5. LYMPHOMA-II (NON-HODGKIN LYMPHOMA-I)_820fe86ccb759d66db9b1d33e3b9d74a copy

Page 1: Cover Page

  • University: Almaarefa University

  • Course: Lymphoma-II

Page 2: Learning Objectives

  • Define Lymphoma

  • Classify lymphomas

  • Recall etiology, common types, pathomorphological features, diagnosis, prognosis, and staging of Non-Hodgkin Lymphoma (NHL)

  • Discuss Burkitt lymphoma: origin, etiology, common sites, types, and clinical features

Page 3: Normal Structure of Lymph Node

  • Image reference: SCIENCEphotoLIBRARY

Page 4: Definition of Lymphoma

  • Malignant neoplasm of lymphoid origin

  • Can cause solid tissue mass (lymphadenopathy) or extra-nodal mass (e.g., brain, intestine)

Page 5: WHO Classification of Lymphoid Neoplasms

I. Non-Hodgkin Lymphoma

  • A. B cell lymphoma

  • B. T cell/NK cell lymphoma

II. Hodgkin Lymphoma

Page 6: Non-Hodgkin Lymphoma (NHL)

  • Overview of NHL as a major type of lymphoma

Page 7: Epidemiology of NHL

  • Most common hematopoietic neoplasm

  • Seventh among all cancers

  • 5 times more common than Hodgkin Lymphoma

  • Predominantly affects males > females

  • Typically occurs in individuals older than 50 years

  • Higher risk in white populations compared to black and Asian Americans

Page 8: Etiology of NHL

  • Chromosomal translocations: most common - t(14;18)

  • Immunodeficiency states (e.g., AIDS, immunosuppression)

  • Chronic inflammation (autoimmune diseases: Sjögren syndrome, Hashimoto thyroiditis)

Page 9: Infections associated with NHL

  • Human T-cell leukemia virus type-1 (HTLV-1)

  • Epstein-Barr virus

  • Hepatitis C virus

  • Kaposi sarcoma-associated herpesvirus (KSHV)

  • Helicobacter pylori

Page 10: Environmental Factors

  • Chemicals: pesticides, herbicides, solvents, organic chemicals, wood preservatives, hair dye

  • Previous chemotherapy treatment

  • Radiation exposure

Page 11: Sites for Non-Hodgkin Lymphoma

A. Nodal lymphoma

  • Begins in lymph nodes

B. Extra-nodal lymphoma

  • Common sites include:

    • Intestine

    • Central nervous system

    • Skin

    • Brain

    • Testis

    • Spleen

    • Ovary

Page 12: General Clinical Manifestations

  1. Asymptomatic lymphadenopathy

    • Progressive, peripheral, and painless

  2. "B symptoms":

    • Fever

    • Night sweats

    • Weight loss >10% in 6 months

Page 13: Features Related to Extra-Nodal Involvement

  • Splenomegaly

  • Hepatomegaly

  • Large abdominal mass

  • Testicular mass

Page 14: General Investigations

  • Complete blood cell (CBC) count

  • Chest radiography

  • CT scan of neck, chest, abdomen, pelvis

  • PET scan

  • Lymph node biopsy

  • Bone marrow aspirate and biopsy

  • Biopsy of extranodal sites

Page 15: General Morphological Features

Gross Features

  • Affected lymph nodes:

    • Enlarged

    • Soft, fleshy consistency

    • Grayish-white appearance

    • Presence of foci of hemorrhage and necrosis

Page 16: Gross Image of Lymph Nodes Involved by NHL

Page 17: Spleen Involvement in NHL

  • Gross image reference

Page 18: Involvement of Small Intestine by NHL

  • Gross image reference

Page 19: Microscopic Features (H&E Stain)

  • Loss of normal architecture

  • Diffuse infiltration by monoclonal malignant lymphoid cells

Subtyping by Immunohistochemistry

  • B cell lymphoma: CD20

  • T cell lymphoma: CD3, CD5

Page 20: Microscopy of NHL - Lymph Node (H&E Stain)

Page 21: Microscopy of NHL - Intestine (H&E Stain)

Page 22: Immuno-histochemical Image

  • B cell lymphoma (NHL) with CD20 stain

Page 23: Origin and Classification of NHL

Page 24: Stages of B and T Cell Generation

  • Origin of various types of Non-Hodgkin Lymphoma

  • Key cells involved: Precursor B lymphoblastic, T cell neoplasms

Page 25: B Cell Neoplasms

A. Precursor B Cell Neoplasms

  • Lymphoblastic leukemia/lymphoma

B. Peripheral B Cell Neoplasms

  • Chronic Lymphocytic leukemia/small lymphocytic lymphoma

  • Diffuse large B cell lymphoma

  • Lymphoplasmacytic lymphoma

  • Mantle cell lymphoma

  • Follicular lymphoma

  • Marginal zone lymphoma

  • Burkitt lymphoma

Page 26: B-Cell Lymphomas

  • Constitute about 90% of all lymphomas

  • Diffuse large B-cell lymphoma (DLBCL): most common, highly aggressive

  • Follicular lymphoma: second most common, slow-growing (indolent)

Page 27: Burkitt Lymphoma (BL)

  • Type of peripheral B cell neoplasm

  • Origin: Germinal center cells

  • Affects children and young adults, males 2-3 times more than females

  • Characterized by translocations of the c-MYC gene on chromosome 8

  • Very aggressive but responds well to intensive chemotherapy

  • Most patients can be cured

Page 28: Three Types of Burkitt Lymphoma

  1. African (endemic) BL

  2. Sporadic (nonendemic) BL

  3. Associated with HIV

Page 29: Endemic BL

  • Most common in children aged 4-7 years in certain regions of Africa

  • Typically associated with EBV infection

  • Common sites include: Mandible, kidneys, ovaries, adrenal glands

Page 30: Sporadic Burkitt Lymphoma

  • Common sites include ileocecum and peritoneum

Page 31: Burkitt Lymphoma Before and After Treatment

  • Image reference: SOCCER STAR

Page 32: Microscopic Features of Burkitt Lymphoma

  • Characteristic “Starry sky” pattern

  • Intermediate-sized malignant lymphoid cells

  • Tingible body macrophages

Page 33: Microscopy of Burkitt Lymphoma (H&E Stain)

  • "Starry sky pattern"

Page 34: T Cell and NK Cell Neoplasms

A. Precursor T Cell Neoplasms

  • T cell acute lymphoblastic leukemia/lymphoma (T-ALL)

B. Peripheral T-Cell and NK Cell Neoplasms

  • Various subtypes including: T cell prolymphocytic leukemia, mycosis fungoides, Large granular lymphocytic leukemia

  • Aggressive natural killer cell lymphoma

Page 35: T Cell and NK Cell Lymphomas

  • Constitute 10% of all NHL

  • Generally more aggressive than B-cell lymphomas

  • Peripheral T cell lymphomas are especially common in Asia

Page 36: Staging of NHL

  • Utilizes the Ann Arbor Staging System

  • Purpose: to guide treatment and prognosis

Page 37: Treatment Options

  • Radiation therapy

  • Chemotherapy

  • Monoclonal antibodies

Page 38: References

  • Key texts: Robbins and Cotran Pathologic Basis of Disease, Robbins Basic Pathology

  • AMBOSS resource link

Page 39: Thank You

  • Closing remarks