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HEMATOLOGY PRML189 FINALS | A.Y. 2025-2026

HEMATOPOIESIS

Definition
  • The process of blood cell formation.

  • Also referred to as hemopoiesis.

  • Classical marker of hematopoietic stem cells (HSCs): CD34.

  • CD = clusters of differentiation.

Types of Blood Cells
  1. Red Blood Cells (RBCs)

  2. White Blood Cells (WBCs)

  3. Platelets

RELATED THEORIES (Origin of Hematopoietic Progenitor Cells)

1. Polphyletic Theory
  • Suggests that all blood cells have their own unique stem cells.

Notes
  • All blood cells originate from separate stem cells

  • Separate stem cells for RBC, WBC, megakaryocytes, and platelets

2. Monophyletic Theory
  • All blood cells are derived from a singular stem cell called a pluripotential stem cell (PSC).

Notes
  • Most widely accepted theory among experimental hematologists

PHASES OF HEMATOPOIESIS

1. Mesoblastic / Megaloblastic Phase
  • Chief site of hemopoiesis: yolk sac

  • First blood cells: primitive erythroblasts (formed during the first 2-8 weeks of life).

Notes
  • Primitive erythroblasts are the first blood cells produced in human life.

  • The hemoglobins produced: Portland, Gower 1, and Gower 2.

  • These hemoglobins deliver oxygen to embryonic tissues and are called embryonic hemoglobins.

2. Hepatic Phase
  • Chief site of hemopoiesis: fetal liver, with contributions from spleen, thymus, lymph nodes.

  • Predominant hemoglobin: Hb F (fetal hemoglobin).

  • Thymus: first fully developed organ in the fetus; major site of T cell production.

Notes
  • Spleen and lymph nodes also participate in fetal hemopoiesis.

3. Medullary / Myeloid Phase
  • Chief site of hemopoiesis: bone marrow (BM).

  • Hematopoiesis starts in the BM cavity before the 5th month of fetal development and becomes the main site by 24 weeks of gestation.

Notes
  • Bone marrow starts producing blood cells before birth, contrary to common misconceptions.

ADULT HEMATOPOIESIS

  • Not only occurs in the bone marrow but also in lymph nodes, spleen, thymus, and liver.

  • Bone marrow can generate (per kilogram of body weight daily):
      - 2.5 billion RBCs
      - 1 billion granulocytes
      - 2.5 billion platelets

Retrogression
  • The process by which red marrow is replaced by yellow marrow during development, occurring between the ages of 5-7 years.

Notes
  • Red marrow becomes restricted to the RSVP (Ribs, Sternum, vertebrae, and Pelvis) in adults.

  • In adults, approximately 50% of marrow is red and 50% is yellow.

Red and Yellow Marrow
  • Red Marrow: Hematopoietically active.

  • Yellow Marrow: Hematopoietically inactive, composed of fat cells.

  • Yellow marrow can revert to active marrow under demand (e.g., blood loss).

LYMPHOID DEVELOPMENT

Primary Lymphoid Organs
  • Consist of bone marrow and thymus where T and B lymphocytes are derived.

Secondary Lymphoid Organs
  • Major organs: spleen and lymph nodes

Function of Secondary Lymphoid Organs
  1. Trapping and concentrating foreign substances

  2. Production of antibodies; induction of antigen-specific T lymphocytes.

Spleen
  • Largest secondary lymphoid organ

  • Important for immunity via antibody production.

Effects of Splenectomy
  • In children: increased risk of bacterial sepsis (e.g. S. pneumoniae).

  • In adults: mild effects similar to children.

RELATED TERMS

Splenectomy
  • The removal of the spleen.

Splenomegaly
  • Enlargement of the spleen.

Minor Secondary Lymphoid Organs
  • Tonsils, appendix, Peyer’s patches, MALT (mucosa-associated lymphoid tissue).

EXTRAMEDULLARY HEMATOPOIESIS
  • Blood cell production outside bone marrow, mainly in the liver and spleen.

Notes
  • It occurs under conditions like bone marrow dysfunction or when demand exceeds supply (e.g., hemolytic anemias).

Conditions Leading to Extramedullary Hematopoiesis
  1. Aplastic anemia

  2. Leukemia

  3. Hemolytic anemias

THALASSEMIA

  • A hematologic disease where the bone marrow attempts to produce more RBCs to counteract severe anemia but remains insufficient.

  • Extramedullary hematopoiesis may occur in the spleen.

Note: From Rodak’s Hematology
  • Various test sources and underlying conditions discussed throughout the document.


BONE MARROW COLLECTION SITES
  • Preferred Sites for Adults:
      - P.S. IL. CREST, A.S. IL. CREST, STERNUM

  • Preferred Site for Children (<2 y.o.):
      - ANTERIOR MEDIAL SURFACE OF THE TIBIA

BONE MARROW ASPIRATE
  • Disturbs BM architecture; spread as a smear, stained, examined for disease.

  • Retained for 10 years due to importance in analysis of individual cell morphology.

M:E (Myeloid-to-Erythroid) Ratio
  • Proportion of myeloid cells to nucleated erythroid precursors in the bone marrow aspirate.

Notes
  • In healthy adults, the M:E ratio varies from roughly 1.5:1 to 3.3:1.

  • In leukemia, the M:E ratio is approximately 10:1.

HEMATOPOIESIS
  • Continues into adulthood with contribution from lymph nodes, spleen, thymus, and liver (in pathological instances).


RETICULOCYTES
  • Immature red blood cells produced in bone marrow, indicating active erythropoiesis.

MATURATION STAGE OF RBCS
  • Stages: Rubriblast, Prorubricyte, Rubricyte, Metarubricyte, Reticulocyte, Mature erythrocyte.

Features
  • Red cell size, nucleus characteristics, presence of nucleoli, cytoplasmic change during maturation noted.

SUPERVITAL STAINS
  • Used to stain reticulocytes; examples include Brilliant Cresyl Blue and New Methylene Blue.


HORMONES RELATED TO ERYTHROPOIESIS
  1. Erythropoietin (EPO)

  2. Growth Hormone (GH)

  3. Testosterone

  4. Prolactin

  5. Estrogen

Erythropoietin Functionality
  • Stimulates release of reticulocytes and maturation in BM; secreted by kidneys.

Erythropoiesis Pathway
  • Involvement of BFU-E, CFU-E, differentiating into recognizable precursors, eventually into mature erythrocytes.

ANEMIAS

Definition
  • Decrease in RBC, hemoglobin, or hematocrit below normal levels.

  • Anemia is a manifestation, NOT a disease.

CLASSIFICATION OF ANEMIAS
  • Morphologic Classification:
      1. Normocytic, Normochromic
      2. Microcytic, Hypochromic
      3. Macrocytic, Normochromic

Examples of Microcytic Anemia:
  • Iron deficiency and Thalassemia; causes include chronic blood loss, malabsorption.

Megaloblastic Anemia Classification:
  • Caused by Vitamin B12 or Folate deficiency.

  

This concludes the definitive study guide based on the provided transcript. Keep this structured format for comprehensive examination preparation and class discussions in hematology.