chapter four

4.1 DNA and RNA—The Nucleic Acids

  • Expected Learning Outcomes:

    • Describe the structure of DNA and relate this to its function.

    • Describe the types of RNA, their structural and functional differences, and how they compare with DNA.

4.1a DNA Structure and Function 1

  • Deoxyribonucleic acid (DNA):

    • A long, thread-like molecule with a uniform diameter but variable length.

    • Most human cells have 46 DNA molecules (chromosomes).

    • The average human DNA molecule is about 2 inches long.

DNA Structure and Function 2

  • DNA and Nucleic Acids:

    • DNA and other nucleic acids are polymers made of nucleotides.

    • Each nucleotide consists of three components:

    • A sugar (deoxyribose)

    • A phosphate group

    • A nitrogenous base

    • DNA Bases: Adenine (A), Thymine (T), Cytosine (C), Guanine (G)

    • Purines: Adenine (A) and Guanine (G) have a double-ring structure.

    • Pyrimidines: Cytosine (C), Thymine (T), and Uracil (U) have a single-ring structure.

The Five Nitrogenous Bases found in DNA and RNA

  • Figure 4.1b:

    • Access text alternatives for the accompanying images.

DNA Structure and Function 3

  • Double Helix Structure:

    • The double helix shape of DNA resembles a spiral staircase.

    • Each sidepiece is a backbone of alternating phosphate groups and deoxyribose.

    • Step-like connections between the backbones are made by base pairs unified by hydrogen bonds.

    • Base Pairing: Purines pair with pyrimidines:

    • A pairs with T using 2 hydrogen bonds.

    • G pairs with C using 3 hydrogen bonds.

    • Law of Complementary Base Pairing: The sequence of one strand dictates the sequence of the other.

DNA Structure and Function 4

  • Function of DNA:

    • The primary function of DNA is to carry genetic instructions (genes) for protein synthesis.

    • Gene Definition: A segment of DNA coding for a specific protein.

    • Humans possess about 20,000 genes, accounting for approximately 2% of total DNA.

    • The remaining 98% is noncoding DNA which plays roles in chromosome structure and regulation of gene activity.

Chromatin and Chromosomes 1

  • DNA Organization:

    • DNA organizes itself with proteins into chromatin, which is a fine filamentous material complexed with histones.

    • Exists as 46 chromosomes in most cells, resulting in a 6 feet long thread packed into the cell nucleus of about 5 μm in diameter.

    • In non-dividing cells, chromatin is slender enough to be undetectable under a light microscope.

    • Forms complex loops and coils, appearing 150 times thicker and 1,000 times shorter than naked DNA.

    • Each chromosome occupies its own region of the nucleus known as a chromosome territory, permeated with channels for regulatory chemicals to access genes.

Chromatin and Chromosomes 3

  • Chromosome Preparation for Division:

    • Prior to cell division, the cell duplicates all nuclear DNA.

    • Each chromosome then consists of two identical DNA strands, referred to as sister chromatids, joined at the constricted centromere.

4.1c RNA Structure and Function

  • Ribonucleic Acids (RNAs):

    • RNAs exist in different forms, each serving various functions.

    • General RNA Structure:

    • Contains the sugar ribose.

    • Bases include A, U, G, C; with uracil (U) replacing thymine found in DNA.

    • Composed of a single nucleotide chain (except in short regions).

    • Smaller than DNA, with lengths varying from less than 100 to just over 10,000 bases per molecule.

    • Functions mainly in cytoplasm.

    • Three important types of RNA for protein synthesis:

      • Messenger RNA (mRNA)

      • Ribosomal RNA (rRNA)

      • Transfer RNA (tRNA)

4.2 Genes and Their Action 1

  • Expected Learning Outcomes:

    • Provide a working definition of a gene and discuss how recent discoveries in genetics have modified our concept of genes.

    • Explain the human genome and its implications for health sciences.

    • Define genetic code and elucidate how DNA codes for protein structure.

4.2 Genes and Their Action 2

  • Expected Learning Outcomes Continued:

    • Describe the process of assembling amino acids to form proteins.

    • Explain the fate of a protein after its amino acid sequence has been synthesized.

    • Discuss mechanisms by which genes can be activated (turned on) or inactivated (turned off).

    • Explain how DNA regulates nonprotein molecule synthesis indirectly.

What Is a Gene? 1

  • Previous Definition: A gene is defined as a segment of DNA coding for a specific protein. However, the body has millions of proteins but only about 20,000 genes.

  • Current Definition: A gene is an information-containing segment of DNA that codes for the production of RNA, which often plays a role in synthesizing one or more proteins.

  • The amino acid sequence of a protein is determined by the nucleotide sequence in DNA.

What Is a Gene? 2

  • Human Chromosomes:

    • Humans have 46 chromosomes arranged in two sets of 23, one from each parent.

    • Genome: All the DNA contained within one set of 23 chromosomes.

    • There are 3.1 billion nucleotide pairs in the human genome.

    • Individual genetic variation arises from single-nucleotide polymorphisms.

    • Genomics: The study of the entire genome; genes and noncoding DNA interact, affecting the structure and function of an organism.

    • Genomic Medicine: The application of genomic knowledge for predicting, diagnosing, and treating diseases (examples include cancer, Alzheimer's disease, schizophrenia, obesity, AIDS, tuberulosis).

4.2b The Genetic Code

  • Proteome Evolution: The human body can generate millions of unique proteins (the proteome) from just 20 amino acids encoded by genes composed of merely four nucleotides (A, T, C, G).

  • Genetic Code: A system that allows these four nucleotides to codify for the amino acid sequences of all proteins.

    • Base Triplet: A sequence of three DNA nucleotides representing one amino acid.

    • Codon: A three-base sequence in mRNA.

    • There are 64 possible codons representing 20 amino acids, with 61 coding for amino acids and 3 serving as stop codons.

    • Start Codon: The codon AUG which codes for methionine and initiates the amino acid sequence of a protein.

    • Stop Codons: UAG, UGA, and UAA are signals indicating "end of message," akin to a period at the end of a sentence.

4.2c Protein Synthesis 1

  • Cellular Identity: All body cells, except sex cells and some immune cells, contain identical genes; however, cells differ because they activate and utilize different genes.

  • Any specific cell uses about one-third to two-thirds of its genes, while the remainder remain inactive.

  • Upon activation of a gene, mRNA (messenger RNA) is synthesized as a code for a specific protein.

    • Central Dogma of Molecular Biology:

    • DNA → RNA → Protein

    • The process from DNA to mRNA occurs through transcription in the nucleus.

    • The conversion from mRNA to protein occurs through translation in the cytoplasm.

Transcription 1

  • Transcription: The process of copying genetic instructions from DNA to mRNA.

    • It employs the enzyme RNA polymerase, which binds to starting sequences in DNA and unwinds the helix.

    • RNA polymerase reads bases from one strand of DNA to build a complementary mRNA strand:

    • For DNA bases:

      • C → G

      • G → C

      • T → A

      • A → U

    • Terminator: A stop sequence found at the end of a gene.

    • Pre-mRNA is the immature RNA created during transcription and later processed to remove introns around splicing exons together.

    • Alternative Splicing: Variations in splicing exons allow for the production of various proteins from a single gene, illustrating that one gene can encode more than one protein.

Alternative Splicing of mRNA

  1. Transcription:

    • Gene (DNA) → Intron/(Pre-mRNA) → Exon

  2. Splicing:

    • mRNA can form multiple versions due to alternative splicing allowing different mRNA products from a single gene.

    • This leads to various proteins being synthesized (Protein 1, Protein 2, Protein 3).

Translation 1

  • Translation: The process in which the nucleotide language of mRNA is interpreted into the amino acid language.

    • A ribosome reads the mRNA code to construct a protein.

    • There are three main participants in translation:

    • Messenger RNA (mRNA): Carries the code from the nucleus to the cytoplasm and has a protein cap serving as a recognition site for ribosomes.

    • Transfer RNA (tRNA): Delivers a single amino acid to the ribosome; contains an anticodon, a series of three nucleotides that complement the mRNA codon.

    • Ribosomes: Organelles that interpret the message and synthesize a peptide chain; consists of a large and small subunit, present free in cytosol, on rough ER, and on the nuclear envelope.

    • The ribosome has three sites involved in the translation process: E (exit), P (peptidyl), and A (aminoacyl) sites.

Translation 2

  • Three Steps of Translation:

    • Initiation:

    • The ribosome assembles with mRNA in the cytosol; the small subunit binds with the leader sequence of mRNA, the large subunit joins, and protein synthesis commences at the AUG codon, with tRNA delivering the initial amino acid, methionine.

    • Elongation:

    • The next tRNA with an amino acid arrives, binding to the A site.

    • The ribosome forms a peptide bond between the first and second amino acids, and the ribosome then shifts down the mRNA by one codon, with the growing peptide now attached to tRNA in the P site.

    • Termination:

    • The ribosome arrives at a stop codon, and the A site binds a release factor protein, causing ribosomal disassembly and dissociation from mRNA.

Translation of mRNA1

  • Figure 4.8:

    • Illustrates the process including components such as nuclear pore, protein cap, ribosomal subunits, tRNA, and protein synthesis pathway utilizing free amino acids and ATP.

Translation of mRNA 2

  • Polyribosomes:

    • Multiple ribosomes can translate the same mRNA molecule simultaneously, forming clusters called polyribosomes.

    • Protein Modification:

    • Proteins destined for lysosomes/excretion undergo modification by the endoplasmic reticulum (ER); the ribosome docks on the ER synthesizing the protein into ER cistern, with modification and packaging into transport vesicles.

Relationship of a DNA Base Sequence to Peptide Structure

  • Figure 4.9:

    • Shows the DNA double helix, base triplets on the template strand, corresponding mRNA codons, tRNA anticodons binding to mRNA codons, and linked amino acids forming a peptide chain.

4.2d Protein Processing and Secretion 1

  • Post-Synthesis Protein Processing:

    • Protein synthesis is incomplete when the amino acid sequence (primary structure) is assembled.

    • Proteins must undergo proper folding into secondary and tertiary structures to function.

    • Chaperone Proteins: Assist in protein folding, help prevent misfolding/misassociation between distinct proteins, often referred to as stress or heat shock proteins produced in response to heat/stress, assisting in correcting misfolded proteins.

Protein Processing and Secretion 2

  • Protein Processing and Secretion Mechanism for Secretory Proteins:

    1. Proteins formed by ribosomes on rough ER.

    2. Proteins are packaged into transport vesicles, which bud from the ER.

    3. Transport vesicles fuse into clusters to form a new cis cistern.

    4. Golgi complex modifies the protein structure.

    5. The trans cistern breaks up into cargo-laden vesicles.

    6. Secretory vesicles release proteins by exocytosis.

Protein Processing and Secretion 3

  • Detailed steps involved in the secretion pathway from the rough ER to the Golgi, to the final exocytosis that releases proteins into the cellular environment.

4.2e Gene Regulation 1

  • Gene Activation:

    • Genes can be turned on and off; cells may permanently deactivate some genes (e.g., liver cells turning off hemoglobin genes).

    • Genes can be activated as needed; expression levels may fluctuate over time, influenced by chemical messengers such as hormones.

    • Example: Mammary gland cells activate casein gene production in response to prolactin only during lactation.

Gene Regulation 2

  • Casein Synthesis and Secretion by Mammary Gland Secretory Cells:

    • Process of activation involving prolactin, transcription activation by regulatory protein, and the downstream production of mRNA for casein leading to secretion.

4.2f Synthesizing Compounds Other Than Proteins

  • Cellular Synthesis:

    • Cells synthesize various compounds (glycogen, fats, steroids, phospholipids, pigments) under indirect genetic control.

    • Synthesized through enzymatic reactions, wherein enzymes as proteins are encoded by genes (e.g., testosterone production).

4.3 DNA Replication and the Cell Cycle 1

  • Expected Learning Outcomes:

    • Describe how DNA is replicated, consequences of replication errors, life history of a cell, events in mitosis, and regulation of cell division timing.

4.3 DNA Replication and the Cell Cycle 2

  • DNA Duplication:

    • Prior to cell division, it is essential for a cell to duplicate its DNA to provide complete genetic copies to each daughter cell.

    • Since DNA regulates all cellular functions, this replication must occur accurately.

    • The Law of Complementary Base Pairing assists in anticipating one strand's sequence if the complementary strand is known.

4.3a DNA Replication 1

  • Four Steps of DNA Replication:

    1. Unwinding the Helix:

    • Histones are released to allow access to the DNA strand.

    1. Unzipping the Helix:

    • A segment of the helix is unwound by the enzyme DNA helicase, creating a replication fork.

    1. Synthesis of Complementary Strands:

    • The enzyme DNA polymerase navigates each strand, reading exposed bases and synthesizing their complementary strands.

    • New, but discontinuous strands are connected by DNA ligase.

    1. Semiconservative Replication:

    • Each new DNA molecule consists of one old (parental) strand and one new (daughter) strand.

    • Newly synthesized histones are used to bundle new DNA strands into nucleosomes.

4.3b Errors and Mutations

  • Replication Errors:

    • DNA polymerase can make errors during replication.

    • DNA Damage Response (DDR):

    • Mechanisms in place for rectifying these errors.

    • DNA polymerase checks base pairs and tends to replace incorrect, unstable pairs with stable, accurate options, estimated as 1 error per billion bases replicated.

    • Mutations:

    • Alterations in DNA structure resulting from replication mistakes or environmental impacts (radiation, viruses, chemicals).

    • Mutations can have varying effects: some cause no harm, others can be lethal, induce cancer, or result in genetic defects in future generations.

4.3c The Cell Cycle 1

  • Components of the Cell Cycle:

    • The cell cycle includes interphase and mitosis.

    • Interphase includes:

    • First Gap Phase (G1):

      • The interval between cell division and DNA replication; during which normal cell functions, protein synthesis occur.

    • Synthesis Phase (S):

      • The period where all nuclear DNA and centrioles are replicated.

    • Second Gap Phase (G2):

      • The interval between DNA replication and cell division; where DNA repair and additional growth occurs.

    • Mitosis consists of:

    • Prophase, Metaphase, Anaphase, Telophase, and Cytokinesis.

The Cell Cycle 3

  • Interphase Specifics:

    • G1 Phase: Initial phase with normal cells functions and preparations for division.

    • S Phase: Concentrates on DNA replication along with centriole duplication.

    • G2 Phase: Cells focus on fixing any DNA errors and get ready for mitosis.

    • G0 Phase: Non-dividing state, cells that leave the cycle for extensive periods can enter this phase.

  • Duration of the cell cycle can vary across different cell types.

4.3d Mitosis 1

  • Mitosis Overview:

    • Cell division yielding two genetically identical daughter cells.

    • Functions of Mitosis:

    • Development from a single fertilized egg to a vast number of cells (~50 trillion).

    • Growth of tissues and organs post-birth.

    • Replacement of deceased cells.

    • Repair of cellular damage.

    • Four phases of mitosis: Prophase, Metaphase, Anaphase, and Telophase.

Mitosis 2

  • Phases of Mitosis:

    • Prophase:

    • Genetic material compacts into chromosomes for easier distribution.

    • Nuclear envelope breaks down; spindle fibers emerge from centrioles, which help pull apart the chromosome pairs by anchoring to kinetochores of centromeres.

    • Metaphase:

    • Chromosomes are aligned on the equator of the cell, forming a structured mitotic spindle.

    • Anaphase:

    • Sister chromatids are separated, with single-stranded daughter chromosomes migrating toward opposing cell poles.

    • Telophase:

    • Chromosomes cluster on either side of the cell, acquire new nuclear envelopes, and revert to chromatin form as the mitotic spindle dissolves.

Mitosis 5

  • Cytokinesis:

    • Involves the division of cytoplasm into two distinct cells.

    • While telophase concludes nuclear division, it coincides with cytokinesis, which is enabled by myosin pulling on actin in the cytoskeleton's terminal web, producing a cleavage furrow around the cell’s equator.

4.3e Regulation of Cell Division 1

  • Cells typically divide under the following conditions:

    • Sufficient cytoplasm for two daughter cells.

    • Completion of DNA replication.

    • Adequate nutrient supply.

    • Growth factors (chemical signals) stimulating division. - Cell death by neighboring cells allowing for space.

  • Cessation of Division:

    • Cells stop dividing under nutrient or growth factor deprivation or through contact inhibition in response to neighboring cell contact.

Regulation of Cell Division 2

  • Cell Cycle Control:

    • Governed by a molecular timer and checkpoints.

    • Molecular Timer: Composed of proteins:

    • Cyclins: Levels fluctuate throughout the cell cycle.

    • Cyclin-dependent Kinases (Cdks): Activated by cyclins for phosphorylating target proteins.

    • Hematics Under Cyclin–Cdk Complex:

    • It directs DNA replication, chromsome composition, nuclear envelope breakdown, mitotic spindle formation, and chromatid separation during respective phases.

Regulation of Cell Division 3

  • Checkpoints in the Cell Cycle:

    • Managed by Cyclin–Cdk complexes for:

    • Start or G1 Checkpoint: Determines if the cell can transition into S phase or revert to the noncyclic G0 phase.

    • G2/M Checkpoint: Late in G2, verifies if the cell is ready for mitosis.

    • A checkpoint transitions from metaphase to anaphase verifies readiness for chromatid separation.

4.4 Chromosomes and Heredity

  • Expected Learning Outcomes:

    • Describe chromosomes' paired arrangement in the human karyotype.

    • Define allele and discuss its influence on traits in an individual.

4.4a The Karyotype

  • Heredity: The process of transferring genetic traits from parent to offspring.

  • Karyotype: A visual representation of all 46 chromosomes arranged by size in pairs:

    • Homologous Chromosomes:

    • One chromosome from each pair inherited from each parent; comprise 23 pairs of homologous chromosomes.

    • Autosomes: 22 pairs that are congruent and carry the same genes.

    • Sex Chromosomes: 1 pair; females possess a homologous X chromosome pair, while males have one X and a notably smaller Y chromosome.

The Normal Human Karyotype

  • Figure 4.16: Illustrates normal karyotype structure.

4.4b Genes and Alleles 1

  • Gene Characteristics:

    • Genes vary but locate at the same position (locus) on chromosomes.

    • Locus: Indicates the precise position of a gene on a chromosome.

    • Alleles: Different variants of a gene, existing at the same locus on homologous chromosomes.

    • Alleles can be:

      • Dominant: Typically expressed in phenotype if present; masks recessive effects.

      • Recessive: Not expressed unless present on both chromosomes; often linked to nonfunctional variants.

4.4b Genes and Alleles 2

  • Genotype vs Phenotype:

    • Genotype: The specific alleles an individual has for a particular gene.

    • Homozygous individuals: possess identical alleles.

    • Heterozygous individuals: have differing alleles.

    • Phenotype: The observable trait of an individual influenced by one or multiple genes.

    • Example: Sickle-cell disease results from homozygous recessive alleles; carriers with one allele exhibit the sickle-cell trait.

4.4e Sex Linkage

  • Sex-Linked Traits: Carried on X or Y chromosomes, which often results in different inheritance patterns between sexes.

  • Example: The recessive color blindness allele is found on the X chromosome without a corresponding locus on the Y chromosome, making color blindness more frequent in males (with female carriers illustrated in Figure 4.20).

4.4h Epigenetics

  • Epigenetic Effects: Gene expression modifications that occur without altering base sequences, which can still be inherited, referred to as epigenetic inheritance.

  • Mechanisms of Epigenetic Changes:

    • DNA methylation: The addition of methyl groups (—CH3) to the DNA structure.

    • Variations in chromatin packaging.

    • Gene silencing via noncoding RNA (ncRNA).

  • Health Implications: These epigenetic changes may be typical, but some could lead to diseases, such as cancer.