Audiological Disorders Prezys

  • Usher Syndrome

    • rare genetic

    • vision (retinitis pigmentosa) & hearing

    • Types

      • I: most sever, profound

        • Hearing & balance loss

      • II: moderate

        • Hearing loss

        • No balance loss

        • Later vision issues

      • III: progressive

        • symptoms show up later

    • Symptoms treated cuz no cure

    • Cause less interaction with peers

    • One of the leading causes of deaf-blindness

  • Cytomegelovirus

    • Common DNA virus, but healthy people are asymptomatic

      • Concern for pregnant people or immunocompromised

    • Symptoms

      • Jaunice

      • Seizure

      • Difficulty localizing

    • Audiogram: Bilateral mild to severe hearing loss

    • Treat and manage symptoms

    • Risks to speech

      • No localization, language delays, speech inteligibility

    • Because of this, doctors perform blood tests at birth

  • Rubella

    • Sensorineural hearing loss

    • Language delays

    • low birth weight, blue & purple spots, cataracts

    • When a pregnant women gets rubella during pregnancy which can affect baby. (most severe when in the first trimester)

  • Meningitis

    • Kids under age 5

    • Hearing loss, tinnitus, difficulty hearing in noisy environment, vision troubles, memory issues, brain damage, kidney failure, shock, death

    • Sensorineural hearing loss

    • Inflammation of the meninges (membrane around brain & spinal cord)

    • Hearing loss when the bacteria goes from the meninges to the auditory pathways

    • The main symptomatic difference between this and cold is a stiff neck

    • Pretty serious infection

    • If cochlea has ossified cant do the cochlear implant surgery

  • Ramsay Hunt Syndrome

    • Shingles affecting the facial nerve

    • Sudden right-sided facial weakness and sever ear pain, facial paralysis, sometimes hearing loss, tinnitus, vertigo, weakness/paralysis on one side of face, dry mouth or eyes, difficulty closing one eye, vesicular rash around one ear

    • Virus stays dormant until later

    • Antivirals taken within first 72 hours

    • Facial paralysis can impact speech production

    • Hearing loss can impact speech perception

  • NF2

    • Rare genetic disorder

    • Non-cancerous tumors along auditory nerve or on skin

    • Rare genetic

    • Bilateral sensorineural hearing loss, mild to severe slope

    • No cure, can treat symptoms

    • Multiple tumors

  • Vestibular schwanoma (acoustic neuroma)

    • Most cases spontaneously

    • Vestibular therapy for balance

    • Just one tumor growing on vestibulocochlear nerve