Module 2 Drugs

Myasthenia Gravis and Alzheimers

Cholinesterase Inhibitors - Neostigmine

MOA - Cholinesterase inhibition causes an increase in ACh at the neuromuscular and central synapses at the NMJ

Indications - Myasthenia fravis treatment; edrophonium - reversal of non-depolarizing neuromuscular blockers

Adverse Effects - Cholinergic crisis

Risks - GI obstruction, Asthma, Bradycardia

RN Implications - Individualized sosing; medical alert bracelet; differentiate myasthenic vs cholinergic crisis

Other drugs in class: Phsostigmine, Edrophonium, Pyridostigmine

Central Cholinesterase Inhibitors - Donepezil

MOA - Centrally selective cholinesterase inhibition causes an increase in ACh in the brain

Indications - Mild to moderate Alzheimer’s

Adverse Effects - N/V/D, dizziness, bradycardia, syncope

Risks - Caution with bradycardia, COPD/asthma

RN Implications - Safety for falls; HR monitoring; Nighttime dosing to minimize GI upset

Other drugs in class: 

Parkinson’s Disease

Dopamine synthesis - Levodopa/Carbidopa

MOA - Increases dopamine in the CNS; prevents peripheral breakdown, so more Levodopa reaches the brain and causes fewer side effects

Indications - Treatment fo bradykinesia, rigidity, tremor

Adverse Effects - Discoloration of urine/sweat

Risks -  CV effects, psychosis, “on-off”, wearing off

RN Implications - High-yield food, avoid large doses of pyridoxine-rich foods; spread protein intake throughout the day; monitor for dyskinesias -> may need amantadine or dose adjustment; Timing “on” periods for PT/ADLs - report worsening on-off to provider

Other drugs in class: none

Dopamine Agonists - Pramipexole

MOA - Stimulates dopamine receptors

Indications - early PD monotherapy

Adverse Effects - Daytime sleep attacks, hallucinations, orthostatic hypotension, impulse control disorders

RN Implications - Screen for compulsive behaviors; caution about driving; counsel the family to watch for personality changes 

Other drugs in class: Ropinrole, Apomorphine, Rotigotine

Dopamine Releaser - Amantadine

MOA - smooths out dopamine release; increases dopamine release, decreases reuptake

Indications - reduced levodopa-induced dyskinesias

Adverse Effects - confusion, dizziness, Insomnia

Risks - Livedo reticularis

RN Implications - reassure about reversible skin changes; safety for falls; avoid activities requiring high alertness early in therapy

Other drugs in class: none

COMT Inhibitors - Entacapone

MOA - Inhibits COMT, causing prolonged levodopa action by decreasing peripheral breakdown

Indications - adjunct to levodopa/carbidopa

Adverse Effects - GI upset, Dyskinesias, Orthostatic Hypotension

Risks - Urine discoloration; Tolacpone hepatotoxicity

RN Implications - LFT monitoring if talcopne used; teach harmless urine discoloration

Other drugs in class: Tolcapone

MAO-B - Inhibitors - Selegiline

MOA - Inhibits MAO-B, causing decreased dopamine breakdown

Indications - Early PD or adjunct to levodopa to reduce “wearing off.”

Adverse Effects - Insomnia, N/V

Risks - Hypertensive crisis with tyramine foods; Interaction with merperidine, SSRIs, other MAOIs

RN Implications - Give no later than noon; Tyramine avoidance 2 weeks after stopping; review the med list carefully

Other drugs in class: Rasagiline

Anticholinergics - Benzotropine

MOA - Muscarinic blockade causes decreased tremor and muscle rigidity

Indications - PD tremor; drug-induced EPS

Adverse Effects - Anticholinergic symptoms

Risks - Glaucoma, BPH, and Elderly Delirium risk

RN Implications - I&O; fiber and fluids; eye pressure monitoring; avoid in older adults with confusion

Other drugs in class: trihexyphenidyl 

Seizure Disorders

Barbiturate AEDS - Phenobarbital

MOA - increases GABA, causing a strong CNS depression

Indications - Tonic Clonic and Partial seizures

Adverse Effects - Sedation, Cognitive Impairment 

Risks - dependence, respiratory Depression, Toxicity

RN Implications - Avoid other CNS Depressants; taper slowly; monitor for respiratory and cardiac depression

Other drugs in class: Primadone

Hydantoins - Phenytoin

MOA - Na channel slowing -> reduced seizure spread

Indications - tonic-clonic and partial seizures

Adverse Effects - CNS (Nystagmus, Ataxia); Gingival hyperplasia, rash

Risks - Dysrhythmias, Hypotension; teratogenic; narrow TI

RN Implications - Slow IV rate, large vein; Good oral hygiene, folic acid; monitor warfarin and OCP levels; Monitor for rash

Other drugs in class: Fosphenytoin

Carbamasepine

Indications - Focal and tonic-clonic seizures, bipolar, and trigeminal neuralgia

Risks - Blood dyscrasias; SJS/TEN; Hypo-osmolarity/SIADH

RN Implications - CBC baseline and trend; monitor NA+ and fluid status; avoid grapefruit Juice; stop if rash appears

Valproic Acid

Indications - Broad-spectrum seizures, bipolar disorder, migraines

Risks -  hepatotoxicity; pancreatitis; thrombocytopenia; teratogenic

RN Implications - LFTs, Amylase, platelets; report abdominal pain, jaundice, easy bruising

Succinimides - Ethosuximide

MOA - Reduced T-type calcium currents in thalamic neurons

Indications - Absence seizures only

Adverse Effects - GI upset, sleepiness, fatigue

Risks - Rare SJS, Blood Dyscrasias

RN Implications - Give with food; monitor for bruising; safety precautions for drowsiness

Other drugs in class: none

Sodium-Channel Modulator - Lamotrigine

MOA - Inhibits glutamate release

Indications - Seizures, bipolar depression

Adverse Effects - dizziness, blurred vision, headache, N/V

Risks - SJS/TEN, Aseptic Meningitis, suicidality when starting

RN Implications - Slow titration; caution if also on valproate 

Other drugs in class: none

SV2A Modulator - Levetiracetam

MOA - Modulates SV2A to reduce neurotransmitter release

Indications - partial seizures, tonic-clonic, myoclonic

Adverse Effects - dizziness, asthenia, fatigue, agitation

Risks - Mood changes, Suicidality

RN Implications - Screen for underlying depression/anxiety; Fewer drug interactions than many AEDs; Seizure diary encouraged

Other drugs in class: Brivaracetam

GABA enhancer + Glutamate Antagonist - Topiramate

MOA - Enhances GABA, blocks sodium channels, antagonizes glutamate receptors

Indications - Seizures, Migraine prophylaxis

Adverse Effects - Somnolence, cognitive slowing, weightloss

Risks - Metabolic acidosis; decreased sweating/increased body temperature; angle-closure glaucoma; Teratogenic

RN Implications - Monitor Bicarbinate; hydration teaching, report eye pain/ vision changes urgently; avoid overheating

Other drugs in class: none

Sodium-Channel Modulator - Oxcarbazepine

MOA - Na Channel blockade

Indications - Partial Seizures

Adverse Effects - dizziness, somnolence, N/V, ataxia

Risks - hyponatremia; SJS/TEN; Hypothyroidism; Multiorgan hypersensitivity 

RN Implications - Monitor sodium; screen for rash, assess confusion/fatigue; backup contraception; watch for edema or signs of hypersensitivity

Other drugs in class: eslicarbazepine

Gabapentinoids - Gabapentin

MOA - Binds α2δ calcium channels, causing a decrease in excitatory neurotransmission

Indications -  neuropathic pain, partial seizures, fibromyalgia

Adverse Effects - Somnolence, dizziness, peripheral edema, weight gain

Risks - Pregabalin; Angioedema; abuse potential 

RN Implications - Avoid alcohol/CNS depressants; monitor weight and edema; teach to report facial/lip swelling immediately; caution with driving

Other drugs in class: Pregabalin

Emergency Seizure Management

MOA - Enhances GABA, causing a rapid CNS depression

Indications - Status Epilepticus; prolonged tonic-clonic seizure

Adverse Effects - Respiratory depression; hypotension

Risks - Airway compromise; Apnea with repeated dosing

RN Implications - Firstline - IV lorazepam or Diazepam; Load with fosphenytoin/phenytoin; Maintain Airway; Establish IV access; Document duration, triggers, motor activity progression 

Other drugs in class: Lorazepam, Diazepam