Mendelian Genetics

Mendelian Genetics Part 1

  • Relevant Material:
    • Scitable by Nature Education: http://www.nature.com/scitable
    • Textbook: Urry et al. (2022). Campbell Biology, Australian and New Zealand Version (12th edition). Pearson. Australia. Chapter 14.
  • Learning outcomes:
    • Topic:
      • Examine the nature and flow of genetic information.
      • Predict outcomes of simple Mendelian inheritance.
      • Explain how complex organisms develop from a single cell.
    • Lecture:
      • Understand and apply Mendel’s law of segregation.
      • Understand and apply Mendel’s law of independent assortment.
      • Use probability laws to determine phenotypic ratios.

Gene Definition

  • Definition of a gene.

Terminology

  • Allele: An alternate form of a gene.
  • Homozygous
  • Heterozygous
  • Gamete
  • True-breeding/pure-breeding
  • Self-cross

Mendel’s First Law: The Law of Segregation

  • The two alleles for a heritable character segregate during gamete formation and end up in different gametes.

Mendel’s Second Law: The Law of Independent Assortment

  • Two or more genes assort independently.
  • Each pair of alleles segregates independently of any other pair of alleles during gamete formation.
  • Independent assortment leads to genetic variation.

Problem

  • How many unique gametes could be produced through independent assortment by a diploid individual with the genotype AaBb?

Mendelian Genetics Part 2

Law of Segregation in Action

  • Monohybrid cross.
  • P Generation: True-breeding yellow (YY) x True-breeding green (yy).
    • Yellow (Y):
      • Genotype: YY
      • Gametes: Y
    • Green (y):
      • Genotype: yy
      • Gametes: y
  • F1 Generation: Yy (all yellow-seeded).
    • Phenotype: Yellow
    • Genotype: Yy
    • Gametes: Y, y

Law of Segregation in Action

  • F2 Generation: Self-cross of F1 (Yy x Yy).

Law of Independent Assortment in Action

  • Dihybrid cross.
  • Two genes:
    • Yellow gene:
      • Two alleles: Y > y
      • Yellow > green
    • Round gene:
      • Two alleles: R > r
      • Round > wrinkled
  • P Generation: True-breeding round yellow (YYRR) x True-breeding green wrinkled (yyrr).
    • Yellow Round: YYRR
      • Gametes: YR
    • Green Wrinkled: yyrr
      • Gametes: yr
  • F1 Generation: YyRr (all round yellow).

Law of Independent Assortment in Action

  • F2 cross: self-cross of F1 generation.
  • Gametes from F1: YR, Yr, yR, yr.
  • Phenotypic ratio in F2: 9:3:3:1.

Summary: Mendelian Phenotypic Ratios

  • Monohybrid cross:
    • One gene: 3:1.
  • Dihybrid cross:
    • Two genes: 9:3:3:1.

Test Cross

  • A test cross can be used to determine genotype.
  • Question: Is the purple plant homozygous (PP) or heterozygous (Pp)?
  • Cross plant with unknown genotype to homozygous recessive plant.
  • Predict a 1:1 phenotypic ratio in offspring if heterozygous.
  • Purple plant (P-) x White plant (pp).
    • If purple plant is PP:
      • F1: All offspring are purple (Pp).
    • If purple plant is Pp:
      • F1: 1/2 offspring are purple (Pp), 1/2 offspring are white (pp).

Summary: Mendelian Phenotypic Ratios

  • Monohybrid cross:
    • One gene, 3:1.
  • Dihybrid cross:
    • Two genes, 9:3:3:1.
  • Test cross:
    • One gene, expect a 1:1 ratio.
    • Two genes, expect a 1:1:1:1 ratio.

Problem

  • Mary is a farmer breeding pea plants. Seed colour in pea plants is controlled by a single gene. Mary crosses true breeding yellow-seeded and green-seeded pea plants. The F1 generation are all yellow-seeded. She then allows the F1 yellow-seeded offspring to self-pollinate to produce the F2 generation. There are 8,500 pea plants in the F2 generation. What are the expected numbers of yellow-seeded and green-seeded pea plants in the F2 generation?

Mendelian Genetics Part 3

  • Learning outcomes:
    • Topic:
      • Examine the nature and flow of genetic information.
      • Predict outcomes of simple Mendelian inheritance.
      • Explain how complex organisms develop from a single cell.
    • Lecture:
      • Understand and apply Mendel’s law of segregation.
      • Understand and apply Mendel’s law of independent assortment.
      • Use probability laws to determine phenotypic ratios.

Probability Laws

  • Simple probability.
  • Multiplication rule.
  • Addition rule.
  • Multiplication (Product) rule:
    • Probability of two or more independent events occurring together is the product of the probabilities that each event will occur by itself.
  • Addition (Sum) rule:
    • Probability of either of two such mutually exclusive events occurring is the sum of their individual probabilities.

Problem

  • Consider a yellow round pea of the following genotype, YyRr.
    1. What is the probability that this plant will produce a YR gamete? 1/4
    2. If this plant is self-crossed, what is the probability of a YYRR genotype in the next generation? 1/16
    3. If the plant is self-crossed, what is the probability of a YYRR or a yyrr genotype in the next generation? 1/16 + 1/16 = 2/16 = 1/8

Problem

  • Two true-breeding stocks of plants were crossed. One parent had red, axial flowers and the other had white, terminal flowers. All offspring produced during the F1 generation had red, axial flowers. 1,000 F2 generation offspring resulted from the self-cross of F1 individuals. Approximately, how many of the F2 generation would you expect to have red, terminal flowers? Assume independent assortment. Round your answer to the nearest whole number.
    • Red, terminal flowers = 3/16.
    • (3/16) * 1000 = 187.5
    • Approximately 188.

Biology with Trixie

  • Coat colour in Labradors is controlled by two genes, B and E.
    • B allele produces black melanin.
    • b allele produces brown melanin.
    • e allele prevents deposition of pigment in hairs.

Extension to Mendelian Genetics Part 1

  • Relevant Material:
    • Scitable by Nature Education: http://www.nature.com/scitable
    • Textbook: Urry et al. (2022). Campbell Biology, Australian and New Zealand Version (12th edition). Pearson. Australia. Chapters 14-15.

Learning Outcomes

  • Topic learning outcomes:
    • Examine the nature and flow of genetic information
    • Predict outcomes of simple Mendelian inheritance
    • Explain how complex organisms develop from a single cell
  • Lecture learning outcomes:
    1. Describe and solve complex inheritance patterns
    2. Use a pedigree to depict autosomal dominant and autosomal recessive inheritance of a trait
    3. Compare and contrast the human X-Y system to other systems
    4. Use a pedigree to depict X-linked dominant and X-linked recessive inheritance of a trait
    5. Understand and describe X- inactivation

Degrees of Dominance: Extending Mendelian Genetics

Incomplete Dominance: Snapdragon

  • One gene, three phenotypes.
  • C gene, two alleles: C^R and C^W.
  • Antirrhinum majus.

Incomplete Dominance: Snapdragon

  • Phenotypic ratio: 1:2:1 (Red:Pink:White).

Codominance: Blood Type

  • Three alleles: IA, IB, i.
  • Six possible genotypes.
  • Four possible phenotypes.

Blood Type

  • ABO blood type.
    • Blood type based on presence or absence of antigens on red blood cells.
    • Inherit one allele from each parent.
  • Rhesus factor.
    • Antigen found on surface of red blood cells (RhD proteins).
    • Rh+ = have D antigen.
    • Rh- = don’t have D antigen.
    • Inherit one allele from each parent.

Multiple Choice Question

  • If a biological female with blood type AB mates with a biological male with blood type O, what possible genotypes could their offspring have?
    1. IAIB only
    2. IAi, IBi (correct)
    3. IAi only
    4. IAIA, IBIB
    5. ii only

Pedigree

Interpreting a Pedigree

  • Is the trait in every generation?
  • Do affected parents have affected offspring?
  • Consanguineous.

Autosomal Dominant or Autosomal Recessive Inheritance?

Autosomal Recessive Inheritance: Albinism

  • Oculocutaneous albinism.
  • Little or no production of pigment melanin.
  • Most common and severe form of albinism, OCA1.
  • Caused by mutations in tyrosinase (TYR) gene.
  • Individuals with OCA1 have two mutated copies of gene.

Autosomal Recessive Inheritance: Cystic Fibrosis

  • Single gene disorder.
  • Cystic Fibrosis Transmembrane Conductance Regulator (CFTR).
  • Individuals with CF have two mutated copies of gene.
  • Phenotype:
    • Chronic obstructive lung disease.
    • Exocrine pancreatic insufficiency.
    • Elevated sweat chloride concentration.
    • Infertility.

Autosomal Dominant Inheritance: Achondroplasia

  • Form of dwarfism caused by dominant allele.
  • Individuals with Achondroplasia have one mutated copy of FGFR3 gene.
  • Two copies of dominant mutated allele is lethal.

Multiple Choice Question

  • Michael has Achondroplasia. His partner is of typical stature. What is the probability that they will have a biological male child of typical stature?
    1. 1/2 (correct)
    2. 1/4
    3. 1/8
    4. 1/16

Extension to Mendelian Genetics Part 3

  • Learning outcomes:
    • Topic learning outcomes:
      • Examine the nature and flow of genetic information
      • Predict outcomes of simple Mendelian inheritance
      • Explain how complex organisms develop from a single cell
    • Lecture learning outcomes:
      1. Describe and solve complex inheritance patterns
      2. Use a pedigree to depict autosomal dominant and autosomal recessive inheritance of a trait
      3. Compare and contrast the human X-Y system to other systems
      4. Use a pedigree to depict X-linked dominant and X-linked recessive inheritance of a trait
      5. Understand and describe X- inactivation

Thomas Hunt Morgan

  • American Scientist.
  • Used Drosophila melanogaster to study genetics.
  • 1910 discovered first mutation in Drosophila.
    • White eyed mutant.
  • Established the chromosomal theory of inheritance.
  • Awarded Nobel Prize of Medicine in 1933.

Genes on X Chromosome Show Unique Inheritance Patterns

  • w+ allele = wild type, red eyes.
  • w allele = mutant, white eyes.
  • Males have white eyes when carry one copy of w allele.
  • Females must have two copies of w to have white eyes.
  • Gene for eye colour on X chromosome

Inheritance of an X-Linked Recessive Trait: Red-Green Colour Blindness

  • Can not distinguish shades of red and green.
  • Caused by mutation in OPN1LW or OPN1MW genes.
  • More common in males.

Inheritance of a X-Linked Dominant Trait: Alport Syndrome

  • Rare disorder.
  • Phenotype includes kidney disease, hearing loss, eye abnormalities.
  • Affected people have a mutation in the COL4A5 gene.
  • More common in biological females (often lethal in males)

How to Determine the Mode of Inheritance in a Pedigree

  1. Are there affected individuals in every generation?
  2. Do affected parents have affected offspring?
  3. Do affected males have affected sons?
  4. What is the ratio of affected males to females?
    • Rare: Most likely X-linked recessive.
    • Most likely Autosomal dominant, autosomal recessive, X-linked dominant, X-linked recessive

X-Inactivation

  • X inactivation occurs in biological female mammals.
  • Biological female mammals (XX):
    • One X chromosome is inactivated in each cell during early embryonic development.
    • Inactive X condenses = Barr body.
    • Most of genes in Barr body not expressed.
    • In the ovaries, Barr body chromosomes reactivated.

Multiple Choice Question

  • Cinnabar eye colour is an X-linked, recessive characteristic in fruit flies. If a female having cinnabar eyes is crossed with a male having wild type, red eyes, what percent of the F1 males will have cinnabar eyes?
    1. 0%
    2. 25%
    3. 50% (correct)
    4. 75%
    5. 100%

Biology with Trixie

  • What can the dogs of Chernobyl teach us about living for decades under extreme radiation?