle

    • Occurs between heart contractions

  • Stroke Volume

    • Volume ejected after each heart contraction

    • Influenced by preload, afterload, and contractility (inotropy)

  • Cardiac Output

    • Volume of blood ejected each minute

    • Stroke volume×HRStroke\ volume \times HR

    • 5-6 L/min at rest

  • Ejection Fraction

    • Amount of blood left in ventricle per contraction

    • Normal: 50-70%

Cardiovascular Disease Prevalence

  • Risk Factors

    • Hypertension

    • High serum cholesterol levels

    • Smoking

    • Sedentary lifestyle

    • Poor diet patterns

    • Overweight/obesity

  • 1 in 4 deaths in the U.S. due to cardiovascular disease

  • Leading cause of death in the U.S.

  • Coronary heart disease – most common type of heart disease

  • ~735,000 individuals in the United States have myocardial infarctions each year

Ischemic Heart Disease

  • Also known as Coronary Artery Disease (CAD) or Coronary Heart Disease (CHD)

    • Pathology

      • Narrowed/blocked arteries in the area of heart supplied becomes ischemic/injured

      • Myocardial infarction may result

      • Narrowing caused by Arteriosclerosis

        • Thickening and loss of elasticity of arterial walls

        • Atherosclerosis

          • Most common type

          • Accumulation of fatty deposits in the inner layer of arteries

  • Coronary Vascular vs. Coronary Artery vs. Cerebrovascular Coronary Artery Disease

Pathogenesis
  • Arterial wall damage by harmful blood substances and/or hypertension

  • Injury leads to infiltration of macromolecules such as cholesterol into smooth muscle cells

  • Platelets attracted

    • Thrombus formation

  • Thrombus can rupture, narrow, or block artery

Coronary Artery Disease Risk Factors

Non-Modifiable
  • Family history

  • Age (40+)

  • Sex

  • Ethnicity

  • Infection

    • Chlamydia Pneumonia

    • Helicobacter pylori

    • ½ US have antibodies for above

Modifiable
  • Smoking

  • High Cholesterol

  • Obesity

  • Hypertension

  • Physical Activity

  • Glucose metabolism

  • Hormonal status

  • Psychologic factors

  • Alcohol Abuse

Coronary Artery Disease Prevention

  • Atherosclerosis begins in adolescence and young adulthood

    • Address modifiable risk factors early

  • Moderate-intensity exercise at least 30 minutes 5-7 days/week

    • Decreased risk for:

      • Coronary events

      • Ischemic stroke

      • Metabolic syndrome

      • Insulin resistance

      • Diabetes

    • Improves heart rate recovery

    • Lowers cholesterol levels

Coronary Artery Disease Diagnosis

  • Cholesterol checks

    • Begin at 20 and recheck every 5 years

  • Coronary angiography

    • X-ray with dye of arteries

  • Echocardiography

    • Ultrasound imaging

  • Stress echocardiography

  • Exercise treadmill testing

    • HRrecovery=change from peak HR and 2 minutes laterHR recovery = change\ from\ peak\ HR\ and\ 2\ minutes\ later

      • 25 – 30 bpm = good, 50-60 bpm = excellent

      • Abnormal recovery = 4x as more likely to die from CAD

    • Decline of systolic pressure after graded exercise: correlates with CAD

Coronary Artery Disease Surgical Interventions

Coronary Stents
  • Drug-coated metal stents with plastic coating

  • Hold and release drugs that inhibit growth of endothelial cells

Coronary Artery Bypass Graft (CABG)
  • Portion of vein or artery grafted onto coronary artery

  • Bypasses blockage

Percutaneous Transluminal Coronary Angioplasty
  • Opens occluded coronary artery without opening chest

  • Involves double lumen balloon catheter

Implications for Rehabilitation

  • Cardiac Rehab Phase 1-3

    • Inpatient, outpatient, maintenance

    • Discharge instructions

    • Sternal Precautions

    • Indications for Exercise

Sternal Precautions
  • No pulling up in bed

    • Must roll side to side

  • No pushing, pulling, or lifting > 5 to 10 pounds for 6 weeks.

    • Vacuuming, lifting children bets, moving furniture, opening doors etc.

  • Move in the tube sternal precautions

    • No driving

    • Avoid horizontal abduction and extreme external rotation

  • Cough with heart pillow for splinting

  • Avoid using armrests to push up from chair

Angina Clinical Manifestations

  • Pain or discomfort in chest

    • Substernal

    • Occasionally refers to the left scapular area

    • Patients will report

      • Squeezing

      • Burning

      • Pressing

      • Heartburn

      • Indigestion

      • Choking

    • Varies in intensity

    • Can last 1 to 15 minutes

    • Usually relieved by rest or nitroglycerine

Angina Pathogenesis

  • Workload exceeds oxygen demand for various reasons

  • Symptom of ischemia secondary to imbalance between cardiac workload

  • 90% secondary to CAD

  • Disruption of plaques can lead to occlusive thrombus

    • Unstable angina or Myocardial Infarction

Types of Angina

Stable or Chronic
  • Demand ischemia

  • Involves coronary arteries

  • Predictable threshold of activity or stress

  • Hot and cold weather may trigger

  • 5 minutes or less is normal

  • Use rest or nitroglycerine

Unstable
  • Unpredictable

  • Changes in intensity, frequency, or threshold

  • Lasts longer than 15 minutes

  • Symptom or worsening cardiac ischemia

Variant (Prinzmetal’s)
  • Caused by coronary artery spasm

  • No CAD

  • Triggers

    • Stress, extreme weather, vasoconstriction meds, smoking/cocaine

  • Nitroglycerine and calcium antagonists

Microvascular
  • Involves coronary microvasculature

  • Endothelial dysfunction = chest pain

  • Most often postmenopausal

  • Most severe and lasts the longest

  • Often first noticed with ADL’s and emotional stress

Medical Management

  • Diagnosis

    • History supported by relief with sublingual nitroglycerin

      • Long-acting nitrates allow increased exertion

  • Treatment

    • Avoid provoking situations

    • Keep nitroglycerin for acute attacks

      • Decreases cardiac workload by decreased cardiac oxygen demand

      • Decreases preload and afterload

    • Medication to decrease heart rate and force of contraction

      • Decreased myocardial demand

    • Anticoagulants for unstable angina

    • Revascularization procedures

      • PTCA and CABG

Rehabilitation Implications

  • Unstable angina requires immediate medical referral

  • If known, need to have nitroglycerin on hand

    • Administer and sit down supported or in supine until symptoms resolve

    • Usually very quick

  • Watch for orthostatic hypotension

    • Common side effect of medications

  • Monitor vitals

    • Exercise below threshold

    • May be blunted heart rate responses

  • Education

Myocardial Infarction

Pathogenesis
  • Heart attack: development of ischemia with resultant necrosis of myocardial tissue

  • Heart deprived of oxygen

  • Leading cause of death among adults in the U.S.

  • Same etiology and risk factors as CAD

  • Angina due to CAD is predictive of Myocardial Infarction

  • 80—90% is secondary to coronary thrombus due to the site of preexisting atherosclerotic stenosis

    • Other causes are cocaine use, vasculitis, aortic stenosis, coronary artery dissection

  • Vessel becomes partially or completely blocked due to plaque

Clinical Manifestations
  • Sudden sensation of pressure with crushing chest pain

  • Often radiates to arm, throat, neck, and back

  • Pain is constant

    • 30-60 minutes

    • Up to hours

  • Pallor, Shortness of breath, diaphoresis

  • Women

    • Sudden nocturnal shortness of breath

    • Chronic, unexplained fatigue

    • Unexplained anxiety

    • Indigestion

  • Silent Myocardial Infarction

    • Associated with no pain

    • More common in older adults, all smokers, diabetes mellitus, and women

    • Vomiting, fever in the first 24 hours and persist for a week

Postinfarction Complications
  • Arrhythmias

    • Most common (90%)

  • Congestive Heart Failure

  • Pericarditis

  • Myocardial rupture

    • Fatal and most often left ventricle

  • Thromboembolism

  • Recurrent Infarction

  • Sudden death

Medical Management

  • Diagnosis

    • Clinical history, ECG interpretation, measurement of cardiac enzyme levels

      • Troponin most common

  • Treatment

    • If during treatment – rapid response/code blue or call 911 if outpatient

      • Chew/swallow aspirin

      • Nitroglycerin if prescribed

      • Unlock door

      • Lied down

    • Early intervention is optimal

    • Reestablish blood flow

      • Acute: thrombolytics

      • Post-acute: Same as CAD (stints, bypass, angioplasty)

Rehabilitation Implications

  • Activity recommended with graded progressions

  • Cardiac rehab can lead to coronary artery collateral growth

  • Specific dosages of aerobic, resistive, and flexibility exercises

  • Sexual activity

    • Follow general recommendations for AHA

    • Orgasm: Physiologically equivalent to brisk walk/climbing a flight to stairs

    • 5 METS

  • Early mobilization

    • Gentle and prevention complications

    • Usually within 24 hours

  • Holding breath and Valsalva contraindicated

  • Monitor vital signs!

  • Special care

    • Patients on thrombolytics

  • Education on precautions/contraindications

  • Referral for mental health and wellness

Heart Failure

  • Heart is unable to pump sufficient amount of blood to supply body’s needs

    • Due to disorders of:

      • Pericardium

      • Myocardium

      • Epicardium

      • Heart valves

      • Large coronary vessels

      • Metabolic abnormalities

    • May occur on both sides or predominantly one

      • Usually due to left ventricular dysfunction

    • Most common reason for hospitalization in ages 65+

Heart Failure Classifications

Left Ventricular Failure
  • Congestive heart failure

  • Leads to pulmonary congestion

Acute Right Ventricular Failure
  • NOT due to other issues

  • Leads to superior and inferior peripheral system congestion

Cor Pulmonale
  • Heart disease due to underlying pulmonary condition

  • Leads to right heart failure

Pathogenesis – Left Heart Failure

First Compensatory Stage

  • To maintain normal cardiac output – chambers enlarge to hold more blood

  • Ventricular dilation

  • Limited dilation before the threshold resulting in decreased contractility

  • Right ventricle continues as normal

  • With reduced left ventricular function, a back begins to occur leading to pulmonary congestion/edema

  • Dyspnea is for all people to some degree.

Second Compensatory Stage

  • Sympathetic nervous system responds

  • Stimulation of heart muscle to increase rate

  • Leads to ventricular hypertrophy

  • More oxygen is required to maintain increased heart rate

  • Angina pectoris begins to occur due to ischemia with hypertrophic demands

Third Compensatory Stage

  • Activation of the renin-angtiotensin- aldosterone system

  • Kidneys begin to retain water and sodium due to decreased blood

  • Further tissue edema

  • Increased load on compromised heart

  • When this stage finally fails, the patient reaches decompensated heart failure

Right Sided Heart Failure
  • Often but not always due to left-sided heart failure

  • Or can be right ventricle weakness and unable to empty

  • Blood will back up into systemic circulation via superior and inferior vena cava

  • Peripheral edema in legs, liver, abdominal organs

    • Ascites

  • Very high venous pressure causes distention of vessels

    • Jugular vein distention

Congestive Heart Failure Medical Management

  • Diagnosis

    • Clinical diagnosis

    • Symptom severity

    • Echocardiogram: primary diagnostic tool.

  • Treat underlying cause

    • Diet, exercise, lifestyle

  • Pharmacologic

    • Reduce heart workload

    • Increase cardiac muscle strength and contraction

    • Diuretics

  • Surgery

    • CABG

    • Cardiac Transplant

    • Pacemaker

Physical Therapy Implications

  • Monitor vital signs

  • Peripheral edema

    • DO NOT COMPRESS

  • Assess jugular vein distention

  • Utilize the Borg Scale

  • Positioning

    • Dependent position

    • Head of bed

  • Slow progression

  • Energy Conservation

  • Patient education

  • Psychosocial

Heart Valve Diseases

Valve Dysfunctions

Functional

  • Congenital deformities

  • Rheumatic fever

  • Trauma

  • Ischemia

  • Prolapse

    • Enlarged valve leaflets bulge backwards

    • Mitral or Tricuspid

Anatomic

  • Insufficiency

    • Regurgitation when the valve does not close properly

    • Blood flows back into the chamber

    • Dilation Occurs

  • Stenosis

    • Valve does not open fully

    • Obstruction leads to chamber hypertrophy

Mitral Valve Stenosis

  • Mild

    • Asymptomatic with left atrial pressure and cardiac output remain normal

  • Moderate

    • Dyspnea and fatigue appear and left atrial pressure rises

      • Decreased cardiac output

  • Severe

    • High left atrial pressure

      • Pulmonary congestion at rest

    • Dyspnea and fatigue, right ventricular failure

  • Diagnosis

    • Echocardiogram

  • Intervention

    • Pharmacologic: anticoagulants, antiarrhythmic agents

    • Surgery: valve replacement, balloon valvotomy

Mitral Valve Regurgitation (Insufficiency)

  • Associated with female, lower BMI, older age

  • May be asymptomatic until severe left ventricular dysfunction occurs

    • Exertional dyspnea

    • Exercise-induced fatigue

  • Diagnosis

    • Clinical with auscultation

    • Echocardiogram

  • Treatment

    • Mild – Diuretics, anticoagulants, anti-hypertensives

    • Moderate-Severe

      • Valve replacement/repair

    • Education

Mitral Valve Prolapse

  • 50% are asymptomatic

  • 40% are only mild to moderate symptoms

    • Fatigue

    • Palpitation

    • Dyspnea

  • Not at greater risk for heart failure

  • Treatment

    • Pharmacologic – antiarrhythmics

    • Exercise

    • Lifestyle education

    • Antibiotics before any invasive procedure

Arrhythmias

Ventricular
  • Fibrillation

    • Often results in cardiac arrest

  • Premature

    • Can be benign but should be documented

Atrial
  • Fibrillation

    • Most common and can lead to stroke/failure

    • Blood clot will originate and travel

Heart Block
  • Slowing or interruption of impulses from atria to ventricles

  • Different degrees and types

Treatment

  • Pharmacology

    • Many types, will learn more later

  • Cardioversion

    • Synchronized electrical shocks

  • Defibrillation

  • Ablations

    • Catheterization threads wire to where arrhythmia originates and the area is destroyed

  • Pacemaker

    • Single chamber – right ventricle

    • Dual chamber – right ventricle and atrium

    • Biventricular

      • Resynchronization therapy: used with heart failure

Pulmonary Disease Notes

Impact of Lung Disease

  • COPD is the 4th leading cause of death in the US.

  • Over 50% of Americans with lung disease are undiagnosed.

  • Lung disease directly impacts exercise and ADLs, requiring modifications to physical therapy recommendations.

  • Smoking statistics:

    • 1960: 55% / 30%

    • 2008: 22.8% / 18.5%

    • 2016: 18.6% / 14.3%

    • 2021: 13% / 10%

  • Patients with chronic respiratory disorders are at risk for acute exacerbations, ER visits, hospitalization, and co-morbidities.

  • Chronic lung disorders result in chronic modification of ADLs and therapeutic interventions.

Leading Causes of Death in US (2021)

  • 1. Heart disease

  • 2. Cancer

  • 3. Medical errors (under-documented)

  • 4. COPD (Chronic lower respiratory disease)

  • 5. Accidents

  • 6. Stroke

  • 7. Alzheimer’s disease

  • 8. Diabetes

  • 9. Influenza & pneumonia

  • Kidney disease

Pulmonary A&P Review

  • Upper airways: above larynx (vocal cords); includes nasopharynx, oropharynx, laryngopharynx.

  • Vocal cords division.

  • Lower airways: below larynx; includes conducting zone & respiratory zone.

Pulmonary A&P Review (Continued)

  • Conducting Zone: Trachea -> Bronchi -> Bronchiole -> Terminal Bronchiole (23-24 bifurcations).

  • Respiratory Zone: Respiratory bronchioles -> Alveolar Duct -> Alveolar Sac -> Alveoli.

  • Respiratory Zone: Actual interface of alveoli with capillary beds (AC membrane) for exchange of CO2 and O2 with RBCs.

  • O2/CO2 exchange (respiration).

  • Gases diffuse from high concentration to low concentration.

    orr</p></li></ul><p>InfrastructureofAlveolarCapillaryInterface</p><ul><li><p>AlveolarTypeIcell:composetheactualstructureofthecell.</p></li><li><p>AlveolarTypeIIcell:producesurfactanttopreventalveolarcollapse.</p></li><li><p>AlveolarTypeIIIcell:alveolarmacrophage(housekeeping).</p></li><li><p>SurfaceAreaofTypeIcells(300million)is</p></li></ul><p>Infrastructure of Alveolar-Capillary Interface</p><ul><li><p>Alveolar Type I cell: compose the actual structure of the cell.</p></li><li><p>Alveolar Type II cell: produce surfactant to prevent alveolar collapse.</p></li><li><p>Alveolar Type III cell: alveolar macrophage (housekeeping).</p></li><li><p>Surface Area of Type I cells (300 million) is70 m^2(tenniscourt).</p></li></ul><p>Ventilationvs.Respiration</p><ul><li><p>Respiration:(tennis court).</p></li></ul><p>Ventilation vs. Respiration</p><ul><li><p>Respiration:O2/CO2 exchange through A/C membrane in the Respiratory Zone.

  • Ventilation: mechanical movement of gas in and out of lungs as a function of thorax musculature, lung compliance, and airway resistance.

  • Control of ventilation: neuro-chemical through carotid bodies and CSF response through BBB.

  • Hypercapnic drive vs. hypoxic drive.

Ventilatory Muscles

  • Muscles of resting ventilation:

    • Inspiration: diaphragm.

    • Expiration: none (passive recoil of thorax).

  • Muscles of active ventilation (accessory muscles):

    • Inspiration: sternocleidomastoid, external intercostals, scalene, trapezius, pectoralis major/minor.

    • Expiration: internal intercostals, transverse abdominis, external/internal obliques, serratus, latissimus dorsi.

Pulmonary Function Test (PFTs)

  • Primary method for Dx/stage lung disease.

  • Total Lung Capacity:

    • The Volume of Air in the Lungs After a Maximum Inhalation

  • Tidal Volume:

    • The Volume of Air Inhaled or Exhaled During Normal Breathing

  • Vital Capacity:

    • The Maximum Amount of Air a Person Can Exhale After a Maximum Inhalation

  • Inspiratory Reserve Volume:

    • The Maximum Amount of Extra Air That Can Be Inhaled Above Tidal Volume

  • Expiratory Reserve Volume:

    • The Maximum Amount of Extra Air That Can Be Exhaled Beyond Tidal Volume

  • Residual Volume:

    • The Volume of Air Remaining in the Lungs After a Maximum Exhalation

Pulmonary Signs and Symptoms

  • Sign (objective finding perceived by examiner) vs Symptom (subjective indicator of disease or change as perceived by the patient).

  • Cough.

  • Dyspnea.

  • Abnormal sputum.

  • Chest pain/discomfort.

  • Hemoptysis.

  • Cyanosis.

  • Digital clubbing.

  • Altered breathing patterns.

Digital Clubbing

  • Fingers & toes.

Altered Breathing Patterns & Sounds

  • Hyperventilation (hyperpnea vs. tachypnea).

  • Hypoventilation (hypopnea vs, bradypnea).

  • Stridor (high-pitched inspiratory sound).

  • Wheeze (musical expiratory sound).

  • Crackles (known as rales, crackling inspiratory sound).

Aging and the Respiratory System

  • Normal physiologic changes.

  • Senile emphysema (shrinking “tennis court”).

  • Chest wall compliance decreases (ribs ossification, joints stiffening).

  • Elastic recoil of lungs decreases (loss of muscle fiber).

  • Overall decreased ventilatory capacity with reduced VC, increased RV, decreased exercise tolerance (increased DOE and SOB).

Classification of Lung Diseases

  • Physiology of Restrictive vs. Obstructive Lung Disease.

  • Both classified/diagnosed through patient Hx, chest assessment, CXR, ABGs, and PFTs.

  • Restrictive Pulmonary Disease: generally the “inability to take a deep breath

    ” due to restriction (stiffening) of lung tissue or the thorax or neurological disorder.

  • Obstructive Pulmonary Disease: generally the “inability to exhale each breath completely

    ” due to a reduced expiratory airflow from obstruction of the airways.

Obstructive Lung Disease

  • Acute or Chronic; Reversible or Non-reversible.

  • Termed COPD in US and COLD in Europe.

  • Prolonged expiratory time required by patient to empty lungs due to thoracic pressure dynamics.

  • Following heart disease, 2nd most debilitating disease of adults under 65 and 3rd leading cause of death (Pack-Years > 60).

  • Environmental irritants cause exacerbations & increase morbidity/mortality rates.

  • Diagnosis/management of COPD recognized world-wide using Global Initiative for Chronic Obstructive Lung Disease (GOLD) standards through NHLBI and WHO.

Acute Obstructive Lung Diseases

  • Acute bronchitis: inflammation of trachea and bronchi with a bacterial or viral etiology.

  • Asthma: potentially reversible obstructive

    airways disease caused by increased Raw due to hyperactivity in the presence of personal airway triggers; may potentially return to normal lung function.

  • Croup and epiglottis: acute obstruction of upper airways.

Chronic Obstructive Lung Diseases

  • Chronic bronchitis, emphysema, asthma.

  • Term COPD used when CB and emphysema present concurrently.

  • Also cystic fibrosis (CF), bronchiectasis, bronchiolitis.

Emphysema

  • Anatomic Definition: permanent destruction of alveoli, connective tissue, and capillary beds resulting in hyper-inflation (air trapping) with loss of elastic recoil of lung tissue.

  • Centrilobular: cigarette smoking (60 pack-yrs).

  • Panlobular: genetic (alpha1-antitrypsin deficiency)

  • Loss of elasticity and alveoli -> air trapping -> barrel chest (1:1) -> increased WOB/DOE -> weight loss/difficulty eating -> accessory muscle hypertrophy.

  • Progressive anatomic changes:

    • Loss of “tennis court” AC interface -> increased pulmonary vascular resistance -> cor pulmonale -> increased pedal edema, palpable liver, JVD’s in neck.

    • Increased SOB at rest -> increased sedentary lifestyle.

Emphysema PFTs Diagnosis & Staging

  • Increased lung volumes.

  • Reduced expiratory flow rates.

  • Decreased diffusion capacity due to loss of capillary beds.

  • Limitation of thoracic cage expansion and diaphragmatic excursion.

  • V/Q ratio near normal due to focused work on breathing. Pursed-lip breathing helps keep alveoli from collapsing. Described as “pink puffer.”

  • Tx: Disease is progressive with low flow O_2 primary support, possible corticosteroids during exacerbations, inhaled bronchodilators when indicated, when cor pulmonale presents < 6 months survival.

Chronic Bronchitis

  • Clinical definition: chronic productive

    cough for 3 months out of year for 2 consecutive years.

  • Chronic irritation of airways -> inflammation, edema, excessive mucous production, hyperplastic mucous glands, physical obstruction of large and small airways by mucous, normal mucous clearance impeded due to increased viscosity.

  • Initially NORMAL alveoli!

  • Cyanosis “Blue Bloater” characteristics with poor ventilation.

  • Hypercapnea and hypoxia increase pulmonary vascular pressure resulting in early cor pulmonale.

  • Polycythemia, digital clubbing, similar PFT changes as seen with emphysema except normal diffusion rates.

  • Treatment: O_2,mucolyticRx,bronchodilators,corticosteriods,lowcarbdiet,chestphysiotherapyorposturaldrainage/percussion.</p></li></ul><p>COPDImplicationsforPT</p><ul><li><p>Chestphysicaltherapy:posturaldrainage,breathingtechniques(pursedlipbreathing),segmentalresistance,breathingexercisestostrengthenventilatorymuscles(inspiratory/expiratorytrainers),physicaltrainingtocombatgeneraldeconditioning,posturetraining.</p></li><li><p>Instructinenergyconservation.</p></li><li><p>Monitor, mucolytic Rx, bronchodilators, corticosteriods, low-carb diet, chest physiotherapy or postural drainage/percussion.</p></li></ul><p>COPD Implications for PT</p><ul><li><p>Chest physical therapy: postural drainage, breathing techniques (pursed-lip breathing), segmental resistance, breathing exercises to strengthen ventilatory muscles (inspiratory/expiratory trainers), physical training to combat general deconditioning, posture training.</p></li><li><p>Instruct in energy conservation.</p></li><li><p>MonitorO_2saturationandHR.</p></li></ul><p>Asthma</p><ul><li><p>Characterizedbyairwayhyperreactivitytovariousexternal/internalstimuliwithrecurrentepisodesofintermittentreversibleairwayobstructionduetobronchospasmandmucousproduction.</p></li><li><p>Extrinsic(Allergic/TypeI):mostcommoninchildren,duetoIgEdocumentedAn/Abrxt.</p></li><li><p>Intrinsic(NonAllergic/TypeII):adultonset,triggeredbycoldair,exercise,emotions,drugs.</p></li><li><p>PrevalencedoubledinUSsince1980andincreasedby400saturation and HR.</p></li></ul><p>Asthma</p><ul><li><p>Characterized by airway hyperreactivity to various external/internal stimuli with recurrent episodes of intermittent reversible airway obstruction due to bronchospasm and mucous production.</p></li><li><p>Extrinsic (Allergic/Type I): most common in children, due to IgE documented An/Ab rxt.</p></li><li><p>Intrinsic (Non-Allergic/Type II): adult onset, triggered by cold air, exercise, emotions, drugs.</p></li><li><p>Prevalence doubled in US since 1980 and increased by 400% in children.</p></li></ul><p>Asthma Triggers</p><ul><li><p>Extrinsic stimuli:</p><ul><li><p>Pollens (tree, grass).</p></li><li><p>Animal dander.</p></li><li><p>Feathers.</p></li><li><p>Mold spores.</p></li><li><p>Household dust.</p></li><li><p>Foods (nuts, shellfish).</p></li></ul></li><li><p>Intrinsic stimuli:</p><ul><li><p>Inhaled irritants (smoke, pollution, sprays).</p></li><li><p>Weather (high humidity, cold, fog).</p></li><li><p>Respiratory infections (common cold, bronchitis).</p></li><li><p>Drugs (ASA, other NSAID- OTC).</p></li><li><p>Emotions (stress).</p></li><li><p>Exercise (super airway cooling).</p></li></ul></li></ul><p>Asthma Pathogenesis (know general story)</p><ul><li><p>Mechanism of reaction (Immediate response):</p><ul><li><p>Triggers may vary with each incident.</p></li><li><p>Activation of T-cells (TH2) begins leukotriene pathway “domino” reaction.</p></li><li><p>Activation of B-cells and eosinophils.</p></li><li><p>Production of IgE by B cells.</p></li><li><p>Binding of IgE with degranulation of mast cells lining TB tree.</p></li><li><p>Release of histamines, SRSA, cytokines, eosinophils.</p></li><li><p>Results in smooth muscle contraction along TB tree.</p></li></ul></li></ul><ul><li><p>Mechanism of reaction (Delayed response):</p><ul><li><p>4-8 hours after initial acute bronchospasm event, the delayed response brings additional bronchospasm due to release of mast cell components into bloodstream.</p></li><li><p>Results in airway edema (swelling) with copious mucous production.</p></li></ul></li></ul><p>Asthma Clinical Manifestations</p><ul><li><p>Recurrent paroxysmal attacks of cough, chest tightness, and difficult breathing, often accompanied by wheezing.</p></li><li><p>Thick, tenacious sputum, which may be difficult to expectorate.</p></li><li><p>Patient may be symptom-free between attacks or may be in chronic state of mild asthma.</p></li><li><p>Hyperinflated lungs with prolonged expiration and diminished breath sounds.</p></li></ul><p>Asthma Treatment</p><ul><li><p>Bronchodilators (smooth muscle relaxants) (eg, albuterol, theophylline, ipratropium).</p></li><li><p>Anti-inflammatory drugs (eg, corticosteroids, cromolyn sodium).</p></li><li><p>Leukotriene synthesis or receptor blockers (eg, zileuton, zafirlukast, montelukast).</p></li><li><p>Recurrent events = airway remodeling.</p></li><li><p>Prevention of triggers.</p></li></ul><p>Cystic Fibrosis</p><ul><li><p>Etiology: Inherited disease transmitted as autosomal recessive trait.</p></li><li><p>1 genetic defect among Caucasians—simple Mendelian cross (25/50/25 per pg).</p></li><li><p>1 in 38 individuals carried one of the 98 CFTR mutations.</p></li></ul><p>CF (Continued)</p><ul><li><p>Genetic defect on Chromosome #7 with blockage of Cl- ion transmission across cell membrane in mucus-secreting cells (inability to reabsorb Cl-).</p></li><li><p>CFTR (CF transmembrane regulator) protein, which forms chloride channel in some cells, does not function properly.</p></li></ul><p>CF Pathogenesis</p><ul><li><p>CF results in dysfunction of exocrine system.</p><ul><li><p>Mucus-secreting glands→symptoms in lungs, pancreas, bile ducts, intestine.</p></li><li><p>Exocrine glands (most common type of sweat gland).</p></li><li><p>Pancreatic exocrine glands (mucus blocks ducts→fibrosis→↓ secretion of digestive enzymes, possible including ↓ insulin secretion).</p></li></ul></li><li><p>Normal lungs at birth.</p></li><li><p>Eventual Pulmonary obstruction occurs due to large quantity of tenacious mucus secreted in bronchi, atelectasis from mucus plugs, respiratory infections, developing COPD changes.</p></li></ul><p>CF Diagnosis</p><ul><li><p>↑ NaCl in sweat due to abnormal reabsorption of Cl- in sweat gland duct; Sweat Test used to diagnose.</p></li><li><p>80% of affected children have abnormalities in pancreatic secretion that can→malabsorption of lipids and possibly other nutrients and steatorrhea.</p></li><li><p>Bile duct obstruction→liver damage→portal hypertension and splenomegaly.</p></li><li><p>Intestinal obstruction in newborn due to thick mucus (Meconium ileus).</p></li><li><p>The earlier diagnosed (symptomatically) the more severe the course; DNA testing to determine degree of Chromosome #7 aberration.</p></li></ul><p>CF Prognosis</p><ul><li><p>CF seen in newborns, children, young adults; prognosis is variable, with median lifespan of about 34 yrs.</p></li><li><p>Usually fatal due to respiratory complications.</p></li><li><p>There is some success using gene therapy to open Cl- channels in airway epithelial cells.</p></li><li><p>PFTs used for staging.</p></li></ul><p>CF Treatment</p><ul><li><p>Pharmacologic tx:</p><ul><li><p>Bronchodilators, mucolytic expectorants to maintain airway patency.</p></li><li><p>Systemic glucocorticoids to limit airway inflammation.</p></li><li><p>Antibiotics to tx respiratory infections.</p></li></ul></li><li><p>Pulmonary hygiene:</p><ul><li><p>Postural drainage/airway clearance (Percussion vest).</p></li><li><p>Breathing exercises (PEP, IPPV).</p></li></ul></li><li><p>Lung transplantation.</p></li></ul><p>CF Implications for PT</p><ul><li><p>Monitor for s/s of pulmonary exacerbation in CF.</p></li><li><p>Teach chest PT and breathing exercises.</p></li><li><p>Encourage proper nutrition (low fat diet).</p></li><li><p>Design and teach exercise programs.</p></li><li><p>Manage osteoporosis in late-stage CF.</p></li><li><p>We want the coughing</p></li></ul><p>Restrictive Lung Disease</p><ul><li><p>Any lung condition that prevents the patient from breathing deeply.</p></li><li><p>Diagnosed via PFTs showing characteristic ↓ in TLC and VC with normal flowrates (insp/expir).</p></li><li><p>Also called restrictive lung dysfunction, restrictive alterations in pulmonary function.</p></li></ul><p>RLD Etiology</p><ul><li><p>Respiratory center depression</p></li><li><p>Neuromuscular problem</p></li><li><p>Thoracic deformity</p></li><li><p>Trauma</p></li><li><p>Obesity</p></li><li><p>Pregnancy</p></li><li><p>Pleural disorders</p></li><li><p>Pleural effusion</p></li><li><p>Pneumothorax</p></li><li><p>Pulmonary fibrosis</p></li><li><p>TB</p></li><li><p>Atelectasis</p></li><li><p>ARDS</p></li><li><p>Pulmonary edema</p></li><li><p>Aspiration pneumonia</p></li></ul><p>Atelectasis</p><ul><li><p>“airless state of the lung” involving collapse of alveoli or incomplete expansion at birth.</p></li><li><p>Causes of collapse:</p><ul><li><p>Compression (eg, tumor, hematoma).</p></li><li><p>Airway obstruction (eg, by secretions that collect after surgery if patient does not cough or breathe deeply).</p></li><li><p>Lack of surfactant (eg, hyaline membrane disease, ARDS).</p></li></ul></li></ul><p>Pulmonary Edema</p><ul><li><p>Excess fluid accumulation in interstitial tissues, alveoli or both.</p></li><li><p>Most common cause left ventricular failure (CHF), but may include many non-cardiac issues like drug overdose, high altitude, diving/submerging, sepsis, medications, smoke inhalation, noxic gas, blood transfusion rxt, shock, IV fluid overload, or DIC.</p></li><li><p>Fluid outside the alveoli compress it, fluid inside alveoli preventO2/CO2exchange,hypoxiaresultswithn~WOB.</p></li><li><p>Tx:diuretics,exchange, hypoxia results with ñWOB.</p></li><li><p>Tx: diuretics,O_2$$, Beta 1 & 2 Rx.

  • Prognosis: potentially reversible, but may lead to respiratory failure.

RLD – Tuberculosis (TB)

  • Was once leading cause of death in U.S.

  • Still one of top causes of death in world.

  • 15,000 new cases annually in US (250-300 in Alabama).

  • Caused by infection with Mycobacterium tuberculosis.

  • Characterized by granulomas, caseous necrosis, and cavity formation.

  • Transmission: airborne.

  • Primary versus secondary infection.

  • Multi-drug resistant TB.

TB (Continued)

  • At-risk groups:

    • Immunocompromised

    • Crowded living conditions

TB Transmission

  • Primary TB: inhalation of Mycobacterium tuberculosis from infected (Secondary TB).

  • + TB skin test denotes exposure.

  • Body forms Ghon foci calcification around MTB.

  • Time bomb? May choose to tx with INH x 1 year.

  • Secondary (post-Primary or Reactivation):

    • Not due to exogenous infection, rather reinfection of endogenous TB.

  • TB treatable but difficult to recognize.

  • Symptoms subtle, easy to ignore, nonspecific (eg, cough, phlegm production, weight loss, dyspnea, night sweats, fever, malaise, anorexia).

  • Diagnosis: H&P, TB skin test, chest radiograph, microscopic examination and culture of sputum.

  • During Secondary Infection, person is extremely contagious and should be placed in respiratory isolation until after 10-14 days of anti-TB Rx.

  • Pharmacologic tx:

    • Agents that inhibit bacterial protein synthesis on DNR/RNA (INH, rifampin, pyrazinamide).

    • Agents that inhibit bacterial DNA/RNA synthesis and function (eg, ethambutol, rifampin).

  • Recommended duration: 6-9 months.

  • Rx side effects may include liver damage, hepatitis, temporary blindness (optic nerve toxicity), temporary loss of hearing.

  • RESPIRATORY ISOLATION (mask only).

RLD: Aspiration Pneumonia

  • Aspiration: inhalation of foreign material, usually food, drink, or vomit; common sequelae of stroke, seizure.

  • Aspiration pneumonia: inflammation of lungs that results from aspiration.

  • Introduction of aerobic and anaerobic bacteria into lungs, difficult to treat/resolve.

RLD: Acute Respiratory Distress Syndrome (ARDS)

  • Acute respiratory failure due to systemic or pulmonary insult (eg, sepsis, trauma, major surgery).

  • Also called adult respiratory distress syndrome, shock lung, hyaline membrane disease (adult or newborn), diffuse alveolar damage.

  • Often fatal (80% mortality rate for patients >35 yrs and 20% fatal for patients <35 yrs).

  • Pathogenesis: damage to alveolar epithelium and capillary endothelium→ pulmonary edema → “drowning” at cellular level.

  • Onset: within 12-48 hrs, w/ initial presentation of ↑ RR (shallow, rapid).

  • Characterized by dropping SaO2 while increasing FIO2

  • Neonates benefit from surfactant replacement Rx

  • Adults do not benefit from surfactant Rx